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"' WibuvL(0o*Ok`&J'w>3Q PP P%Q %1~= bu{_ ޹S7Z Vd}"+WVTiuP\ZQ jVTU?uN@PT:@N@PT:@N@PT:@N@8`E-}jb* Lb@̉?S:7;#P)Vd"`E53Ri+зQ} v$^Jf:+ NEIv; %[?,xk2]V$a&+1XiVIV.Ӌ;xj>ZóbT-P)֊x+ ~Vn]VWW+|Z+ˊiRI ۉ=YCP`E0_Q 0_Q jjVT`E5VTWT|'@PT:@N@PT:@N@PT:@N@PT:o_R#¤o_MB-Rc(E@QTEQME5PDH;DLoDj,EP0cdy##d E#KQg!=#=5E E#CQ$GHE!9F,+csȐdPn0iH攂ER G8?n[Ic^o7y#ҠpHM3X# [$oZI.TGC`EJ ZQAKĖ>]m VpZG|1U[_N+h-ATs:w*+6!W95bfp1_g+qT|X+XfF0TB'F"~n+0ćnllo0LWbZ>žoMӊA!)flkuPVhm>3љXCoPAb}X Y| kgEŒc*enRwFZ|ԽvXE]Wx(K%#JX랴Z r:0(h5r% }mW$GWZVxMuVdcNh?2hXakW(;ayh\g)7n1HOu[㸯pAts~EE I|+N⢯*dFsϪݬ&7{P++h,BNs< |W3 opB`쉣% Ы5JWtb/m﹙;#M6{_n.`(ۘVp˜mWζbwUZHБ:hKXq:uZgoGX1SG}zv|-(Nxܼ?Vc׋\ΨpZ7 oFSrgӢXʳ)[f"*Q牴Ywwp Vjp<SV][ҫ3Uj7Obq 켐wBf_5ubW8geb4j,⽻hK:Q{v‚I"q:(hqwS:(nGXOc"-}uPvͷx# #jn⾂uq9z5aDktafY_7YqbER+:.[(񫕴BGߝ;4Zy|^S32+vG8_RBnkŔHw[57|2uh_z~R9k_ᇑ yRY:2S~>tdOS< kXqL<njU#ږ0uZ{m \ ? 3 Ax22 ߢ gmst$6i C@+RՆo1HWe7 B5j#E9\չO-a " &"2_qJD4] nkĆۧ/+t KG?s_kY^}LX2HC-c,!Ca8+:ؘ}0'S'åY[*aEkAE]zl>LhwM[n}WMN|u?"Ԣfϡ+}>ڮ+ªG!mk($,@,Y0~gpq_ȑiǽ FV[e8 F-F\[:[5+|c׊+3+wm3VAn P( V\| ˵VWVC҃'I+ܜY}:ptr%u",Rf_|HeTFGwW ec2 :s܂rct +% -&a+عt̛[{qp^_)xHX1rnaQC  $ ESigns and Symptoms%f  ZMINOR Manifestations Fever Occurs in the majority of cases, usually with the onset of symptoms Usually ranging from 38.4  40.0 C (101-104 F) Arthralgia Usually involves large joints May be mild or severe Group A streptococcal infection Group A beta-haemolytic streptococci may not be seen on a throat swab since the infection may be resolved at the time of onset of ARF symptoms. ASOT  serum reaches a peak level around 3-6 weeks after infection and starts to fall at 6-8 weeks Anti DNase B  reaches a peak level up to 6-8 weeks after infection and starts to fall at around 3 months after the infection. ** Normal antibody titre ranges vary with age and geography **HxvZ Z8Z!0" dZr0Z(ZFZGCucc C4 c  c  g  c s c   a <A  E         Y    W    < aDifficulties with ARF Diagnosis %f  BA combination of signs and symptoms is required to confirm ARF People with ARF do not always present to the health system with symptoms because Symptoms may not be considered serious Transport to the health facility may be difficult Health staff may not recognise the signs and symptoms of ARF ARF may be confused with other illnesses, for example Sore joints may be confused with a sports injury or  growing pains YntxDCYcc< C  C 7 C DC  eTreatment for ARF%f  :Treat the acute illness Benzathine penicillin G injection or Oral Penicillin for 10 days Relieve symptoms Bed rest Relief of arthritis, pain and fever (Paracetamol or Aspirin) Treat chorea (use Carbamazepine or Valproic acid if severe) Anti-heart failure medication (e.g. Diuretics, ACEi, Digoxin if required) VBnncC"ccc c  c C-cc c/cccc ; fARF Management Plan%f  )First dose of Benzathine penicillin G (start secondary prophylaxis) Baseline echocardiogram (if available) ARF alert on medical notes & computer systems (if applicable) Education for person and family Refer to local doctor / health facility Dental examination Long-term secondary prophylaxis plan )x&cccc.ccclC  d    '  9 gManagement of Probable ARF<%f%f%f  LTreat the symptoms } Dose of Benzathine penicillin G } as for ARF Echocardiogram (if available) } Medical officer review after one month, and Repeat echocardiogram (if available) If NOT ARF& cease Benzathine but monitor for ARF symptoms If ARF& continue Benzathine and manage as for ARF:j" xQxkn?C CCCcC C (CCCCCcccec ' hSummary%f  >The Jones Criteria is used to guide the diagnosis of ARF with a combination of MAJOR Manifestations, MINOR Manifestations and evidence of recent GAS Infection A long-term Management Plan should be established to prevent recurrence of ARF and development or worsening of RHD Probable ARF cases should also be monitored ?xOG'g R!-$e   i  jSecondary Prophylaxis%f  Secondary prophylaxis is the terms used to describe regular delivery of antibiotics to prevent recurrence of GAS infection and subsequent development of ARF. Secondary prophylaxis is recommended for people who have had ARF, or who have RHD to Prevent further Group A Streptococcal infections Prevent recurrence ARF Prevent the development or worsening of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD. PxnCc$   kStandard Treatment%f  Benzathine penicillin G 1,200,000 units for ALL people e"30kg 600,000 units for children <30kg Every 3 or 4 weeks (by intramuscular injection) Penicillin V Given if needles cannot be given due to excessive bleeding 250mg twice daily (by mouth) Erythromycin Given if Penicillin allergy has been confirmed by a Medical Officer 250mg twice daily (by mouth)Zwnx ZXnx Zkq<nC CKCK'Cc c  CMC cc C  C [$c$ $c$$^   lConsiderations%f  When should secondary prophylaxis be considered? ARF confirmed by the Revised Jones Criteria RHD confirmed on echocardiogram ARF or RHD not confirmed by the Revised Jones Criteria, but considered highly  probable Precautions Do not give Benzathine Penicillin G or Penicillin V if there is a documented Penicillin allergy Drug reactions are rare Continue secondary prophylaxis during pregnancy Continue secondary prophylaxis during anticoagulation (e.g. with Warfarin)1Pnq<x Pxnx}x1 <}x0  +  V  . x  ~ m$Guidelines for Secondary Prophylaxis%%%f % nCeasing Secondary Prophylaxis%f  Secondary Prophylaxis should only be ceased following: No ARF signs/symptoms for at least 5 years, and Medical Specialist review (Paediatrician / Physician / Cardiologist) and Echocardiogram to establish presence & severity of RHD (if available) D8 " 2x n7cca&CCCCa C * C  C  C  C a)CCC$  G o(Benzathine Penicillin injection delivery))%f ) Assessment and Preparation Confirm person s identity Review known drug allergies Discuss and record any recent ARF or RHD symptoms (refer to medical officer if required) Obtain consent for injection nchC'CCCT4    X   p(Benzathine Penicillin injection delivery))%f ) q Documentation%f  rCalculating Injection Delivery%f  sNotes on Injection Delivery%f  t$Factors affecting Injection Delivery%%%f % u(Strategies to improve Injection Delivery))%f ) Appoint a dedicated staff member at each clinic to oversee secondary prophylaxis coordination Identify people who need secondary prophylaxis Identify local health facility for each person Develop systems for follow-up Provide ongoing education for people who require injections and their families Communicate with local RHD programme and other health service providers Reduce injection pain Discuss alternative therapy issuesx  vwxSummary%f  uAntibiotics need to be present in the body at all times to help prevent GAS infections and prevent recurrent ARF Benzathine penicillin injections should be given unless there are contraindications to injections or documented penicillin allergy Medical Specialist review is required before ceasing secondary prophylaxis Strategies to improve secondary prophylaxis delivery: Good relationships between community and health staff Education for the community and health staff Systems for follow-up Communication between health services Reduce injection pain Document Benzathine Penicillin injections and monitor injection deliveryvxnIZpJ7@q  y  z{ Definitions %f  <Valve Regurgitation suggests that heart valves Are thickened and sticky against the walls of the heart Do not meet in the middle Leak (the blood flows backwards over the valve) Valve Stenosis suggests that heart valves Become stuck to each other Do not allow blood to flow through easily (restricted forward flow) /q<xx+` W+ *f = |Signs and Symptoms of RHD%f  rSymptoms of RHD may not develop for many years A murmur but no symptoms usually suggests mild-moderate disease Symptoms usually suggest moderate-severe disease Symptoms depend upon the type and severity of disease, and may include Breathlessness with exertion or when lying down flat Waking at night feeling breathless Feeling tired General weakness Peripheral oedema/q<xrxGq<xx/  ()G<?    $ }Heart valve involvement%f  .Mitral valve is affected in over 90% of cases of RHD Mitral regurgitation most commonly found in children & adolescents Mitral stenosis represents longer term chronic disease, commonly in adults Most common complication of mitral stenosis is atrial fibrillation Aortic valve next most commonly affected Generally associated with disease of the mitral valve. Tends to develop as a long term complication of aortic regurgitation Tricuspid and pulmonary valves are much less commonly affected Usually affected in very severe RHD when all valves are affected5ZZ Z*Z~x?ZAZ.C7 C    #  }      'A / ~Clinical Examination%f  Investigations%f  .Electrocardiogram (ECG) To determine sinus rhythm Chest X-ray (CXR) To determine size and placement of heart To identify cardiac failure (pulmonary congestion) Echocardiography To identify heart valve damage To estimate severity of disease Useful to compare results with future echocardiogram resultsZZZ\Z Z Z|Z E|   / Key element in RHD Management%f   Secondary prophylaxis Functions of secondary prophylaxis with established RHD Prevent Group A Streptococcal infections Prevent the repeated development of ARF Prevent the development of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD.pZ8ZZG$E8Cc$N   Elements in RHD Management%f   KRHD and Pregnancy%f   MManagement of RHD in Pregnancy%f   QInfective Endocarditis%f   S-Procedures that increase risk of Endocarditis..%f-   TSurgery for RHD%f   "Guidelines for managing Mild RHDN#%f%f%f%f #  &Guidelines for managing Moderate RHD<'%f%f%f '  $Guidelines for managing Severe RHD<%%f%f%f %  Summary%f  RHD presents as damage to the heart valves The mitral valve is most commonly affected, followed by Aortic, Pulmonary and Tricuspid RHD can be mild, moderate or severe RHD may be asymptomatic Management of RHD includes Treatment of cardiac and other symptoms Long-term secondary prophylaxis (to prevent recurrent ARF) Regular medical and cardiology review Management of existing pregnancy Dental assessment, family planning referral4xn    Elements of a Disease Register%f  }A disease register is a list of people who have a common illness or disease. For example: Tuberculosis register HIV/AIDS register Vaccine-preventable diseases register (measles, rubella) Acute Rheumatic Fever & Rheumatic Heart Disease A disease register should be secure so that the information is not lost or damaged A disease register can be a computer database or a paper list[xnx[N0R    >   ~ :Paper Register  Book or List%f   8Computer Register  Database%f   Information on the Register%f  Information to identify each person (clinic or hospital number) Personal information (name, date of birth, gender, contact details) Current disease status (ARF only, or mild, moderate, severe RHD) Diagnoses, date of diagnoses How the diagnosis was made (hospital admission, screening programme) Secondary prophylaxis details (medication, amount received each year) Surgery details Dates for next medical review (or for heart valve surgery) Date and cause of death.x$c/ c *c8+c  ($c$.((,c,00  Notification of ARF and RHD%f  dAll people who have confirmed and suspected ARF and RHD should be notified to the RHD register so that health authorities can undertake the following: Identify high risk individuals who require priority care Coordinate secondary prophylaxis and follow-up programmes Help identify others who may be at risk Provide information on the local rates of disease Fn<   '  3 Sources of Information%f  eThe following sources may contain information on individuals for the RHD Register Benzathine Penicillin injection books Echocardiogram reports Heart valve surgery lists Notes from Medical Specialists, Heart Specialists, dentists and researchers Hospital admission and discharge records (e.g. ICD-9 or ICD-10 coding) School and community screening referrals:fxc)= ) Reports from the Register%f  VLists of individuals needing urgent care Lists of people receiving inadequate levels of secondary prophylaxis Delivery of Benzathine penicillin injections (for each full year on treatment) Specialist clinic lists Echocardiogram and Surgery waiting lists People who are deceased and cause of death Rates of disease for the region or countryjWx  ccc W Summary%f  A Disease Register can be on paper or computer The information should be confidential and secure The information on the register should Help coordinate health care for individuals Help describe the level of disease in the community All confirmed and suspected cases of ARF and RHD should be notified to the register Sources of information for the register may include Benzathine penicillin injection books Echocardiogram reports and surgery lists Hospital admission books and computer systems School screening referralstx`nxn_    #WHO recommendations for RHD Control$$%f $ A strong commitment from local Government A committed and skilled RHD Advisory Group An RHD Register of all people with confirmed and suspected ARF and RHD A well-trained programme coordinator Notification of ARF and RHD to the relevant health authority Well-coordinated secondary prevention activities A priority system to help deliver care to individuals at highest risk Reliable resources including medications and laboratory support Programmes established centrally and expanded regionally*+x0x(  Core Programme Objectives%f   Identify and register individuals with ARF and RHD Standardise and improve delivery of secondary prophylaxis Standardise diagnosis and management of ARF and RHD Provide training and support for health workers Provide support to the community Report on the programme and rates of disease$!q<x!   'Objective 1 - Identify & Register cases,( %f'f ( Collect information on known cases of ARF & RHD Benzathine Penicillin injection books and clinic records Echocardiogram reports and cardiac surgery lists Hospital admission & death reports Identify new cases Health centres or hospital when individuals present with ARF or RHD School health (screening) programmes Antenatal Clinics Maintain a paper or computer register of all people with confirmed or suspected ARF & RHD 0ZnPZ|nZZ0nAZ</{    Z      ,Objective 2 - Optimise Secondary Prophylaxis,- %f!'f - LEstablish secondary prophylaxis delivery Identify people who need secondary prophylaxis Identify health facilities where individuals receive secondary prophylaxis Improve secondary prophylaxis  identify specific barriers to treatment Identify people who do not receive adequate Benzathine penicillin injections (>80% injections) Establish recall and reminder systems Support communication between health facilities Refer new cases to peripheral health facilities for ongoing management Identify people who move between health centres for treatment){nHnn)zG   ' jObjective 3  Training and Support for Health Workers,6 %f*'f5  Standardise guidelines for diagnosis and management of ARF and RHD Revised Jones Criteria for diagnosis of ARF Standardise dosing and delivery of secondary prophylaxis Train health workers Curriculum development Training programmes for students and trained staff Updates for staff in rural and remote areas Communicate Referral of new cases to local community health facilities Update staff about on local ARF/ RHD issues Report on RHD in the communityCZfxZwxZ ZxCew      TB g  x t   >Objective 4  Community Support %f  9Educate and Inform Targeted education for people with ARF and RHD Community education materials (posters & brochures) Manage individuals with ARF & RHD Promote ongoing medical care / echocardiogram / pregnancy counseling / dental care Prioritise treatment for severe cases Cardiac assessment Surgery and supportcn x"Tx&'Mcc"  S    &' : G>Objective 5  Screening for RHD %f  Screening may be undertaken when acute cases are identified and managed, and when time and resources become available. Considerations for screening Who to screened (e.g. school children are easier / RHD may be more common in adults) Methods of diagnosis available (e.g. auscultation & clinical assessment, echocardiogram) Availability of trained staff Processes for reporting RHD cases to the RHD programme Health resources available for long-term management of more RHD cases. xLnvEc  :c<x    A RHD Programme Difficulties%f  Lack of local resources (including dedicated staff) Limited funds and other resources Heavy workloads for primary care health staff Priority of other health issues (e.g. TB, Malaria, HIV/AIDS, respiratory disease) The RHD programme is complex Difficulties around communication with remote health facilities Limited travel to provide training & education Demanding data management Programme expanded too quicklyxnco2 c 3  !  -  Q     + Summary%f  EAn RHD Programme should have Local (Government) commitment A manageable RHD Register Well-trained, dedicated staff at all levels Systems to identify known cases and refer of new cases A priority system for severe cases Secondary Prophylaxis monitoring and improvement Ongoing support for health staff and the community. 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S  6 L   ?@    P*    6HP   z @   R*  H  09g ? 3380___PPT10.@ h(  h h 0+  ?7    X*  h 0/  z 7   Z*  h 6\4   ?@    X*  h 68   z @   Z* H h 09g ? 3380___PPT10.+*'  0L0 & (  ~  s *| 40]H   H  0޽h ? ___f3̙;/f9___PPT10i.a+D='  = @B +  0L0  l(    s *$8 4 F]9    ,66Rwxj  C BA*VF_Group_F_Logo_2COL *`  C 8A State of Geneva9 9 X  C 0AMenziesLogo 0 ~ T  C ,Amcri_logo H  0޽h ? ___f3̙;/f9___PPT10i.Q+D='  = @B +3  0L0 2* (  |  B  ?#" `&i+ @Introduction Acute Rheumatic Fever and Rheumatic Heart DiseasezA '(f'%f'f%f@  V  0޽h ?"` ___f3̙;/f9___PPT10i.s +D='  = @B +  0L0 0 P(  ~  s *Ц 4]      0 4"`zIY   H  0޽h ? 33___PPT10i.QWr+D='  = @B +  0L0 P *(  ~  s * 4]      < 4"`z[   X  s 0A 7 jf2  0Ԕ"`&H  0޽h ? 33___PPT10i.Q+D='  = @B +   0L0 p (    # Lt      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]      < 4"`z[   H  0޽h ? 33___PPT10i.Q+D='  = @B +   0L0  (    # Lh       ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]       6 4"`Z   H  0޽h ? 33___PPT10i.Y0+D='  = @B +   0L0   T(    # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    h   C @A (Disease Progression]% H  0޽h ? 33___PPT10i.QP+D='  = @B +  C 0L0 P(    # L       ? @  5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]       64 4"`,Z   H  0޽h ? 33___PPT10i.Y0+D='  = @B +  0L0  g(  /  B*  ?#" `&i4 /Acute Rheumatic Fever Diagnosis and Management>0'(f'%f/  V  0޽h ?"` ___f3̙;/f9___PPT10i.px+D='  = @B +t%   0L0 s$k$ $$(  x d   #"*d  ) <2 ? C  dC  MM" ' < ?"` C  6ESR e"30mm/hr or CRP e"30mg/LC   MMl % <F ?"` C F>6___PPT9 (! PR interval on ECG&(" C   MM # <P ?"`C  t Arthralgia  C   MM ! < Y ?"`C oFeverC   MM   <S ?C MINOR ManifestationsJZGGG  MM  <l ?C   dC  MMJ  <n ?d  F>6___PPT9 Subcutaneous nodules&(" C   MM  <8 ?C   dC  MMI  << ?d  F>6___PPT9 Erythema marginatum&(" C   MM  <, ?C   (Anti-deoxyribonuclease B (Anti-DNase B) ))C  ) MM  < ?d   "Sydenham s ChoreaC   MM   < ?C  !Anti-streptolysin O titre (ASOT) ""C  " MM   < ?d  s Arthritis  C   MM   < ?C GAS on Throat swab (Culture)C   MM   < ?d rCarditis  C   MM*   < ?C GAS InfectionDZGf3 C G  MM   <d ?d MAJOR ManifestationsJZGfGfG  MM`B  0o ?dZB  s *1 ?dZB  s *1 ?dZB  s *1 ?d  ZB  s *1 ?d  ZB  s *1 ?d  `B  0o ?dd ZB  s *1 ? `B  0o ? ZB   s *1 ?CC ZB ^ s *o ? C `B  0o ?d  `B _ 0o ?C  -  <  ' MAJOR Criteria - signs and symptoms more often associated with ARF MINOR Criteria - signs and symptoms that help support the diagnosis Evidence of recent GAS Infection is required0xE A2aEEfAEfAF a  e  a $ ,    Z,  ?4#" `m     S ^      ? A@  A5% 8c8c     ?4A)BCD|E|| "0e ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H  0޽h ? 7X(=^___PPT10i.̴`+D='  = @B +    0L0     (       <T 4"`Y      S ^,      ? A@  A5% 8c8c     ?4A)BCD|E|| "0e ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H   0޽h ? 7X(=^___PPT10i.̴`+D='  = @B +    0L0   P 06 (  0 0 # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]     0 0 2   D0 2  0  < 4"`zY[   H 0 0޽h ? ___f3̙;/f9___PPT10i.ݴI+D='  = @B +    0L0  ~ p 8 (  8 8 # L'      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]     8 0- 2   D0 2 ~ 8 s *- 4zg    H 8 0޽h ? ___f3̙;/f9___PPT10i.ݴI+D='  = @B +   0L0  x @ (  @ @ # L<      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]     @ 0> 2   D0 2 x @ c $@ 4z   H @ 0޽h ? ___f3̙;/f9___PPT10i.ݴI+D='  = @B +  D 0L0  x  (    # LK      ? @  5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]      0,R 2   D0 2 x  c $T 4z   H  0޽h ? ___f3̙;/f9___PPT10i.ݴI+D='  = @B +    0L0   0 ((  ( (  6h 4"`Y    ( S ^hi      ? A@  A5% 8c8c     ?4A)BCD|E|| "0e ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H ( 0޽h ? ___f3̙;/f9___PPT10i.M+D='  = @B +   0L0  Hj(  H H # Ls      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    ~ H s *t 4zg%   H H 0޽h ? ___f3̙;/f9___PPT10i.% +D='  = @B +   0L0  Pd(  P P # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    x P c $P 4z   H P 0޽h ? ___f3̙;/f9___PPT10i.`)A`+D='  = @B +   0L0  X(  X X # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]     X s * 4Tg    *P@ 0@8`XH X 0޽h ? ___f3̙;/f9___PPT10i. +D='  = @B +   0L0  `(  ` ` # Lh      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]     `  6d 4"`z   H ` 0޽h ? ___f3̙;/f9___PPT10i. #+D='  = @B +  0L0 0 hf(  h. h B  ?#" `&i+ .Secondary Prophylaxis to prevent recurrent ARF>/'(f'%f.  V h 0޽h ?"` ___f3̙;/f9___PPT10i.s +D='  = @B +   0L0 P p~(  p p # Lķ      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]     p  0 4"`z   H p 0޽h ? ___f3̙;/f9___PPT10i.U+D='  = @B +%   0L0 $  p x(  x x # LX      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]     x  `0  ?4#" `z   H x 0޽h ? ___f3̙;/f9___PPT10i.z+D='  = @B +   0L0  (    # L@      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]       6 4"`H   H  0޽h ? 33___PPT10i.ԴC+D='  = @B +  0L0  %d(  +  B0  ?"P ` aAge at first diagnosis of ARF (or RHD) Severity of disease If carditis was present with first ARFbnbC b  7  $ #""oda9    < ? 2  ~v0___PPT106___PPT9 Continue for life c    @@``  < ?72  ~v0___PPT106___PPT9 Severe RHD and after Surgery>  c c c    @@``  <  ? 2  WMinimum of 10 years after last ARF, or Until age 25 years (whichever is longer) NX @cc cc $U     @@``  <  ?7  2 ~v0___PPT106___PPT9 &Mild-moderate RHD (or healed carditis)>  cc $     @@``n   < ?    VMinimum of 5 years after last ARF, or Until age 18 years (whichever is longer) >W ?cc c$T     @@``   <h ?7  ~v0___PPT106___PPT9 ARF (no carditis). cc     @@``   B\= ?  ~v0___PPT106___PPT9 !Duration of secondary prophylaxis$"("g "   @@``   B ?7  ~v0___PPT106___PPT9 Disease Classification$(g    @@``ZB   s *8c ?7ZB  s *8c ?7  ZB  s *8c ?77 ZB  s *8c ? TB  c $ ?7  TB  c $ ?  TB  c $ ?7  TB  c $ ?  TB  c $ ?72 2 Z  BK  ?" ` tTime (years) since last ARF illness Ongoing risk factors (e.g. level of poverty) If medication is received regularly6unCCiC u   00Q "`,k QLength of time for secondary prophylaxis depends on a number of factors includingR0PRaQ    # LV      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]      0W  + < ** Secondary prophylaxis guidelines may vary **.= - =  % 0@]  HWorld Health Organisation guidelines for secondary prophylaxis duration:IIaH  H  0޽h ? ___f3̙;/f9___PPT10i.+D='  = @B +   0L0  d(  x  c $h 4z     # Llh      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H  0޽h ? ___f3̙;/f9___PPT10i.+D='  = @B +   0L0  j(  ~  s *,{ 4z     # L{      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H  0޽h ? ___f3̙;/f9___PPT10i.pjA+D='  = @B +  0L0   ~ (    B  ?"ztld___PPT9F> <Check medication name, dose and expiry date Prepare medication according to the product information Administer 1,200,000 units for all persons e" 30kg Administer 600,000 units for small children <30kg Administer with a size 23-gauge needle Dispose of used needles and syringes in a puncture-proof container. Use a new needle and syringe for each injection Administer medication immediately after preparation dxenxng x+cc8cCK+CKCCk c  c CfC    # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H  0޽h ? ___f3̙;/f9___PPT10i.+D='  = @B +   0L0   0j (    # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    ~  B,  ?"zT Record in the Benzathine penicillin injection book and/or medical notes Dose and batch number Date given and date next due Signature (of person giving injection) Record next date due on a reminder card (if applicable) H[nx9Hc?CCCC' c CCC<G  [  9 H  0޽h ? ___f3̙;/f9___PPT10i.+ȑ+D='  = @B +  0L0 Pk(    B  ?"zT___PPT9 -#Record the number of injectionsPRESCRIBED for the full year 13 injections should be given each year if prescribed every 4 weeks 17 injections should be given each year if prescribed every 3 weeks Count the number of injections GIVEN in the full year 3. Calculate the number of injections GIVEN (10) divided by the number PRESCRIBED (13) and multiply by 100. EXAMPLE: If 13 injections are PRESCRIBED, and 10 were GIVEN: (10 13) x 100 = 77% RECEIVED In this example, 77% of injections were RECEIVED for the individual for the year.>nd$ned6ndxmedxhRc6cCC:C C:CCC  C c0cCc ccc CG g  $G$$G$$C$ $G$(g((g((g(>(g(H     k   `mVW  # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H  0޽h ? ___f3̙;/f9___PPT10i.+ȑ+D='  = @B +   0L0   p! (  5  B  ?"zT qReceiving lessthan 80% of injections places an individual at higher risk of recurrent ARF Follow-up may be required If injections were PRESCRIBED for the full year but none were GIVEN, record 0%. Receiving less than 50% of injections places an individual at extreme risk of recurrent ARF and progression of RHD Immediate intervention is required for this individual. [x8  d[ccO c  c s c 8 e  g 9 9 <=>?  # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H  0޽h ? ___f3̙;/f9___PPT10i.+ȑ+D='  = @B +   0L0  z  (    # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    &  BD  ?"MT RRelationship between the person with ARF/RHD & the health system Education of the person, family & health workers Person / family refusing treatment Person forgetting treatment Difficulty traveling to health facility Pain and fear of injections Health staff workloads and priorities Alternative therapy use / distrust of health service $RxS S H  0޽h ? ___f3̙;/f9___PPT10i. G+D='  = @B +   0L0 j(    # L       ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    ~  s * 4MT   H  0޽h ? ___f3̙;/f9___PPT10i.h+D='  = @B +  0L0  (     B  ?"zTt  Symptoms Skin rash Itchy eyes2 n    %  Bx   ?"  +Treatment Antihistamine (oral or injection)>,x   +  *   `' ? ?"6?@`NNN?N] \Penicillin Allergy%f  H  0޽h ? ___f3̙;/f9___PPT10i.~+D='  = @B +! 0L0 ?(    B+  ?"zTt  -Symptoms Wheezing Hives Itching Swelling of the face and lips Difficulty breathing Vomiting Falling Blood pressure Loss of consciousness Cardiac arrest X n CSCc7 C    #   `4 ? ?"6?@`NNN?N] U Anaphylaxis %f  '  B7  ?"  -Treatment Adrenaline (subcutaneous injection)>.x    -  H  0޽h ? ___f3̙;/f9___PPT10i.~+D='  = @B +  " 0L0 d(    # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    x  c $@ 4zT,   H  0޽h ? ___f3̙;/f9___PPT10i.3+D='  = @B + # 0L0 0i(  1  BK  ?#" `&Y4 1Rheumatic Heart Disease Diagnosis and Management>2'(f'%f1  V  0޽h ?"` ___f3̙;/f9___PPT10i.px+D='  = @B +$ 0L0 P&(  `  s *"`j Z `  s *"`< 9U   c $DX 4'   Rheumatic heart disease is the result of damage to the heart valves which occur after repeated episodes of ARF Early diagnosis and treatment of RHD are important to prevent progression of disease Signs and symptoms may not develop for many years The aim of RHD management is to prevent or delay heart valve surgery RHD can be prevented if ARF is diagnosed and managed early. 50% of people with RHD do not remember having ARFwxx2xwf  v 5 $   `(g ? ?"6?@`NNN?N] V Introduction %f  H  0޽h ? 33___PPT10i.P`+D='  = @B +  % 0L0 pj(    # L4m      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    ~  s * n 4'   H  0޽h ? 33___PPT10i.&C+D='  = @B +  & 0L0 d(    # L~      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    x  c $D 4'`   H  0޽h ? ___f3̙;/f9___PPT10i.+D='  = @B +  ' 0L0 d(    # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    x  c $X 4'   H  0޽h ? ___f3̙;/f9___PPT10i.+D='  = @B +f  ( 0L0 e ]  (     N  ' 1Mitral regurgitation A pansystolic murmur heard loudest at the apex and radiating laterally to the axilla Mitral stenosis A low-pitched, diastolic rumble heard best at the apex with the bell of the stethoscope and with the person lying in the left lateral position. Aortic regurgitation A diastolic blowing decrescendo murmur best heard at the left sternal border with the person sitting up and leaning forward in full expiration. Aortic stenosis A loud, low pitched mid-systolic ejection murmur best heard in the aortic area, radiating to the neck. V   i Tf 2   # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H  0޽h ? 33___PPT10i.=f+D='  = @B +  ) 0L0 j(    # L|      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    ~  s *@ 4'`   H  0޽h ? 33___PPT10i.יp}+D='  = @B +  * 0L0  (      # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]       c $ 4zT   *pbrH   0޽h ? 33___PPT10i.@O+D='  = @B +  + 0L0   0(: (  (N ( B}  ?"'9Y  Effective baseline assessment, education and referral Initial management heart failure (treatment with diuretics and ACEi) atrial fibrillation (Digoxin and anti-coagulation) Routine review and structured care planning Regular secondary prophylaxis Regular clinical assessment and follow-up echocardiography (if available) Dental care and Infective endocarditis prophylaxis plan Family planning referral (for women) Vaccination (if available) Appropriate surgical intervention Special consideration in particular circumstances (e.g. pregnancy)6Jxfn,nexJ%,YQ  !1T6 z ,  "  C  ( # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H ( 0޽h ? 33___PPT10i.+D='  = @B +  F 0L0    (    B  ?"'Y >hThe cardiovascular changes which occur during pregnancy may threaten the health of the woman and the foetus. Changes include increased heart rate and blood volume reduction in systemic and pulmonary resistance increased cardiac output. RHD may be identified for the first time during pregnancy. Highest risk of complications immediately after delivery ~rnnvn|p<  8 G   g    # L      ? @  5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H  0޽h ? 33___PPT10i.+D='  = @B +G  H 0L0 F > 0( (  ( ( B  ?"'Y j\Management generally includes restricting physical activity and salt intake administering secondary prophylaxis (Benzathine penicillin can be continued during pregnancy) avoiding community-acquired infectious diseases education about monitoring own signs and symptoms and seeking care if shortness of breath close monitoring of heart function (specifically in woman who have symptoms of RHD). Special attention should be given to women with high risk RHD including women with mitral and/or aortic stenosis atrial fibrillation prosthetic heart valves those receiving anticoagulant therapy with warfarin. lnSnR:2S0  ~   ( # LD&      ? @  5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H ( 0޽h ? 33___PPT10i.+D='  = @B +g  I 0L0 f ^ P0 (  0  0 Bt+  ?"'Y "Infective Endocarditis is a serious complication of RHD Endocarditis is caused by bacteria in the bloodstream. In RHD, endocarditis most commonly occurs in the mitral or aortic valves Uncommonly occurs during dental or surgical procedures but often the source of the infection is not clear May occur after heart valve surgery Antibiotics prior to dental and surgical procedures are given to help prevent endocarditis. All people with ARF and RHD should have regular dental care to prevent dental decay and the potential risk of endocarditis.8x}Z} #  0 # LP0      ? @  5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    H 0 0޽h ? 33___PPT10i.+D='  = @B +- K 0L0 ,,/@6,(  @ @ # L=      ? @  5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]     @ B  " # <V  @ #"F: 'IVN 9@ <4I ? V  `  MM 8@ <0 ?   Placement of orthodontic bands(#    MM5 7@ <pY ? V  KSurgical procedures of the genitourinary tract in the presence of infection(LK#   L MM 6@ <a ?   *Dental cleaning where bleeding is expected(+*#   + MMK 5@ <l ? V  aVaginal delivery in the presence of infection, prolonged labour or prolonged rupture of membranes(ba#   b MM2 4@ <w ?   .Intra-ligamentary local anaesthetic injections(/.#  &   MM  3@ <8{ ? V  "Cystoscopy and urethral dilatation(#"#   # MM 2@ < ?  &Endodontic surgery and instrumentation('&#   ' MM 1@ < ? V Prostate surgery(#    MM 0@ <4 ?  .Surgical repair or fixation of a fractured jaw(/.#   / MM /@ <0 ? `V %Endoscopic retrograde cholangiography(&%#   & MM  .@ < ?`  #Maxillary or mandibular osteotomies($##   $ MM -@ <( ? V` 1Surgery of the intestinal mucosa or biliary tract(21#   2 MM  ,@ < ? ` #Surgical drainage of dental abscess($##   $ MM  +@ < ? V #Dilatation of oesophageal stricture($##   $ MM *@ < ?  +Initial placement of orthodontic appliances(,+#   , MM )@ <x ? V $Sclerotherapy of oesophageal varices(%$#   % MM (@ <  ?   Gingival surgery(#    MM '@ < ? jV  &Surgery involving the bronchial mucosa('&#   ' MM &@ <0  ?j  Dental implant placement(#    MM %@ < ? Vj &Bronchoscopy with a rigid bronchoscope('&#   ' MM $@ < ? j Periodontal procedures(#    MM #@ <<. ? V Tonsillectomy/adenoidectomy(#    MM "@ <d8 ?  Dental extractions(#    MM !@ <B ? <V OTHER PROCEDURES*#    MM  @ << ?<  DENTAL PROCEDURES*#    MM`B :@ 01 ?<V<`B ;@ 01 ? V `B <@ 01 ?< `B =@ 01 ?V<V `B @@ 01 ?V`B B@ 01 ? < `B F@ 01 ?V`B N@ 01 ?jVj`B V@ 01 ? V `B ^@ 01 ?V`B f@ 01 ?V`B n@ 01 ?`V``B v@ 01 ?V`B ~@ 01 ?V`B @ 01 ? V `B @ 01 ? V `B @ 01 ? V H @ 0޽h ? 33___PPT10i.+D='  = @B +  J 0L0   p8Q (  8 8 # Ld      ? @  5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN 5%  N 5%  N    5%    !"?N@ABC DEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    e 8 BDa  ?"'Y The need for surgery depends on Severity of symptoms Evidence that the heart valves are severely damaged Left ventricular chamber size and function Availability of long-term management after surgery (i.e. anticoagulation) Heart valves can be repaired or replaced Assessment before surgery includes Echocardiogram to assess severity of heart valve damage Complete dental assessment and treatment (if required) Review and management of other health problems (e.g. kidney, vascular and chronic respiratory disease, cancers and obesity) xnLnn La/M  H 8 0޽h ? 33___PPT10i.+D='  = @B + / 0L0  H(  HfR H 0"` l H 6"`@ l H 6"`S RB H s *Dp *V  H 0 @F tHeart valve REPAIR2(2    H 0 @'&F yHeart valve REPLACEMENT2(2     H 0    8Anticoagulation required Longer time before re-operation49(2 9   H 0(  `  QRHD(20     H 0Ć    3No Anticoagulation Shorter time before re-operationJ4(2 4 (  H  ` ? ?"6?@`NNN?N] ZSurgery Outcomes%f  H H 0޽h ? 33___PPT10i.ph+D='  = @B +R , 0L0 QIP0(  0 0 # L      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    W 0 B  ?"'`D<4___PPT9 7Definition - RHD with any trivial to mild valve lesion.$8q<x8 8  TE 0 #"*TE   0 <  ?"`@ D E (With appropriate endocarditis prevention))  ) MM  0 <  ?"`TD @ E !Dental review following diagnosis""  " MM  0 <  ?"`@ i D  $Before ceasing secondary prophylaxis%%  % MM 0 <  ?"`Ti @ D  Specialist medical review   MM  0 <   ?"`@ i  3Every 2 years for children Every 5 years for adults44  4 MM  0 <t  ?"`T @ i  Echocardiogram (if available)   MM  0 <Կ  ?"`@ S   2Every 12 months Earlier if clinical deterioration33  3 MM  0 <  ?"`TS @  7Specialist medical review for children aged to 18 years88  8 MM  0 <  ?"`@ pS  ~By local Medical Officer   MM 0 <d  ?"`Tp@ S  }Primary care management   MM  0 <  ?"`@ p %Long-term prevention of recurrent ARF&&  & MM 0 <  ?"`T@ p {Secondary Prophylaxis   MMfB 0 6o ?T`B 0 01 ?TppfB 0 6o ?TEEfB 0 6o ?TTE`B 0 01 ?@ @ EfB 0 6o ?E`B 0 01 ?TS S ZB 0 s *1 ?T  ZB 0 s *1 ?Ti i ZB 0 s *1 ?TD D H 0 0޽h ? 33___PPT10i. <+D='  = @B + - 0L0 p8u(  8 8 # L4      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abV      8 B  ?"'D<4___PPT9 =Definition - Any moderate valve lesion, no symptoms, and normal LV function with stable metallic prosthetic valves, or children (to 18 years old) with a history of chorea including those with no valve damage>q<x?  x TE 8 #"*TE   8 <  ?"`@ D E (With appropriate endocarditis prevention))  ) MM  8 <)  ?"`TD @ E !Dental review following diagnosis""  " MM  8 <4  ?"`@ i D  $Before ceasing secondary prophylaxis%%  % MM 8 <>  ?"`Ti @ D  Specialist medical review   MM  8 <xP  ?"`@ i  3Every 1 years for children Every 2 years for adults44  4 MM  8 <W  ?"`T @ i  Echocardiogram (if available)   MM  8 <  ?"`@ S   2Every 12 months Earlier if clinical deterioration33  3 MM  8 <f  ?"`TS @  Specialist medical review   MM  8 <i  ?"`@ pS  ~By local Medical Officer   MM 8 <y  ?"`Tp@ S  }Primary care management   MM  8 <s  ?"`@ p %Long-term prevention of recurrent ARF&&  & MM 8 <   ?"`T@ p {Secondary Prophylaxis   MMfB 8 6o ?T`B 8 01 ?TppfB 8 6o ?TEEfB 8 6o ?TTE`B 8 01 ?@ @ EfB 8 6o ?E`B 8 01 ?TS S ZB 8 s *1 ?T  ZB 8 s *1 ?Ti i ZB 8 s *1 ?TD D H 8 0޽h ? 33___PPT10i. <+D='  = @B + . 0L0 @"(  @ @ # Lq      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]     @ BH  ?"s 'v @ K @ Bě  ?"'D<4___PPT9 Definition - Any moderate-severe valve lesion with shortness of breath, tiredness, oedema, angina or syncope and impaired or increased left ventricular function or a history of valve surgery including mitral valvotomy, any valve repair and bio-prosthetic valves (porcine and homograph)2q<x    Td  @ #""Td    @ <<  ?"`@ c d  uManagement Plan   MM @ <  ?"`Tc @ d  Refer to Heart Specialist   MM @ <  ?"`@ S c  uEvery 6 months    MM  @ <̿  ?"`TS @ c  Specialist medical review   MM  @ <`  ?"`@ pS  ~By local Medical Officer   MM  @ <  ?"`Tp@ S  }Primary care management   MM   @ <  ?"`@ p %Long-term prevention of recurrent ARF&&  & MM  @ <  ?"`T@ p {Secondary Prophylaxis   MMfB @ 6o ?T`B @ 01 ?TppfB @ 6o ?Td d fB @ 6o ?TTd `B @ 01 ?@ @ d fB @ 6o ?d `B @ 01 ?TS S ZB @ s *1 ?Tc c H @ 0޽h ? 33___PPT10i. <+D='  = @B +  0 0L0 Pj(  P P # Lp      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]    ~ P s *| 4   H P 0޽h ? ___f3̙;/f9___PPT10i.td+D='  = @B + 1 0L0 X](  X% X < "`&W) -Notification of ARF & RHD and Data ManagementN.0 '(f'f'(f . V X 0޽h ?"` ___f3̙;/f9___PPT10i.u@U+D='  = @B +  2 0L0 `d(  ` ` # L -      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]  -  x ` c $ - 4 K  -  H ` 0޽h ? ___f3̙;/f9___PPT10i.P+D='  = @B +{  3 0L0 z r 0h (  h h # L@-      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]  -   h B-  ?"'6  PPaper registers may contain information for a local health facility, or may provide information to a larger, central computer register. Possible Problems Books may get lost or damaged (not safe) The same people may be included more than once (duplicates) Long lists be difficult to read and analyse Important information may be missingxn / Q   h B\)-  ?" ' Benefits No specialised training required Books and lists can be transported easily External support is not required (e.g. electricity as for computers)2 n    H h 0޽h ? ___f3̙;/f9___PPT10i.޴h+D='  = @B +o  4 0L0 n f Pp (  p p # L3-      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]  -  b p B4-  ?"'  NA computer registers is called a database. A database is able to record specific information for many people. Possible Problems Computers and connections usually cost money Specialised training and support are usually required Electricity and other interruptions cause barriers to use The information may not be easily transportableLxnn$    p BtA-  ?" ' (Benefits The information can be secured (safe) Duplicate entries can be avoided Information can be searched, sorted and updated quickly Reports can be produced automatically2 n $    H p 0޽h ? ___f3̙;/f9___PPT10i.O+D=' - = @B +  5 0L0 pxd(  x x # LJ-      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]  -  x x c $`K- 4' -  H x 0޽h ? ___f3̙;/f9___PPT10i.-Y+D=' - = @B +  6 0L0 j(    # LY-      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]  -  ~  s *Y- 4'YG -  H  0޽h ? ___f3̙;/f9___PPT10i.P++D=' - = @B +  7 0L0 d(    # Lf-      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]  -  x  c $pg- 4'9  -  H  0޽h ? ___f3̙;/f9___PPT10i..fj!+D=' - = @B +  8 0L0 d(    # Ltq-      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]  -  x  c $Lr- 4'  -  H  0޽h ? ___f3̙;/f9___PPT10i..fj!+D=' - = @B +  9 0L0 j(    # L`-      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab]  -  ~  s *Ά 4 -  H  0޽h ? ___f3̙;/f9___PPT10i..fj!+D=' - = @B + : 0L0 (    <- "`'X+ lRHD Control Programmes&0'(f  V  0޽h ?"` ___f3̙;/f9___PPT10i.xo+D=' - = @B +  ; 0L0 0^(     Fؓ-      ? A@  A5% 8c8c     ?4A)BCD|E||c " ?@  `    @ABC DEEFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `abN E5%  N E5%  N F   5%    !"?N@ABC DEFFGHIJK5%LMNOPQRSTUWYZ[ \]^_ `ab }  -  x  c $- 4  -  H  0޽h ? ___f3̙;/f9___PPT10i.8 5+D=' - = @B +  < 0L0 P^(     F0-      ? 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It has been made possible thanks to the financial support of the Vodafone Group Foundation and the International Solidarity, State of Geneva, and assistance from Menzies School of Health Research and the Murdoch Childrens Research Institute.  0    X  Y Introduction f  bRheumatic Heart Disease is the most common cause of heart disease in children and young adults Approximately 15.6 million people affected worldwide Almost 500,000 new cases each year Approx 350,000 deaths each year Most disease occurs in developing countries. Rheumatic Heart Disease is a disease of poverty Rheumatic Heart Disease can be prevented. D`nZxG8  f$ Z  Z Definitions f  Group A beta-haemolytic streptococci (GAS) Humans are exposed to GAS in the environment Throat and skin are common sites of GAS infection GAS infections usually resolve without treatment Untreated GAS infections can lead to acute rheumatic fever in some people.t+nC CCCc"0$  J  [ Definitions f  QAcute Rheumatic Fever (ARF) A delayed auto-immune response following untreated GAS infection Develops after the GAS infection has resolved Commonly affects the joints, heart, central nervous system and skin Most common between the ages of 5 and 15 years Can recur following further untreated GAS infections Rheumatic Heart Disease (RHD) Residual damage to heart valves following recurrent ARF Valves become scarred, stiff, thickened Blood leaks (blood flows backwards through valves which do not close properly) Blood is blocked (blood can not flow through valves which do not open properly)(nn#######l#3## ##0## #$ O  \ Risk Factors %f   Risk factors ARF include Poverty Poor housing, overcrowded housing Lack of adequate health care Untreated GAS infections Risk factor for RHD Recurrent ARF Prevention The first episode of ARF can be prevented by treating GAS infections with penicillin (primary prophylaxis) If the first ARF episode is not prevented, recurrent ARF can be prevented with long-term penicillin (secondary prophylaxis)&Z`nZ!Zn Zn#`#### #  #  # T #  #d##<`  %   ]Disease Progression%f  CControl of Disease%f   ARF and RHD can be prevented by sustainable control strategies including Trained health staff who diagnose and management disease effectively Secondary prophylaxis to prevent further ARF and the development or worsening of RHD. Community education and awareness Screening for unknown RHD in the community. Control strategies should focus on Prompt identification and treatment of GAS infections Identifying people who have had ARF once and preventing further ARF and the development of RHD.IZnZ$ZnH####$##TI E W ! -   ^  _Revised Jones Criteria%f  ARF can be confirmed if certain signs and symptoms are present. The Revised Jones Criteria (below) can help guide the diagnosis.xC$  ; ' `  Revised Jones Criteria%f  The World Health Organisation set the international standard for diagnosis of ARF. First episode or recurrent episode of ARF (no RHD): 2 MAJOR manifestations or 1 MAJOR and 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ARF (with existing RHD): 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ** Individual country guidelines also exist **^xnZZ0 fn]nZ5ZRCC4CAGfEGfcac A  G f E  G fcCAGfEGfcace c%c c C $g$f(A((G(f(E((G(f,c,,a,0C04c44e4 4c4%4c4 8A88C808A8<     bSigns and Symptoms%f  2MAJOR Manifestations Arthritis Painful, swollen joints (usually knees, ankles, wrists, elbows) Very common with ARF, often the first symptom Usually  migratory - disappears from one joint as it starts in another (poly-arthritis), however may just be present in one joint (mono-arthritis). Carditis May present as a heart  murmur Chest pain and/or difficulty breathing may be present in more severe cases 2!xn 0 dnmx Cc(cuccc*ccc Ck c  "   cSigns and Symptoms%f  Sydenham s chorea Twitchy, jerking movements and muscle weakness (most obvious in the face, hands and feet) May occur on both sides or only one side of body More common in teenagers and females (rare after age 20) May be associated with irritability and or depression May begin up to 3-4 months after the streptococcal throat infection, and often occurs without other symptoms Usually resolves within 6 weeks (may last 6 months or more) May recur in females during pregnancyxnC/c+cVcccc&cxk  0  9 6 m  < & dSigns and Symptoms%f  Subcutaneous nodules Painless lumps on the outside surfaces of elbows, wrists, knees, ankles in groups of 3-4 (up to 12) The skin is not red or inflamed Last 1-2 weeks (rarely more than 1 month) Nodules are more common when Carditis is also present. Erythema marginatum Painless, flat pink patches on the skin that spread outward in a circular pattern Usually occurs early, may last months, rarely lasts years Usually on the back or front of body, almost never on the face Hard to see in dark-skinned people.xnPPnCYc c/cc7cc C cx    )    9  >  $ ESigns and Symptoms%f  ZMINOR Manifestations Fever Occurs in the majority of cases, usually with the onset of symptoms Usually ranging from 38.4  40.0 C (101-104 F) Arthralgia Usually involves large joints May be mild or severe Group A streptococcal infection Group A beta-haemolytic streptococci may not be seen on a throat swab since the infection may be resolved at the time of onset of ARF symptoms. ASOT  serum reaches a peak level around 3-6 weeks after infection and starts to fall at 6-8 weeks Anti DNase B  reaches a peak level up to 6-8 weeks after infection and starts to fall at around 3 months after the infection. ** Normal antibody titre ranges vary with age and geography **HxvZ Z8Z!0" dZr0Z(ZFZGCucc C4 c  c  g  c s c   a <A  E         Y    W    < aDifficulties with ARF Diagnosis %f  BA combination of signs and symptoms is required to confirm ARF People with ARF do not always present to the health system with symptoms because Symptoms may not be considered serious Transport to the health facility may be difficult Health staff may not recognise the signs and symptoms of ARF ARF may be confused with other illnesses, for example Sore joints may be confused with a sports injury or  growing pains YntxDCYcc< C  C 7 C DC  eTreatment for ARF%f  :Treat the acute illness Benzathine penicillin G injection or Oral Penicillin for 10 days Relieve symptoms Bed rest Relief of arthritis, pain and fever (Paracetamol or Aspirin) Treat chorea (use Carbamazepine or Valproic acid if severe) Anti-heart failure medication (e.g. Diuretics, ACEi, Digoxin if required) VBnncC"ccc c  c C-cc c/cccc ; fARF Management Plan%f  )First dose of Benzathine penicillin G (start secondary prophylaxis) Baseline echocardiogram (if available) ARF alert on medical notes & computer systems (if applicable) Education for person and family Refer to local doctor / health facility Dental examination Long-term secondary prophylaxis plan )x&cccc.ccclC  d    '  9 gManagement of Probable ARF<%f%f%f  LTreat the symptoms } Dose of Benzathine penicillin G } as for ARF Echocardiogram (if available) } Medical officer review after one month, and Repeat echocardiogram (if available) If NOT ARF& cease Benzathine but monitor for ARF symptoms If ARF& continue Benzathine and manage as for ARF:j" xQxkn?C CCCcC C (CCCCCcccec ' hSummary%f  >The Jones Criteria is used to guide the diagnosis of ARF with a combination of MAJOR Manifestations, MINOR Manifestations and evidence of recent GAS Infection A long-term Management Plan should be established to prevent recurrence of ARF and development or worsening of RHD Probable ARF cases should also be monitored ?xOG'g R!-$e   i  jSecondary Prophylaxis%f  Secondary prophylaxis is the terms used to describe regular delivery of antibiotics to prevent recurrence of GAS infection and subsequent development of ARF. Secondary prophylaxis is recommended for people who have had ARF, or who have RHD to Prevent further Group A Streptococcal infections Prevent recurrence ARF Prevent the development or worsening of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD. PxnCc$   kStandard Treatment%f  Benzathine penicillin G 1,200,000 units for ALL people e"30kg 600,000 units for children <30kg Every 3 or 4 weeks (by intramuscular injection) Penicillin V Given if needles cannot be given due to excessive bleeding 250mg twice daily (by mouth) Erythromycin Given if Penicillin allergy has been confirmed by a Medical Officer 250mg twice daily (by mouth)Zwnx ZXnx Zkq<nC CKCK'Cc c  CMC cc C  C [$c$ $c$$^   lConsiderations%f  When should secondary prophylaxis be considered? ARF confirmed by the Revised Jones Criteria RHD confirmed on echocardiogram ARF or RHD not confirmed by the Revised Jones Criteria, but considered highly  probable Precautions Do not give Benzathine Penicillin G or Penicillin V if there is a documented Penicillin allergy Drug reactions are rare Continue secondary prophylaxis during pregnancy Continue secondary prophylaxis during anticoagulation (e.g. with Warfarin)1Pnq<x Pxnx}x1 <}x0  +  V  . x  ~ m$Guidelines for Secondary Prophylaxis%%%f % nCeasing Secondary Prophylaxis%f  Secondary Prophylaxis should only be ceased following: No ARF signs/symptoms for at least 5 years, and Medical Specialist review (Paediatrician / Physician / Cardiologist) and Echocardiogram to establish presence & severity of RHD (if available) D8 " 2x n7cca&CCCCa C * C  C  C  C a)CCC$  G o(Benzathine Penicillin injection delivery))%f ) Assessment and Preparation Confirm person s identity Review known drug allergies Discuss and record any recent ARF or RHD symptoms (refer to medical officer if required) Obtain consent for injection nchC'CCCT4    X   p(Benzathine Penicillin injection delivery))%f ) q Documentation%f  rCalculating Injection Delivery%f  sNotes on Injection Delivery%f  t$Factors affecting Injection Delivery%%%f % u(Strategies to improve Injection Delivery))%f ) Appoint a dedicated staff member at each clinic to oversee secondary prophylaxis coordination Identify people who need secondary prophylaxis Identify local health facility for each person Develop systems for follow-up Provide ongoing education for people who require injections and their families Communicate with local RHD programme and other health service providers Reduce injection pain Discuss alternative therapy issuesx  vwxSummary%f  uAntibiotics need to be present in the body at all times to help prevent GAS infections and prevent recurrent ARF Benzathine penicillin injections should be given unless there are contraindications to injections or documented penicillin allergy Medical Specialist review is required before ceasing secondary prophylaxis Strategies to improve secondary prophylaxis delivery: Good relationships between community and health staff Education for the community and health staff Systems for follow-up Communication between health services Reduce injection pain Document Benzathine Penicillin injections and monitor injection deliveryvxnIZpJ7@q  y  z{ Definitions %f  <Valve Regurgitation suggests that heart valves Are thickened and sticky against the walls of the heart Do not meet in the middle Leak (the blood flows backwards over the valve) Valve Stenosis suggests that heart valves Become stuck to each other Do not allow blood to flow through easily (restricted forward flow) /q<xx+` W+ *f = |Signs and Symptoms of RHD%f  rSymptoms of RHD may not develop for many years A murmur but no symptoms usually suggests mild-moderate disease Symptoms usually suggest moderate-severe disease Symptoms depend upon the type and severity of disease, and may include Breathlessness with exertion or when lying down flat Waking at night feeling breathless Feeling tired General weakness Peripheral oedema/q<xrxGq<xx/  ()G<?    $ }Heart valve involvement%f  .Mitral valve is affected in over 90% of cases of RHD Mitral regurgitation most commonly found in children & adolescents Mitral stenosis represents longer term chronic disease, commonly in adults Most common complication of mitral stenosis is atrial fibrillation Aortic valve next most commonly affected Generally associated with disease of the mitral valve. Tends to develop as a long term complication of aortic regurgitation Tricuspid and pulmonary valves are much less commonly affected Usually affected in very severe RHD when all valves are affected5ZZ Z*Z~x?ZAZ.C7 C    #  }      'A / ~Clinical Examination%f  Investigations%f  .Electrocardiogram (ECG) To determine sinus rhythm Chest X-ray (CXR) To determine size and placement of heart To identify cardiac failure (pulmonary congestion) Echocardiography To identify heart valve damage To estimate severity of disease Useful to compare results with future echocardiogram resultsZZZ\Z Z Z|Z E|   / Key element in RHD Management%f   Secondary prophylaxis Functions of secondary prophylaxis with established RHD Prevent Group A Streptococcal infections Prevent the repeated development of ARF Prevent the development of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD.pZ8ZZG$E8Cc$N   Elements in RHD Management%f   KRHD and Pregnancy%f   MManagement of RHD in Pregnancy%f   QInfective Endocarditis%f   S-Procedures that increase risk of Endocarditis..%f-   TSurgery for RHD%f   "Guidelines for managing Mild RHDN#%f%f%f%f #  &Guidelines for managing Moderate RHD<'%f%f%f '  $Guidelines for managing Severe RHD<%%f%f%f %  Summary%f  RHD presents as damage to the heart valves The mitral valve is most commonly affected, followed by Aortic, Pulmonary and Tricuspid RHD can be mild, moderate or severe RHD may be asymptomatic Management of RHD includes Treatment of cardiac and other symptoms Long-term secondary prophylaxis (to prevent recurrent ARF) Regular medical and cardiology review Management of existing pregnancy Dental assessment, family planning referral4xn    Elements of a Disease Register%f  }A disease register is a list of people who have a common illness or disease. For example: Tuberculosis register HIV/AIDS register Vaccine-preventable diseases register (measles, rubella) Acute Rheumatic Fever & Rheumatic Heart Disease A disease register should be secure so that the information is not lost or damaged A disease register can be a computer database or a paper list[xnx[N0R    >   ~ :Paper Register  Book or List%f   8Computer Register  Database%f   Information on the Register%f  Information to identify each person (clinic or hospital number) Personal information (name, date of birth, gender, contact details) Current disease status (ARF only, or mild, moderate, severe RHD) Diagnoses, date of diagnoses How the diagnosis was made (hospital admission, screening programme) Secondary prophylaxis details (medication, amount received each year) Surgery details Dates for next medical review (or for heart valve surgery) Date and cause of death.x$c/ c *c8+c  ($c$.((,c,00  Notification of ARF and RHD%f  dAll people who have confirmed and suspected ARF and RHD should be notified to the RHD register so that health authorities can undertake the following: Identify high risk individuals who require priority care Coordinate secondary prophylaxis and follow-up programmes Help identify others who may be at risk Provide information on the local rates of disease Fn<   '  3 Sources of Information%f  eThe following sources may contain information on individuals for the RHD Register Benzathine Penicillin injection books Echocardiogram reports Heart valve surgery lists Notes from Medical Specialists, Heart Specialists, dentists and researchers Hospital admission and discharge records (e.g. ICD-9 or ICD-10 coding) School and community screening referrals:fxc)= ) Reports from the Register%f  VLists of individuals needing urgent care Lists of people receiving inadequate levels of secondary prophylaxis Delivery of Benzathine penicillin injections (for each full year on treatment) Specialist clinic lists Echocardiogram and Surgery waiting lists People who are deceased and cause of death Rates of disease for the region or countryjWx  ccc W Summary%f  A Disease Register can be on paper or computer The information should be confidential and secure The information on the register should Help coordinate health care for individuals Help describe the level of disease in the community All confirmed and suspected cases of ARF and RHD should be notified to the register Sources of information for the register may include Benzathine penicillin injection books Echocardiogram reports and surgery lists Hospital admission books and computer systems School screening referralstx`nxn_    #WHO recommendations for RHD Control$$%f $ A strong commitment from local Government A committed and skilled RHD Advisory Group An RHD Register of all people with confirmed and suspected ARF and RHD A well-trained programme coordinator Notification of ARF and RHD to the relevant health authority Well-coordinated secondary prevention activities A priority system to help deliver care to individuals at highest risk Reliable resources including medications and laboratory support Programmes established centrally and expanded regionally*+x0x(  Core Programme Objectives%f   Identify and register individuals with ARF and RHD Standardise and improve delivery of secondary prophylaxis Standardise diagnosis and management of ARF and RHD Provide training and support for health workers Provide support to the community Report on the programme and rates of disease$!q<x!   'Objective 1 - Identify & Register cases,( %f'f ( Collect information on known cases of ARF & RHD Benzathine Penicillin injection books and clinic records Echocardiogram reports and cardiac surgery lists Hospital admission & death reports Identify new cases Health centres or hospital when individuals present with ARF or RHD School health (screening) programmes Antenatal Clinics Maintain a paper or computer register of all people with confirmed or suspected ARF & RHD 0ZnPZ|nZZ0nAZ</{    Z      ,Objective 2 - Optimise Secondary Prophylaxis,- %f!'f - LEstablish secondary prophylaxis delivery Identify people who need secondary prophylaxis Identify health facilities where individuals receive secondary prophylaxis Improve secondary prophylaxis  identify specific barriers to treatment Identify people who do not receive adequate Benzathine penicillin injections (>80% injections) Establish recall and reminder systems Support communication between health facilities Refer new cases to peripheral health facilities for ongoing management Identify people who move between health centres for treatment){nHnn)zG   ' jObjective 3  Training and Support for Health Workers,6 %f*'f5  Standardise guidelines for diagnosis and management of ARF and RHD Revised Jones Criteria for diagnosis of ARF Standardise dosing and delivery of secondary prophylaxis Train health workers Curriculum development Training programmes for students and trained staff Updates for staff in rural and remote areas Communicate Referral of new cases to local community health facilities Update staff about on local ARF/ RHD issues Report on RHD in the communityCZfxZwxZ ZxCew      TB g  x t   >Objective 4  Community Support %f  9Educate and Inform Targeted education for people with ARF and RHD Community education materials (posters & brochures) Manage individuals with ARF & RHD Promote ongoing medical care / echocardiogram / pregnancy counseling / dental care Prioritise treatment for severe cases Cardiac assessment Surgery and supportcn x"Tx&'Mcc"  S    &' : G>Objective 5  Screening for RHD %f  Screening may be undertaken when acute cases are identified and managed, and when time and resources become available. Considerations for screening Who to screened (e.g. school children are easier / RHD may be more common in adults) Methods of diagnosis available (e.g. auscultation & clinical assessment, echocardiogram) Availability of trained staff Processes for reporting RHD cases to the RHD programme Health resources available for long-term management of more RHD cases. xLnvEc  :c<x    A RHD Programme Difficulties%f  Lack of local resources (including dedicated staff) Limited funds and other resources Heavy workloads for primary care health staff Priority of other health issues (e.g. TB, Malaria, HIV/AIDS, respiratory disease) The RHD programme is complex Difficulties around communication with remote health facilities Limited travel to provide training & education Demanding data management Programme expanded too quicklyxnco2 c 3  !  -  Q     + Summary%f  EAn RHD Programme should have Local (Government) commitment A manageable RHD Register Well-trained, dedicated staff at all levels Systems to identify known cases and refer of new cases A priority system for severe cases Secondary Prophylaxis monitoring and improvement Ongoing support for health staff and the community. Z%0x(%    fH<  . 7 $ h /4            !!""##$$%%&&''(())**++,,--..//00112233445566778899::;;<<==>>??@@AABDCFDHENFPHRIUJVK  0N0  6(    s *54 F]9   ,66RwxX  C 0AMenziesLogo *xH  0޽h ? ___f3̙;/f9___PPT10i.Q+D=' = @B +rQɴWs -xV1(A  D/ 0 """)))UUUMMMBBB999|PP3f333f3333f3ffffff3f̙3ff333f333333333f33333333f33f3ff3f3f3f3333f33̙33333f333333f3333f3ffffff3f33ff3f3f3f3fff3ffffffffff3ffff̙fff3fffff3fff333f3f3ff3ff33f̙̙3̙ff̙̙̙3f̙3f333f3333f3ffffff3f̙3f3f3f333f3333f3ffffff3f̙3f3ffffffffff!___www    """)))UUUMMMBBB999|PP3f333f3333f3ffffff3f̙3ff333f333333333f33333333f33f3ff3f3f3f3333f33̙33333f333333f3333f3ffffff3f33ff3f3f3f3fff3ffffffffff3ffff̙fff3fffff3fff333f3f3ff3ff33f̙̙3̙ff̙̙̙3f̙3f333f3333f3ffffff3f̙3f3f3f333f3333f3ffffff3f̙3f3ffffffffff!___www4'A x(xKʦ """)))UUUMMMBBB999|PP3f3333f333ff3fffff3f3f̙f3333f3333333333f3333333f3f33ff3f3f3f3333f3333333f3̙33333f333ff3ffffff3f33f3ff3f3f3ffff3fffffffff3fffffff3f̙ffff3ff333f3ff33fff33f3ff̙3f3f3333f333ff3fffff̙̙3̙f̙̙̙3f̙3f3f3333f333ff3fffff3f3f̙3ffffffffff!___wwwCCCCCCCCCCCCCCCCCCCCCCCCC㔽mmmmmmGG 㔔mmmmmm______________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________________Slide 2Slide 3 Introduction Definitions Definitions Risk FactorsDisease ProgressionControl of Disease Slide 10Revised Jones CriteriaRevised Jones CriteriaSigns and SymptomsSigns and SymptomsSigns and SymptomsSigns and Symptoms Difficulties with ARF DiagnosisTreatment for ARFARF Management PlanManagement of Probable ARFSummary Slide 22Secondary ProphylaxisStandard TreatmentConsiderations%Guidelines for Secondary ProphylaxisCeasing Secondary Prophylaxis)Benzathine Penicillin injection delivery)Benzathine Penicillin injection deliveryDocumentationCalculating Injection DeliveryNotes on Injection Delivery%Factors affecting Injection Delivery)Strategies to improve Injection Delivery Slide 35 Slide 36Summary Slide 38 Slide 39 DefinitionsSigns and Symptoms of RHDHeart valve involvementClinical ExaminationInvestigationsKey element in RHD ManagementElements in RHD ManagementRHD and PregnancyManagement of RHD in PregnancyInfective Endocarditis.Procedures that increase risk of EndocarditisSurgery for RHD Slide 52#Guidelines for managing Mild RHD'Guidelines for managing Moderate RHD%Guidelines for managing Severe RHDSummary Slide 57Elements of a Disease RegisterPaper Register Book or ListComputer Register DatabaseInformation on the RegisterNotification of ARF and RHDSources of InformationReports from the RegisterSummary Slide 66$WHO recommendations for RHD ControlCore Programme Objectives(Objective 1 - Identify & Register cases-Objective 2 - Optimise Secondary Prophylaxis6Objective 3 Training and Support for Health Workers Objective 4 Community Support Objective 5 Screening for RHDRHD Programme DifficultiesSummary  Fonts UsedDesign Template Slide TitlesK,#IO7l)xeԄO3:%G>o}Y,ej̦NA'ҝNg_&쮡Ns 5mSZ*vʫɿ/u.#Ӯ+=x[-Ww[}w?~3tsNeXmk+ԦFwFTK<αS˿ugsT'^M,GؒdZ3:,{ĆOwgf_v(֌cwMʪ5G1rG;?Bϫ[pm}[du\fަ2knCo5=QE?l[SlOS8t*]vFE2>7}Mzf)TI%)$IJI$RI$I%)d]λN}gu=AYʎ3ڵiIW+~~؈[w96|ZWɏjγdɩM͍}˨]~E~A7[^ڝVO;)oϳeW_*h?яؾjdG6z=ecr?cјGC'ݯKOfZXQ'};S`;wLΖ /u;6ઽWS}j'5pٶƺ_w+ G&{}~"˟7}?`>W힍ol'_Y-zqooC\?s'_Uzza|ʛU ui3nJF6kZw1Y[ hth;J'ӝ߭l?=[w?¬^CW=߱z}^=ޗ7z>§KKb1XY,8̷n=_eiQ2FG }f#RDWwql'W [wCcڇ]Wi\;(вrCC" }!1AQa"q2#BR$3br %&'()*456789:CDEFGHIJSTUVWXYZcdefghijstuvwxyz w!1AQaq"2B #3Rbr $4%&'()*56789:CDEFGHIJSTUVWXYZcdefghijstuvwxyz ?(((OX=:Wu M+Jmf5-F/>{B{<*TMrnM$ն-[z '&)5)IɤRNdrvJ-[-Lju x].Mi-QY&oz ST~nE.DŖBlPi(Uw5@}u,(YafujX=Jd8Tܿ{+8`oɳ >SN5&Te̛N6i`QEo 3C- 3C-WgV&}sh3P+BcFa:WÕR5Զʺp?OKN@I!m[h?Ȱž|ox7zT sxz֝鰾喝gnY77䝢3|IVx[YDlwN2Jߋ4@|1=_DpRun8fyvQ7JXU E̕IŸ;=_q2qU<> F#ZoӥJ2);Z1NRj)}rWOm8iFG.mmkrP-$j/~ik8 ^W6^~9kK az͐fAwb$_`3_߱Cq¾)I4 W'ƽ N5iIof{yxC<w6wZ&օ٦ۣf=ŘJF>z*BE UUjt^I;*p{E EK_p 6mLf~ V&<n*L%\]\J xNB4ԏ,*Mu~=CFյ kZw<5jp/4-VB4]]i4<@n#y mgoi/ٳF?ekJ&}M^sfU˄tK_Pφu@l.4<>23??ï~`1y6*jBvpN[etR[[x$, ؅c)ԥQ%_ ]F1`q9bhߒ5(գ:jѩ? 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It has been made possible thanks to the support of the Vodafone Group Foundation and the International Solidarity, State of Geneva, and the ongoing support from Menzies School of Health Research, Caritas Australia, Cure Kids and Fiji Water. 0    X  Y Introduction f  bRheumatic Heart Disease is the most common cause of heart disease in children and young adults Approximately 15.6 million people affected worldwide Almost 500,000 new cases each year Approx 350,000 deaths each year Most disease occurs in developing countries. Rheumatic Heart Disease is a disease of poverty Rheumatic Heart Disease can be prevented. D`nZxG8  f$ Z  Z Definitions f  Group A beta-haemolytic streptococci (GAS) Humans are exposed to GAS in the environment Throat and skin are common sites of GAS infection GAS infections usually resolve without treatment Untreated GAS infections can lead to acute rheumatic fever in some people.t+nC CCCc"0$  J  [ Definitions f  QAcute Rheumatic Fever (ARF) A delayed auto-immune response following untreated GAS infection Develops after the GAS infection has resolved Commonly affects the joints, heart, central nervous system and skin Most common between the ages of 5 and 15 years Can recur following further untreated GAS infections Rheumatic Heart Disease (RHD) Residual damage to heart valves following recurrent ARF Valves become scarred, stiff, thickened Blood leaks (blood flows backwards through valves which do not close properly) Blood is blocked (blood can not flow through valves which do not open properly)(nn#######l#3## ##0## #$ O  \ Risk Factors %f   Risk factors ARF include Poverty Poor housing, overcrowded housing Lack of adequate health care Untreated GAS infections Risk factor for RHD Recurrent ARF Prevention The first episode of ARF can be prevented by treating GAS infections with penicillin (primary prophylaxis) If the first ARF episode is not prevented, recurrent ARF can be prevented with long-term penicillin (secondary prophylaxis)&Z`nZ!Zn Zn#`#### #  #  # T #  #d##<`  %   ]Disease Progression%f  CControl of Disease%f   ARF and RHD can be prevented by sustainable control strategies including Trained health staff who diagnose and management disease effectively Secondary prophylaxis to prevent further ARF and the development or worsening of RHD. Community education and awareness Screening for unknown RHD in the community. Control strategies should focus on Prompt identification and treatment of GAS infections Identifying people who have had ARF once and preventing further ARF and the development of RHD.IZnZ$ZnH####$##TI E W ! -   ^  _Revised Jones Criteria%f  ARF can be confirmed if certain signs and symptoms are present. The Revised Jones Criteria (below) can help guide the diagnosis.xC$  ; ' `Revised Jones Criteria%f  The World Health Organisation set the international standard for diagnosis of ARF. First episode or recurrent episode of ARF (no RHD): 2 MAJOR manifestations or 1 MAJOR and 2 MINOR manifestations and Evidence of pr                          ! " # $ % & ' ( ) * + , - . / 0 1 2 3 4 5 6 7 8 9 : ; < = > ? @ A B C D E F G H I J K L M N O P Q R S T U V W X Y Z [ \ ] ^ _ ` a b c d e f g h i j k l m n o p q r s t u v w x y { | } ~  eceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ARF (with existing RHD): 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ** Individual country guidelines also exist **^xnZZ0 fn]nZ5ZRCC4CAGfEGfcac A  G f E  G fcCAGfEGfcace c%c c C $g$f(A((G(f(E((G(f,c,,a,0C04c44e4 4c4%4c4 8A88C808A8<     bSigns and Symptoms%f  2MAJOR Manifestations Arthritis Painful, swollen joints (usually knees, ankles, wrists, elbows) Very common with ARF, often the first symptom Usually  migratory - disappears from one joint as it starts in another (poly-arthritis), however may just be present in one joint (mono-arthritis). Carditis May present as a heart  murmur Chest pain and/or difficulty breathing may be present in more severe cases 2!xn 0 dnmx Cc(cuccc*ccc Ck c  "   cSigns and Symptoms%f  Sydenham s chorea Twitchy, jerking movements and muscle weakness (most obvious in the face, hands and feet) May occur on both sides or only one side of body More common in teenagers and females (rare after age 20) May be associated with irritability and or depression May begin up to 3-4 months after the streptococcal throat infection, and often occurs without other symptoms Usually resolves within 6 weeks (may last 6 months or more) May recur in females during pregnancyxnC/c+cVcccc&cxk  0  9 6 m  < & dSigns and Symptoms%f  Subcutaneous nodules Painless lumps on the outside surfaces of elbows, wrists, knees, ankles in groups of 3-4 (up to 12) The skin is not red or inflamed Last 1-2 weeks (rarely more than 1 month) Nodules are more common when Carditis is also present. Erythema marginatum Painless, flat pink patches on the skin that spread outward in a circular pattern Usually occurs early, may last months, rarely lasts years Usually on the back or front of body, almost never on the face Hard to see in dark-skinned people.xnPPnCYc c/cc7cc C cx    )    9  >  $ ESigns and Symptoms%f  ZMINOR Manifestations Fever Occurs in the majority of cases, usually with the onset of symptoms Usually ranging from 38.4  40.0 C (101-104 F) Arthralgia Usually involves large joints May be mild or severe Group A streptococcal infection Group A beta-haemolytic streptococci may not be seen on a throat swab since the infection may be resolved at the time of onset of ARF symptoms. ASOT  serum reaches a peak level around 3-6 weeks after infection and starts to fall at 6-8 weeks Anti DNase B  reaches a peak level up to 6-8 weeks after infection and starts to fall at around 3 months after the infection. ** Normal antibody titre ranges vary with age and geography **HxvZ Z8Z!0" dZr0Z(ZFZGCucc C4 c  c  g  c s c   a <A  E         Y    W    < aDifficulties with ARF Diagnosis %f  BA combination of signs and symptoms is required to confirm ARF People with ARF do not always present to the health system with symptoms because Symptoms may not be considered serious Transport to the health facility may be difficult Health staff may not recognise the signs and symptoms of ARF ARF may be confused with other illnesses, for example Sore joints may be confused with a sports injury or  growing pains YntxDCYcc< C  C 7 C DC  eTreatment for ARF%f  :Treat the acute illness Benzathine penicillin G injection or Oral Penicillin for 10 days Relieve symptoms Bed rest Relief of arthritis, pain and fever (Paracetamol or Aspirin) Treat chorea (use Carbamazepine or Valproic acid if severe) Anti-heart failure medication (e.g. Diuretics, ACEi, Digoxin if required) VBnncC"ccc c  c C-cc c/cccc ; fARF Management Plan%f  )First dose of Benzathine penicillin G (start secondary prophylaxis) Baseline echocardiogram (if available) ARF alert on medical notes & computer systems (if applicable) Education for person and family Refer to local doctor / health facility Dental examination Long-term secondary prophylaxis plan )x&cccc.ccclC  d    '  9 gManagement of Probable ARF<%f%f%f  LTreat the symptoms } Dose of Benzathine penicillin G } as for ARF Echocardiogram (if available) } Medical officer review after one month, and Repeat echocardiogram (if available) If NOT ARF& cease Benzathine but monitor for ARF symptoms If ARF& continue Benzathine and manage as for ARF:j" xQxkn?C CCCcC C (CCCCCcccec ' hSummary%f  >The Jones Criteria is used to guide the diagnosis of ARF with a combination of MAJOR Manifestations, MINOR Manifestations and evidence of recent GAS Infection A long-term Management Plan should be established to prevent recurrence of ARF and development or worsening of RHD Probable ARF cases should also be monitored ?xOG'g R!-$e   i  jSecondary Prophylaxis%f  Secondary prophylaxis is the terms used to describe regular delivery of antibiotics to prevent recurrence of GAS infection and subsequent development of ARF. Secondary prophylaxis is recommended for people who have had ARF, or who have RHD to Prevent further Group A Streptococcal infections Prevent recurrence ARF Prevent the development or worsening of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD. PxnCc$   kStandard Treatment%f  Benzathine penicillin G 1,200,000 units for ALL people e"30kg 600,000 units for children <30kg Every 3 or 4 weeks (by intramuscular injection) Penicillin V Given if needles cannot be given due to excessive bleeding 250mg twice daily (by mouth) Erythromycin Given if Penicillin allergy has been confirmed by a Medical Officer 250mg twice daily (by mouth)Zwnx ZXnx Zkq<nC CKCK'Cc c  CMC cc C  C [$c$ $c$$^   lConsiderations%f  When should secondary prophylaxis be considered? ARF confirmed by the Revised Jones Criteria RHD confirmed on echocardiogram ARF or RHD not confirmed by the Revised Jones Criteria, but considered highly  probable Precautions Do not give Benzathine Penicillin G or Penicillin V if there is a documented Penicillin allergy Drug reactions are rare Continue secondary prophylaxis during pregnancy Continue secondary prophylaxis during anticoagulation (e.g. with Warfarin)1Pnq<x Pxnx}x1 <}x0  +  V  . x  ~ m$Guidelines for Secondary Prophylaxis%%%f % nCeasing Secondary Prophylaxis%f  Secondary Prophylaxis should only be ceased following: No ARF signs/symptoms for at least 5 years, and Medical Specialist review (Paediatrician / Physician / Cardiologist) and Echocardiogram to establish presence & severity of RHD (if available) D8 " 2x n7cca&CCCCa C * C  C  C  C a)CCC$  G o(Benzathine Penicillin injection delivery))%f ) Assessment and Preparation Confirm person s identity Review known drug allergies Discuss and record any recent ARF or RHD symptoms (refer to medical officer if required) Obtain consent for injection nchC'CCCT4    X   p(Benzathine Penicillin injection delivery))%f ) q Documentation%f  rCalculating Injection Delivery%f  sNotes on Injection Delivery%f  t$Factors affecting Injection Delivery%%%f % u(Strategies to improve Injection Delivery))%f ) Appoint a dedicated staff member at each clinic to oversee secondary prophylaxis coordination Identify people who need secondary prophylaxis Identify local health facility for each person Develop systems for follow-up Provide ongoing education for people who require injections and their families Communicate with local RHD programme and other health service providers Reduce injection pain Discuss alternative therapy issuesx  vwxSummary%f  uAntibiotics need to be present in the body at all times to help prevent GAS infections and prevent recurrent ARF Benzathine penicillin injections should be given unless there are contraindications to injections or documented penicillin allergy Medical Specialist review is required before ceasing secondary prophylaxis Strategies to improve secondary prophylaxis delivery: Good relationships between community and health staff Education for the community and health staff Systems for follow-up Communication between health services Reduce injection pain Document Benzathine Penicillin injections and monitor injection deliveryvxnIZpJ7@q  y  z{ Definitions %f  <Valve Regurgitation suggests that heart valves Are thickened and sticky against the walls of the heart Do not meet in the middle Leak (the blood flows backwards over the valve) Valve Stenosis suggests that heart valves Become stuck to each other Do not allow blood to flow through easily (restricted forward flow) /q<xx+` W+ *f = |Signs and Symptoms of RHD%f  rSymptoms of RHD may not develop for many years A murmur but no symptoms usually suggests mild-moderate disease Symptoms usually suggest moderate-severe disease Symptoms depend upon the type and severity of disease, and may include Breathlessness with exertion or when lying down flat Waking at night feeling breathless Feeling tired General weakness Peripheral oedema/q<xrxGq<xx/  ()G<?    $ }Heart valve involvement%f  .Mitral valve is affected in over 90% of cases of RHD Mitral regurgitation most commonly found in children & adolescents Mitral stenosis represents longer term chronic disease, commonly in adults Most common complication of mitral stenosis is atrial fibrillation Aortic valve next most commonly affected Generally associated with disease of the mitral valve. Tends to develop as a long term complication of aortic regurgitation Tricuspid and pulmonary valves are much less commonly affected Usually affected in very severe RHD when all valves are affected5ZZ Z*Z~x?ZAZ.C7 C    #  }      'A / ~Clinical Examination%f  Investigations%f  .Electrocardiogram (ECG) To determine sinus rhythm Chest X-ray (CXR) To determine size and placement of heart To identify cardiac failure (pulmonary congestion) Echocardiography To identify heart valve damage To estimate severity of disease Useful to compare results with future echocardiogram resultsZZZ\Z Z Z|Z E|   / Key element in RHD Management%f   Secondary prophylaxis Functions of secondary prophylaxis with established RHD Prevent Group A Streptococcal infections Prevent the repeated development of ARF Prevent the development of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD.pZ8ZZG$E8Cc$N   Elements in RHD Management%f   KRHD and Pregnancy%f   MManagement of RHD in Pregnancy%f   QInfective Endocarditis%f   S-Procedures that increase risk of Endocarditis..%f-   TSurgery for RHD%f   "Guidelines for managing Mild RHDN#%f%f%f%f #  &Guidelines for managing Moderate RHD<'%f%f%f '  $Guidelines for managing Severe RHD<%%f%f%f %  Summary%f  RHD presents as damage to the heart valves The mitral valve is most commonly affected, followed by Aortic, Pulmonary and Tricuspid RHD can be mild, moderate or severe RHD may be asymptomatic Management of RHD includes Treatment of cardiac and other symptoms Long-term secondary prophylaxis (to prevent recurrent ARF) Regular medical and cardiology review Management of existing pregnancy Dental assessment, family planning referral4xn    Elements of a Disease Register%f  }A disease register is a list of people who have a common illness or disease. For example: Tuberculosis register HIV/AIDS register Vaccine-preventable diseases register (measles, rubella) Acute Rheumatic Fever & Rheumatic Heart Disease A disease register should be secure so that the information is not lost or damaged A disease register can be a computer database or a paper list[xnx[N0R    >   ~ :Paper Register  Book or List%f   8Computer Register  Database%f   Information on the Register%f  Information to identify each person (clinic or hospital number) Personal information (name, date of birth, gender, contact details) Current disease status (ARF only, or mild, moderate, severe RHD) Diagnoses, date of diagnoses How the diagnosis was made (hospital admission, screening programme) Secondary prophylaxis details (medication, amount received each year) Surgery details Dates for next medical review (or for heart valve surgery) Date and cause of death.x$c/ c *c8+c  ($c$.((,c,00  Notification of ARF and RHD%f  dAll people who have confirmed and suspected ARF and RHD should be notified to the RHD register so that health authorities can undertake the following: Identify high risk individuals who require priority care Coordinate secondary prophylaxis and follow-up programmes Help identify others who may be at risk Provide information on the local rates of disease Fn<   '  3 Sources of Information%f  eThe following sources may contain information on individuals for the RHD Register Benzathine Penicillin injection books Echocardiogram reports Heart valve surgery lists Notes from Medical Specialists, Heart Specialists, dentists and researchers Hospital admission and discharge records (e.g. ICD-9 or ICD-10 coding) School and community screening referrals:fxc)= ) Reports from the Register%f  VLists of individuals needing urgent care Lists of people receiving inadequate levels of secondary prophylaxis Delivery of Benzathine penicillin injections (for each full year on treatment) Specialist clinic lists Echocardiogram and Surgery waiting lists People who are deceased and cause of death Rates of disease for the region or countryjWx  ccc W Summary%f  A Disease Register can be on paper or computer The information should be confidential and secure The information on the register should Help coordinate health care for individuals Help describe the level of disease in the community All confirmed and suspected cases of ARF and RHD should be notified to the register Sources of information for the register may include Benzathine penicillin injection books Echocardiogram reports and surgery lists Hospital admission books and computer systems School screening referralstx`nxn_    #WHO recommendations for RHD Control$$%f $ A strong commitment from local Government A committed and skilled RHD Advisory Group An RHD Register of all people with confirmed and suspected ARF and RHD A well-trained programme coordinator Notification of ARF and RHD to the relevant health authority Well-coordinated secondary prevention activities A priority system to help deliver care to individuals at highest risk Reliable resources including medications and laboratory support Programmes established centrally and expanded regionally*+x0x(  Core Programme Objectives%f   Identify and register individuals with ARF and RHD Standardise and improve delivery of secondary prophylaxis Standardise diagnosis and management of ARF and RHD Provide training and support for health workers Provide support to the community Report on the programme and rates of disease$!q<x!   'Objective 1 - Identify & Register cases,( %f'f ( Collect information on known cases of ARF & RHD Benzathine Penicillin injection books and clinic records Echocardiogram reports and cardiac surgery lists Hospital admission & death reports Identify new cases Health centres or hospital when individuals present with ARF or RHD School health (screening) programmes Antenatal Clinics Maintain a paper or computer register of all people with confirmed or suspected ARF & RHD 0ZnPZ|nZZ0nAZ</{    Z      ,Objective 2 - Optimise Secondary Prophylaxis,- %f!'f - LEstablish secondary prophylaxis delivery Identify people who need secondary prophylaxis Identify health facilities where individuals receive secondary prophylaxis Improve secondary prophylaxis  identify specific barriers to treatment Identify people who do not receive adequate Benzathine penicillin injections (>80% injections) Establish recall and reminder systems Support communication between health facilities Refer new cases to peripheral health facilities for ongoing management Identify people who move between health centres for treatment){nHnn)zG   ' jObjective 3  Training and Support for Health Workers,6 %f*'f5  Standardise guidelines for diagnosis and management of ARF and RHD Revised Jones Criteria for diagnosis of ARF Standardise dosing and delivery of secondary prophylaxis Train health workers Curriculum development Training programmes for students and trained staff Updates for staff in rural and remote areas Communicate Referral of new cases to local community health facilities Update staff about on local ARF/ RHD issues Report on RHD in the communityCZfxZwxZ ZxCew      TB g  x t   >Objective 4  Community Support %f  9Educate and Inform Targeted education for people with ARF and RHD Community education materials (posters & brochures) Manage individuals with ARF & RHD Promote ongoing medical care / echocardiogram / pregnancy counseling / dental care Prioritise treatment for severe cases Cardiac assessment Surgery and supportcn x"Tx&'Mcc"  S    &' : G>Objective 5  Screening for RHD %f  Screening may be undertaken when acute cases are identified and managed, and when time and resources become available. Considerations for screening Who to screened (e.g. school children are easier / RHD may be more common in adults) Methods of diagnosis available (e.g. auscultation & clinical assessment, echocardiogram) Availability of trained staff Processes for reporting RHD cases to the RHD programme Health resources available for long-term management of more RHD cases. xLnvEc  :c<x    A RHD Programme Difficulties%f  Lack of local resources (including dedicated staff) Limited funds and other resources Heavy workloads for primary care health staff Priority of other health issues (e.g. TB, Malaria, HIV/AIDS, respiratory disease) The RHD programme is complex Difficulties around communication with remote health facilities Limited travel to provide training & education Demanding data management Programme expanded too quicklyxnco2 c 3  !  -  Q     + Summary%f  EAn RHD Programme should have Local (Government) commitment A manageable RHD Register Well-trained, dedicated staff at all levels Systems to identify known cases and refer of new cases A priority system for severe cases Secondary Prophylaxis monitoring and improvement Ongoing support for health staff and the community. Z%0x(%    fH<  . 7 $ h /4            !!""##$$%%&&''(())**++,,--..//00112233445566778899::;;<<==>>??@@AABDCFDHENFPHRIUJVK7  0N0 6.  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It has been made possible thanks to the support of the Vodafone Group Foundation and the International Solidarity, State of Geneva, and the ongoing support from Menzies School of Health Research, Caritas Australia, Cure Kids and Fiji Water. 0    X  Y Introduction f  bRheumatic Heart Disease is the most common cause of heart disease in children and young adults Approximately 15.6 million people affected worldwide Almost 500,000 new cases each year Approx 350,000 deaths each year Most disease occurs in developing countries. Rheumatic Heart Disease is a disease of poverty Rheumatic Heart Disease can be prevented. D`nZxG8  f$ Z  Z Definitions f  Group A beta-haemolytic streptococci (GAS) Humans are exposed to GAS in the environment Throat and skin are common sites of GAS infection GAS infections usually resolve without treatment Untreated GAS infections can lead to acute rheumatic fever in some people.t+nC CCCc"0$  J  [ Definitions f  QAcute Rheumatic Fever (ARF) A delayed auto-immune response following untreated GAS infection Develops after the GAS infection has resolved Commonly affects the joints, heart, central nervous system and skin Most common between the ages of 5 and 15 years Can recur following further untreated GAS infections Rheumatic Heart Disease (RHD) Residual damage to heart valves following recurrent ARF Valves become scarred, stiff, thickened Blood leaks (blood flows backwards through valves which do not close properly) Blood is blocked (blood can not flow through valves which do not open properly)(nn#######l#3## ##0## #$ O  \ Risk Factors %f   Risk factors ARF include Poverty Poor housing, overcrowded housing Lack of adequate health care Untreated GAS infections Risk factor for RHD Recurrent ARF Prevention The first episode of ARF can be prevented by treating GAS infections with penicillin (primary prophylaxis) If the first ARF episode is not prevented, recurrent ARF can be prevented with long-term penicillin (secondary prophylaxis)&Z`nZ!Zn Zn#`#### #  #  # T #  #d##<`  %   ]Disease Progression%f  CControl of Disease%f   ARF and RHD can be prevented by sustainable control strategies including Trained health staff who diagnose and management disease effectively Secondary prophylaxis to prevent further ARF and the development or worsening of RHD. Community education and awareness Screening for unknown RHD in the community. Control strategies should focus on Prompt identification and treatment of GAS infections Identifying people who have had ARF once and preventing further ARF and the development of RHD.IZnZ$ZnH####$##TI E W ! -   ^  _Revised Jones Criteria%f  ARF can be confirmed if certain signs and symptoms are present. The Revised Jones Criteria (below) can help guide the diagnosis.xC$  ; ' `Revised Jones Criteria%f  The World Health Organisation set the international standard for diagnosis of ARF. First episode or recurrent episode of ARF (no RHD): 2 MAJOR manifestations or 1 MAJOR and 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ARF (with existing RHD): 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ** Individual country guidelines also exist **^xnZZ0 fn]nZ5ZRCC4CAGfEGfcac A  G f E  G fcCAGfEGfcace c%c c C $g$f(A((G(f(E((G(f,c,,a,0C04c44e4 4c4%4c4 8A88C808A8<     bSigns and Symptoms%f  2MAJOR Manifestations Arthritis Painful, swollen joints (usually knees, ankles, wrists, elbows) Very common with ARF, often the first symptom Usually  migratory - disappears from one joint as it starts in another (poly-arthritis), however may just be present in one joint (mono-arthritis). Carditis May present as a heart  murmur Chest pain and/or difficulty breathing may be present in more severe cases 2!xn 0 dnmx Cc(cuccc*ccc Ck c  "   cSigns and Symptoms%f  Sydenham s chorea Twitchy, jerking movements and muscle weakness (most obvious in the face, hands and feet) May occur on both sides or only one side of body More common in teenagers and females (rare after age 20) May be associated with irritability and or depression May begin up to 3-4 months after the streptococcal throat infection, and often occurs without other symptoms Usually resolves within 6 weeks (may last 6 months or more) May recur in females during pregnancyxnC/c+cVcccc&cxk  0  9 6 m  < & dSigns and Symptoms%f  Subcutaneous nodules Painless lumps on the outside surfaces of elbows, wrists, knees, ankles in groups of 3-4 (up to 12) The skin is not red or inflamed Last 1-2 weeks (rarely more than 1 month) Nodules are more common when Carditis is also present. Erythema marginatum Painless, flat pink patches on the skin that spread outward in a circular pattern Usually occurs early, may last months, rarely lasts years Usually on the back or front of body, almost never on the face Hard to see in dark-skinned people.xnPPnCYc c/cc7cc C cx    )    9  >  $ ESigns and Symptoms%f  ZMINOR Manifestations Fever Occurs in the majority of cases, usually with the onset of symptoms Usually ranging from 38.4  40.0 C (101-104 F) Arthralgia Usually involves large joints May be mild or severe Group A streptococcal infection Group A beta-haemolytic streptococci may not be seen on a throat swab since the infection may be resolved at the time of onset of ARF symptoms. ASOT  serum reaches a peak level around 3-6 weeks after infection and starts to fall at 6-8 weeks Anti DNase B  reaches a peak level up to 6-8 weeks after infection and starts to fall at around 3 months after the infection. ** Normal antibody titre ranges vary with age and geography **HxvZ Z8Z!0" dZr0Z(ZFZGCucc C4 c  c  g  c s c   a <A  E         Y    W    < aDifficulties with ARF Diagnosis %f  BA combination of signs and symptoms is required to confirm ARF People with ARF do not always present to the health system with symptoms because Symptoms may not be considered serious Transport to the health facility may be difficult Health staff may not recognise the signs and symptoms of ARF ARF may be confused with other illnesses, for example Sore joints may be confused with a sports injury or  growing pains Ynt xDCYcc< C  C 7 C DC  eTreatment for ARF%f  :Treat the acute illness Benzathine penicillin G injection or Oral Penicillin for 10 days Relieve symptoms Bed rest Relief of arthritis, pain and fever (Paracetamol or Aspirin) Treat chorea (use Carbamazepine or Valproic acid if severe) Anti-heart failure medication (e.g. Diuretics, ACEi, Digoxin if required) VBnncC"ccc c  c C-cc c/cccc ; fARF Management Plan%f  )First dose of Benzathine penicillin G (start secondary prophylaxis) Baseline echocardiogram (if available) ARF alert on medical notes & computer systems (if applicable) Education for person and family Refer to local doctor / health facility Dental examination Long-term secondary prophylaxis plan )x&cccc.ccclC  d    '  9 gManagement of Probable ARF<%f%f%f  LTreat the symptoms } Dose of Benzathine penicillin G } as for ARF Echocardiogram (if available) } Medical officer review after one month, and Repeat echocardiogram (if available) If NOT ARF& cease Benzathine but monitor for ARF symptoms If ARF& continue Benzathine and manage as for ARF:j" xQxkn?C CCCcC C (CCCCCcccec ' hSummary%f  >The Jones Criteria is used to guide the diagnosis of ARF with a combination of MAJOR Manifestations, MINOR Manifestations and evidence of recent GAS Infection A long-term Management Plan should be established to prevent recurrence of ARF and development or worsening of RHD Probable ARF cases should also be monitored ?xOG'g R!-$e   i  jSecondary Prophylaxis%f  Secondary prophylaxis is the terms used to describe regular delivery of antibiotics to prevent recurrence of GAS infection and subsequent development of ARF. Secondary prophylaxis is recommended for people who have had ARF, or who have RHD to Prevent further Group A Streptococcal infections Prevent recurrence ARF Prevent the development or worsening of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD. PxnCc$   kStandard Treatment%f  Benzathine penicillin G 1,200,000 units for ALL people e"30kg 600,000 units for children <30kg Every 3 or 4 weeks (by intramuscular injection) Penicillin V Given if needles cannot be given due to excessive bleeding 250mg twice daily (by mouth) Erythromycin Given if Penicillin allergy has been confirmed by a Medical Officer 250mg twice daily (by mouth)Zwnx ZXnx Zkq<nC CKCK'Cc c  CMC cc C  C [$c$ $c$$^   lConsiderations%f  When should secondary prophylaxis be considered? ARF confirmed by the Revised Jones Criteria RHD confirmed on echocardiogram ARF or RHD not confirmed by the Revised Jones Criteria, but considered highly  probable Precautions Do not give Benzathine Penicillin G or Penicillin V if there is a documented Penicillin allergy Drug reactions are rare Continue secondary prophylaxis during pregnancy Continue secondary prophylaxis during anticoagulation (e.g. with Warfarin)1Pnq<x Pxnx}x1 <}x0  +  V  . x  ~ m$Guidelines for Secondary Prophylaxis%%%f % nCeasing Secondary Prophylaxis%f  Secondary Prophylaxis should only be ceased following: No ARF signs/symptoms for at least 5 years, and Medical Specialist review (Paediatrician / Physician / Cardiologist) and Echocardiogram to establish presence & severity of RHD (if available) D8 " 2x n7cca&CCCCa C * C  C  C  C a)CCC$  G o(Benzathine Penicillin injection delivery))%f ) Assessment and Preparation Confirm person s identity Review known drug allergies Discuss and record any recent ARF or RHD symptoms (refer to medical officer if required) Obtain consent for injection nchC'CCCT4    X   p(Benzathine Penicillin injection delivery))%f ) q Documentation%f  rCalculating Injection Delivery%f  sNotes on Injection Delivery%f  t$Factors affecting Injection Delivery%%%f % u(Strategies to improve Injection Delivery))%f ) Appoint a dedicated staff member at each clinic to oversee secondary prophylaxis coordination Identify people who need secondary prophylaxis Identify local health facility for each person Develop systems for follow-up Provide ongoing education for people who require injections and their families Communicate with local RHD programme and other health service providers Reduce injection pain Discuss alternative therapy issuesx  vwxSummary%f  uAntibiotics need to be present in the body at all times to help prevent GAS infections and prevent recurrent ARF Benzathine penicillin injections should be given unless there are contraindications to injections or documented penicillin allergy Medical Specialist review is required before ceasing secondary prophylaxis Strategies to improve secondary prophylaxis delivery: Good relationships between community and health staff Education for the community and health staff Systems for follow-up Communication between health services Reduce injection pain Document Benzathine Penicillin injections and monitor injection deliveryvxnIZpJ7@q  y  z{ Definitions %f  <Valve Regurgitation suggests that heart valves Are thickened and sticky against the walls of the heart Do not meet in the middle Leak (the blood flows backwards over the valve) Valve Stenosis suggests that heart valves Become stuck to each other Do not allow blood to flow through easily (restricted forward flow) /q<xx+` W+ *f = |Signs and Symptoms of RHD%f  rSymptoms of RHD may not develop for many years A murmur but no symptoms usually suggests mild-moderate disease Symptoms usually suggest moderate-severe disease Symptoms depend upon the type and severity of disease, and may include Breathlessness with exertion or when lying down flat Waking at night feeling breathless Feeling tired General weakness Peripheral oedema/q<xrxGq<xx/  ()G<?    $ }Heart valve involvement%f  .Mitral valve is affected in over 90% of cases of RHD Mitral regurgitation most commonly found in children & adolescents Mitral stenosis represents longer term chronic disease, commonly in adults Most common complication of mitral stenosis is atrial fibrillation Aortic valve next most commonly affected Generally associated with disease of the mitral valve. Tends to develop as a long term complication of aortic regurgitation Tricuspid and pulmonary valves are much less commonly affected Usually affected in very severe RHD when all valves are affected5ZZ Z*Z~x?ZAZ.C7 C    #  }      'A / ~Clinical Examination%f  Investigations%f  .Electrocardiogram (ECG) To determine sinus rhythm Chest X-ray (CXR) To determine size and placement of heart To identify cardiac failure (pulmonary congestion) Echocardiography To identify heart valve damage To estimate severity of disease Useful to compare results with future echocardiogram resultsZZZ\Z Z Z|Z E|   / Key element in RHD Management%f   Secondary prophylaxis Functions of secondary prophylaxis with established RHD Prevent Group A Streptococcal infections Prevent the repeated development of ARF Prevent the development of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD.pZ8ZZG$E8Cc$N   Elements in RHD Management%f   KRHD and Pregnancy%f   MManagement of RHD in Pregnancy%f   QInfective Endocarditis%f   S-Procedures that increase risk of Endocarditis..%f-   TSurgery for RHD%f   "Guidelines for managing Mild RHDN#%f%f%f%f #  &Guidelines for managing Moderate RHD<'%f%f%f '  $Guidelines for managing Severe RHD<%%f%f%f %  Summary%f  RHD presents as damage to the heart valves The mitral valve is most commonly affected, followed by Aortic, Pulmonary and Tricuspid RHD can be mild, moderate or severe RHD may be asymptomatic Management of RHD includes Treatment of cardiac and other symptoms Long-term secondary prophylaxis (to prevent recurrent ARF) Regular medical and cardiology review Management of existing pregnancy Dental assessment, family planning referral4xn    Elements of a Disease Register%f  }A disease register is a list of people who have a common illness or disease. For example: Tuberculosis register HIV/AIDS register Vaccine-preventable diseases register (measles, rubella) Acute Rheumatic Fever & Rheumatic Heart Disease A disease register should be secure so that the information is not lost or damaged A disease register can be a computer database or a paper list[xnx[N0R    >   ~ :Paper Register  Book or List%f   8Computer Register  Database%f   Information on the Register%f  Information to identify each person (clinic or hospital number) Personal information (name, date of birth, gender, contact details) Current disease status (ARF only, or mild, moderate, severe RHD) Diagnoses, date of diagnoses How the diagnosis was made (hospital admission, screening programme) Secondary prophylaxis details (medication, amount received each year) Surgery details Dates for next medical review (or for heart valve surgery) Date and cause of death.x$c/ c *c8+c  ($c$.((,c,00  Notification of ARF and RHD%f  dAll people who have confirmed and suspected ARF and RHD should be notified to the RHD register so that health authorities can undertake the following: Identify high risk individuals who require priority care Coordinate secondary prophylaxis and follow-up programmes Help identify others who may be at risk Provide information on the local rates of disease Fn<   '  3 Sources of Information%f  eThe following sources may contain information on individuals for the RHD Register Benzathine Penicillin injection books Echocardiogram reports Heart valve surgery lists Notes from Medical Specialists, Heart Specialists, dentists and researchers Hospital admission and discharge records (e.g. ICD-9 or ICD-10 coding) School and community screening referrals:fxc)= ) Reports from the Register%f  VLists of individuals needing urgent care Lists of people receiving inadequate levels of secondary prophylaxis Delivery of Benzathine penicillin injections (for each full year on treatment) Specialist clinic lists Echocardiogram and Surgery waiting lists People who are deceased and cause of death Rates of disease for the region or countryjWx  ccc W Summary%f  A Disease Register can be on paper or computer The information should be confidential and secure The information on the register should Help coordinate health care for individuals Help describe the level of disease in the community All confirmed and suspected cases of ARF and RHD should be notified to the register Sources of information for the register may include Benzathine penicillin injection books Echocardiogram reports and surgery lists Hospital admission books and computer systems School screening referralstx`nxn_    #WHO recommendations for RHD Control$$%f $ A strong commitment from local Government A committed and skilled RHD Advisory Group An RHD Register of all people with confirmed and suspected ARF and RHD A well-trained programme coordinator Notification of ARF and RHD to the relevant health authority Well-coordinated secondary prevention activities A priority system to help deliver care to individuals at highest risk Reliable resources including medications and laboratory support Programmes established centrally and expanded regionally*+x0x(  Core Programme Objectives%f   Identify and register individuals with ARF and RHD Standardise and improve delivery of secondary prophylaxis Standardise diagnosis and management of ARF and RHD Provide training and support for health workers Provide support to the community Report on the programme and rates of disease$!q<x!   'Objective 1 - Identify & Register cases,( %f'f ( Collect information on known cases of ARF & RHD Benzathine Penicillin injection books and clinic records Echocardiogram reports and cardiac surgery lists Hospital admission & death reports Identify new cases Health centres or hospital when individuals present with ARF or RHD School health (screening) programmes Antenatal Clinics Maintain a paper or computer register of all people with confirmed or suspected ARF & RHD 0ZnPZ|nZZ0nAZ</{    Z      ,Objective 2 - Optimise Secondary Prophylaxis,- %f!'f - LEstablish secondary prophylaxis delivery Identify people who need secondary prophylaxis Identify health facilities where individuals receive secondary prophylaxis Improve secondary prophylaxis  identify specific barriers to treatment Identify people who do not receive adequate Benzathine penicillin injections (>80% injections) Establish recall and reminder systems Support communication between health facilities Refer new cases to peripheral health facilities for ongoing management Identify people who move between health centres for treatment){nHnn)zG   ' jObjective 3  Training and Support for Health Workers,6 %f*'f5  Standardise guidelines for diagnosis and management of ARF and RHD Revised Jones Criteria for diagnosis of ARF Standardise dosing and delivery of secondary prophylaxis Train health workers Curriculum development Training programmes for students and trained staff Updates for staff in rural and remote areas Communicate Referral of new cases to local community health facilities Update staff about on local ARF/ RHD issues Report on RHD in the communityCZfxZwxZ ZxCew      TB g  x t   >Objective 4  Community Support %f  9Educate and Inform Targeted education for people with ARF and RHD Community education materials (posters & brochures) Manage individuals with ARF & RHD Promote ongoing medical care / echocardiogram / pregnancy counseling / dental care Prioritise treatment for severe cases Cardiac assessment Surgery and supportcn x"Tx&'Mcc"  S    &' : G>Objective 5  Screening for RHD %f  Screening may be undertaken when acute cases are identified and managed, and when time and resources become available. Considerations for screening Who to screened (e.g. school children are easier / RHD may be more common in adults) Methods of diagnosis available (e.g. auscultation & clinical assessment, echocardiogram) Availability of trained staff Processes for reporting RHD cases to the RHD programme Health resources available for long-term management of more RHD cases. xLnvEc  :c<x    A RHD Programme Difficulties%f  Lack of local resources (including dedicated staff) Limited funds and other resources Heavy workloads for primary care health staff Priority of other health issues (e.g. TB, Malaria, HIV/AIDS, respiratory disease) The RHD programme is complex Difficulties around communication with remote health facilities Limited travel to provide training & education Demanding data management Programme expanded too quicklyxnco2 c 3  !  -  Q     + Summary%f  EAn RHD Programme should have Local (Government) commitment A manageable RHD Register Well-trained, dedicated staff at all levels Systems to identify known cases and refer of new cases A priority system for severe cases Secondary Prophylaxis monitoring and improvement Ongoing support for health staff and the community. Z%0x(%    fH<  . 7 $ h /4            !!""##$$%%&&''(())**++,,--..//00112233445566778899::;;<<==>>??@@AABDCFDHENFPHRIUJVKr5Ws ;^V1(A  D/ 0|DArialnd RomanPPHwؖO 0ؖDVerdana RomanPPHwؖO 0ؖ" DWingdingsRomanPPHwؖO 0ؖ0DTimes New RomanPPHwؖO 0ؖ@DGaramond RomanPPHwؖO 0ؖ@ .  @n?" dd@  @@``  D       %,; (`    uw x         )     &      !"#$%&'()*+,-./012569:;<?@CDEFGHIJR$UE5jXkBvhFR$:DORfaFR$mt"r-8P R$I}_e,D-} b$TAdY˴8^ IR$~a# aN+X3dVR$Bo+esۓ R$.1@lC(]nb$ `5jcl49; 0AA f3@38Oʚ;_R8ʚ;4ddddpO 0<ppzp ppp]  <4dddd 0P<4KdKd 0P<4!d!d 0PN___PPT10DTimes New RomanPPtO 0tDArialNew RomanPPtO 0t ppn___PPT9PH`b2g`kznX{&|(}J2J?  %O  =V QDiagnosis and Management of Acute Rheumatic Fever and Rheumatic Heart Disease nQ8P(' f'(f' f'(f R W This presentation is intended to support the Curriculum for training health workers and others involved in the diagnosis and management of acute rheumatic fever and rheumatic heart disease. It has been made possible thanks to the support of the Vodafone Group Foundation and the International Solidarity, State of Geneva, and the ongoing support from Menzies School of Health Research, Caritas Australia, Cure Kids and Fiji Water. 0    X  Y Introduction f  bRheumatic Heart Disease is the most common cause of heart disease in children and young adults Approximately 15.6 million people affected worldwide Almost 500,000 new cases each year Approx 350,000 deaths each year Most disease occurs in developing countries. Rheumatic Heart Disease is a disease of poverty Rheumatic Heart Disease can be prevented. D`nZxG8  f$ Z  Z Definitions f  Group A beta-haemolytic streptococci (GAS) Humans are exposed to GAS in the environment Throat and skin are common sites of GAS infection GAS infections usually resolve without treatment Untreated GAS infections can lead to acute rheumatic fever in some people.t+nC CCCc"0$  J  [ Definitions f  QAcute Rheumatic Fever (ARF) A delayed auto-immune response following untreated GAS infection Develops after the GAS infection has resolved Commonly affects the joints, heart, central nervous system and skin Most common between the ages of 5 and 15 years Can recur following further untreated GAS infections Rheumatic Heart Disease (RHD) Residual damage to heart valves following recurrent ARF Valves become scarred, stiff, thickened Blood leaks (blood flows backwards through valves which do not close properly) Blood is blocked (blood can not flow through valves which do not open properly)(nn#######l#3## ##0## #$ O  \ Risk Factors %f   Risk factors ARF include Poverty Poor housing, overcrowded housing Lack of adequate health care Untreated GAS infections Risk factor for RHD Recurrent ARF Prevention The first episode of ARF can be prevented by treating GAS infections with penicillin (primary prophylaxis) If the first ARF episode is not prevented, recurrent ARF can be prevented with long-term penicillin (secondary prophylaxis)&Z`nZ!Zn Zn#`#### #  #  # T #  #d##<`  %   ]Disease Progression%f  CControl of Disease%f   ARF and RHD can be prevented by sustainable control strategies including Trained health staff who diagnose and management disease effectively Secondary prophylaxis to prevent further ARF and the development or worsening of RHD. Community education and awareness Screening for unknown RHD in the community. Control strategies should focus on Prompt identification and treatment of GAS infections Identifying people who have had ARF once and preventing further ARF and the development of RHD.IZnZ$ZnH####$##TI E W ! -   ^  _Revised Jones Criteria%f  ARF can be confirmed if certain signs and symptoms are present. The Revised Jones Criteria (below) can help guide the diagnosis.xC$  ; ' `Revised Jones Criteria%f  The World Health Organisation set the international standard for diagnosis of ARF. First episode or recurrent episode of ARF (no RHD): 2 MAJOR manifestations or 1 MAJOR and 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ARF (with existing RHD): 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ** Individual country guidelines also exist **^xnZZ0 fn]nZ5ZRCC4CAGfEGfcac A  G f E  G fcCAGfEGfcace c%c c C $g$f(A((G(f(E((G(f,c,,a,0C04c44e4 4c4%4c4 8A88C808A8<     bSigns and Symptoms%f  2MAJOR Manifestations Arthritis Painful, swollen joints (usually knees, ankles, wrists, elbows) Very common with ARF, often the first symptom Usually  migratory - disappears from one joint as it starts in another (poly-arthritis), however may just be present in one joint (mono-arthritis). Carditis May present as a heart  murmur Chest pain and/or difficulty breathing may be present in more severe cases 2!xn 0 dnmx Cc(cuccc*ccc Ck c  "   cSigns and Symptoms%f  Sydenham s chorea Twitchy, jerking movements and muscle weakness (most obvious in the face, hands and feet) May occur on both sides or only one side of body More common in teenagers and females (rare after age 20) May be associated with irritability and or depression May begin up to 3-4 months after the streptococcal throat infection, and often occurs without other symptoms Usually resolves within 6 weeks (may last 6 months or more) May recur in females during pregnancyxnC/c+cVcccc&cxk  0  9 6 m  < & dSigns and Symptoms%f  Subcutaneous nodules Painless lumps on the outside surfaces of elbows, wrists, knees, ankles in groups of 3-4 (up to 12) The skin is not red or inflamed Last 1-2 weeks (rarely more than 1 month) Nodules are more common when Carditis is also present. Erythema marginatum Painless, flat pink patches on the skin that spread outward in a circular pattern Usually occurs early, may last months, rarely lasts years Usually on the back or front of body, almost never on the face Hard to see in dark-skinned people.xnPPnCYc c/cc7cc C cx    )    9  >  $ ESigns and Symptoms%f  ZMINOR Manifestations Fever Occurs in the majority of cases, usually with the onset of symptoms Usually ranging from 38.4  40.0 C (101-104 F) Arthralgia Usually involves large joints May be mild or severe Group A streptococcal infection Group A beta-haemolytic streptococci may not be seen on a throat swab since the infection may be resolved at the time of onset of ARF symptoms. ASOT  serum reaches a peak level around 3-6 weeks after infection and starts to fall at 6-8 weeks Anti DNase B  reaches a peak level up to 6-8 weeks after infection and starts to fall at around 3 months after the infection. ** Normal antibody titre ranges vary with age and geography **HxvZ Z8Z!0" dZr0Z(ZFZGCucc C4 c  c  g  c s c   a <A  E         Y    W    < aDifficulties with ARF Diagnosis %f  BA combination of signs and symptoms is required to confirm ARF People with ARF do not always present to the health system with symptoms because Symptoms may not be considered serious Transport to the health facility may be difficult Health staff may not recognise the signs and symptoms of ARF ARF may be confused with other illnesses, for example Sore joints may be confused with a sports injury or  growing pains YntxDCYcc< C  C 7 C DC  eTreatment for ARF%f  :Treat the acute illness Benzathine penicillin G injection or Oral Penicillin for 10 days Relieve symptoms Bed rest Relief of arthritis, pain and fever (Paracetamol or Aspirin) Treat chorea (use Carbamazepine or Valproic acid if severe) Anti-heart failure medication (e.g. Diuretics, ACEi, Digoxin if required) VBnncC"ccc c  c C-cc c/cccc ; fARF Management Plan%f  )First dose of Benzathine penicillin G (start secondary prophylaxis) Baseline echocardiogram (if available) ARF alert on medical notes & computer systems (if applicable) Education for person and family Refer to local doctor / health facility Dental examination Long-term secondary prophylaxis plan )x&cccc.ccclC  d    '  9 gManagement of Probable ARF<%f%f%f  LTreat the symptoms } Dose of Benzathine penicillin G } as for ARF Echocardiogram (if available) } Medical officer review after one month, and Repeat echocardiogram (if available) If NOT ARF& cease Benzathine but monitor for ARF symptoms If ARF& continue Benzathine and manage as for ARF:j" xQxkn?C CCCcC C (CCCCCcccec ' hSummary%f  >The Jones Criteria is used to guide the diagnosis of ARF with a combination of MAJOR Manifestations, MINOR Manifestations and evidence of recent GAS Infection A long-term Management Plan should be established to prevent recurrence of ARF and development or worsening of RHD Probable ARF cases should also be monitored ?xOG'g R!-$e   i  jSecondary Prophylaxis%f  Secondary prophylaxis is the terms used to describe regular delivery of antibiotics to prevent recurrence of GAS infection and subsequent development of ARF. Secondary prophylaxis is recommended for people who have had ARF, or who have RHD to Prevent further Group A Streptococcal infections Prevent recurrence ARF Prevent the development or worsening of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD. PxnCc$   kStandard Treatment%f  Benzathine penicillin G 1,200,000 units for ALL people e"30kg 600,000 units for children <30kg Every 3 or 4 weeks (by intramuscular injection) Penicillin V Given if needles cannot be given due to excessive bleeding 250mg twice daily (by mouth) Erythromycin Given if Penicillin allergy has been confirmed by a Medical Officer 250mg twice daily (by mouth)Zwnx ZXnx Zkq<nC CKCK'Cc c  CMC cc C  C [$c$ $c$$^   lConsiderations%f  When should secondary prophylaxis be considered? ARF confirmed by the Revised Jones Criteria RHD confirmed on echocardiogram ARF or RHD not confirmed by the Revised Jones Criteria, but considered highly  probable Precautions Do not give Benzathine Penicillin G or Penicillin V if there is a documented Penicillin allergy Drug reactions are rare Continue secondary prophylaxis during pregnancy Continue secondary prophylaxis during anticoagulation (e.g. with Warfarin)1Pnq<x Pxnx}x1 <}x0  +  V  . x  ~ m$Guidelines for Secondary Prophylaxis%%%f % nCeasing Secondary Prophylaxis%f  Secondary Prophylaxis should only be ceased following: No ARF signs/symptoms for at least 5 years, and Medical Specialist review (Paediatrician / Physician / Cardiologist) and Echocardiogram to establish presence & severity of RHD (if available) D8 " 2x n7cca&CCCCa C * C  C  C  C a)CCC$  G o(Benzathine Penicillin injection delivery))%f ) Assessment and Preparation Confirm person s identity Review known drug allergies Discuss and record any recent ARF or RHD symptoms (refer to medical officer if required) Obtain consent for injection nchC'CCCT4    X   p(Benzathine Penicillin injection delivery))%f ) q Documentation%f  rCalculating Injection Delivery%f  sNotes on Injection Delivery%f  t$Factors affecting Injection Delivery%%%f % u(Strategies to improve Injection Delivery))%f ) Appoint a dedicated staff member at each clinic to oversee secondary prophylaxis coordination Identify people who need secondary prophylaxis Identify local health facility for each person Develop systems for follow-up Provide ongoing education for people who require injections and their families Communicate with local RHD programme and other health service providers Reduce injection pain Discuss alternative therapy issuesx  vwxSummary%f  uAntibiotics need to be present in the body at all times to help prevent GAS infections and prevent recurrent ARF Benzathine penicillin injections should be given unless there are contraindications to injections or documented penicillin allergy Medical Specialist review is required before ceasing secondary prophylaxis Strategies to improve secondary prophylaxis delivery: Good relationships between community and health staff Education for the community and health staff Systems for follow-up Communication between health services Reduce injection pain Document Benzathine Penicillin injections and monitor injection deliveryvxnIZpJ7@q  y  z{ Definitions %f  <Valve Regurgitation suggests that heart valves Are thickened and sticky against the walls of the heart Do not meet in the middle Leak (the blood flows backwards over the valve) Valve Stenosis suggests that heart valves Become stuck to each other Do not allow blood to flow through easily (restricted forward flow) /q<xx+` W+ *f =                           ! " # $ % & ' ( ) * + , - . / 0 1 2 3 4 5 6 7 8 9 : ; < = > ? @ A B C D E F G H I J K L M N O P Q R S T U V W X Y Z [ \ ] ^ _ ` a b c d e f g h i j k l m n o p q r s t u v w x y z { | ~  |Signs and Symptoms of RHD%f  rSymptoms of RHD may not develop for many years A murmur but no symptoms usually suggests mild-moderate disease Symptoms usually suggest moderate-severe disease Symptoms depend upon the type and severity of disease, and may include Breathlessness with exertion or when lying down flat Waking at night feeling breathless Feeling tired General weakness Peripheral oedema/q<xrxGq<xx/  ()G<?    $ }Heart valve involvement%f  .Mitral valve is affected in over 90% of cases of RHD Mitral regurgitation most commonly found in children & adolescents Mitral stenosis represents longer term chronic disease, commonly in adults Most common complication of mitral stenosis is atrial fibrillation Aortic valve next most commonly affected Generally associated with disease of the mitral valve. Tends to develop as a long term complication of aortic regurgitation Tricuspid and pulmonary valves are much less commonly affected Usually affected in very severe RHD when all valves are affected5ZZ Z*Z~x?ZAZ.C7 C    #  }      'A / ~Clinical Examination%f  Investigations%f  .Electrocardiogram (ECG) To determine sinus rhythm Chest X-ray (CXR) To determine size and placement of heart To identify cardiac failure (pulmonary congestion) Echocardiography To identify heart valve damage To estimate severity of disease Useful to compare results with future echocardiogram resultsZZZ\Z Z Z|Z E|   / Key element in RHD Management%f   Secondary prophylaxis Functions of secondary prophylaxis with established RHD Prevent Group A Streptococcal infections Prevent the repeated development of ARF Prevent the development of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD.pZ8ZZG$E8Cc$N   Elements in RHD Management%f   KRHD and Pregnancy%f   MManagement of RHD in Pregnancy%f   QInfective Endocarditis%f   S-Procedures that increase risk of Endocarditis..%f-   TSurgery for RHD%f   "Guidelines for managing Mild RHDN#%f%f%f%f #  &Guidelines for managing Moderate RHD<'%f%f%f '  $Guidelines for managing Severe RHD<%%f%f%f %  Summary%f  RHD presents as damage to the heart valves The mitral valve is most commonly affected, followed by Aortic, Pulmonary and Tricuspid RHD can be mild, moderate or severe RHD may be asymptomatic Management of RHD includes Treatment of cardiac and other symptoms Long-term secondary prophylaxis (to prevent recurrent ARF) Regular medical and cardiology review Management of existing pregnancy Dental assessment, family planning referral4xn    Elements of a Disease Register%f  }A disease register is a list of people who have a common illness or disease. For example: Tuberculosis register HIV/AIDS register Vaccine-preventable diseases register (measles, rubella) Acute Rheumatic Fever & Rheumatic Heart Disease A disease register should be secure so that the information is not lost or damaged A disease register can be a computer database or a paper list[xnx[N0R    >   ~ :Paper Register  Book or List%f   8Computer Register  Database%f   Information on the Register%f  Information to identify each person (clinic or hospital number) Personal information (name, date of birth, gender, contact details) Current disease status (ARF only, or mild, moderate, severe RHD) Diagnoses, date of diagnoses How the diagnosis was made (hospital admission, screening programme) Secondary prophylaxis details (medication, amount received each year) Surgery details Dates for next medical review (or for heart valve surgery) Date and cause of death.x$c/ c *c8+c  ($c$.((,c,00  Notification of ARF and RHD%f  dAll people who have confirmed and suspected ARF and RHD should be notified to the RHD register so that health authorities can undertake the following: Identify high risk individuals who require priority care Coordinate secondary prophylaxis and follow-up programmes Help identify others who may be at risk Provide information on the local rates of disease Fn<   '  3 Sources of Information%f  eThe following sources may contain information on individuals for the RHD Register Benzathine Penicillin injection books Echocardiogram reports Heart valve surgery lists Notes from Medical Specialists, Heart Specialists, dentists and researchers Hospital admission and discharge records (e.g. ICD-9 or ICD-10 coding) School and community screening referrals:fxc)= ) Reports from the Register%f  VLists of individuals needing urgent care Lists of people receiving inadequate levels of secondary prophylaxis Delivery of Benzathine penicillin injections (for each full year on treatment) Specialist clinic lists Echocardiogram and Surgery waiting lists People who are deceased and cause of death Rates of disease for the region or countryjWx  ccc W Summary%f  A Disease Register can be on paper or computer The information should be confidential and secure The information on the register should Help coordinate health care for individuals Help describe the level of disease in the community All confirmed and suspected cases of ARF and RHD should be notified to the register Sources of information for the register may include Benzathine penicillin injection books Echocardiogram reports and surgery lists Hospital admission books and computer systems School screening referralstx`nxn_    #WHO recommendations for RHD Control$$%f $ A strong commitment from local Government A committed and skilled RHD Advisory Group An RHD Register of all people with confirmed and suspected ARF and RHD A well-trained programme coordinator Notification of ARF and RHD to the relevant health authority Well-coordinated secondary prevention activities A priority system to help deliver care to individuals at highest risk Reliable resources including medications and laboratory support Programmes established centrally and expanded regionally*+x0x(  Core Programme Objectives%f   Identify and register individuals with ARF and RHD Standardise and improve delivery of secondary prophylaxis Standardise diagnosis and management of ARF and RHD Provide training and support for health workers Provide support to the community Report on the programme and rates of disease$!q<x!   'Objective 1 - Identify & Register cases,( %f'f ( Collect information on known cases of ARF & RHD Benzathine Penicillin injection books and clinic records Echocardiogram reports and cardiac surgery lists Hospital admission & death reports Identify new cases Health centres or hospital when individuals present with ARF or RHD School health (screening) programmes Antenatal Clinics Maintain a paper or computer register of all people with confirmed or suspected ARF & RHD 0ZnPZ|nZZ0nAZ</{    Z      ,Objective 2 - Optimise Secondary Prophylaxis,- %f!'f - LEstablish secondary prophylaxis delivery Identify people who need secondary prophylaxis Identify health facilities where individuals receive secondary prophylaxis Improve secondary prophylaxis  identify specific barriers to treatment Identify people who do not receive adequate Benzathine penicillin injections (>80% injections) Establish recall and reminder systems Support communication between health facilities Refer new cases to peripheral health facilities for ongoing management Identify people who move between health centres for treatment){nHnn)zG   ' jObjective 3  Training and Support for Health Workers,6 %f*'f5  Standardise guidelines for diagnosis and management of ARF and RHD Revised Jones Criteria for diagnosis of ARF Standardise dosing and delivery of secondary prophylaxis Train health workers Curriculum development Training programmes for students and trained staff Updates for staff in rural and remote areas Communicate Referral of new cases to local community health facilities Update staff about on local ARF/ RHD issues Report on RHD in the communityCZfxZwxZ ZxCew      TB g  x t   >Objective 4  Community Support %f  9Educate and Inform Targeted education for people with ARF and RHD Community education materials (posters & brochures) Manage individuals with ARF & RHD Promote ongoing medical care / echocardiogram / pregnancy counseling / dental care Prioritise treatment for severe cases Cardiac assessment Surgery and supportcn x"Tx&'Mcc"  S    &' : G>Objective 5  Screening for RHD %f  Screening may be undertaken when acute cases are identified and managed, and when time and resources become available. Considerations for screening Who to screened (e.g. school children are easier / RHD may be more common in adults) Methods of diagnosis available (e.g. auscultation & clinical assessment, echocardiogram) Availability of trained staff Processes for reporting RHD cases to the RHD programme Health resources available for long-term management of more RHD cases. xLnvEc  :c<x    A RHD Programme Difficulties%f  Lack of local resources (including dedicated staff) Limited funds and other resources Heavy workloads for primary care health staff Priority of other health issues (e.g. TB, Malaria, HIV/AIDS, respiratory disease) The RHD programme is complex Difficulties around communication with remote health facilities Limited travel to provide training & education Demanding data management Programme expanded too quicklyxnco2 c 3  !  -  Q     + Summary%f  EAn RHD Programme should have Local (Government) commitment A manageable RHD Register Well-trained, dedicated staff at all levels Systems to identify known cases and refer of new cases A priority system for severe cases Secondary Prophylaxis monitoring and improvement Ongoing support for health staff and the community. Z%0x(%    fH<  . 7 $ h /4            !!""##$$%%&&''(())**++,,--..//00112233445566778899::;;<<==>>??@@AABDCFDHENFPHRIUJVKro^Ws K^u/V1(A  D/ 0|DArialnd RomanPPHwؖO 0ؖDVerdana RomanPPHwؖO 0ؖ" DWingdingsRomanPPHwؖO 0ؖ0DTimes New RomanPPHwؖO 0ؖ@DGaramond RomanPPHwؖO 0ؖ@ .  @n?" dd@  @@``  D       %,; (`    uw x         )     &      !"#$%&'()*+,-./012569:;<?@CDEFGHIJR$UE5jXkBvhFR$:DORfaFR$mt"r-8P R$I}_e,D-} b$TAdY˴8^ IR$~a# aN+X3dVR$Bo+esۓ R$.1@lC(]nb$ `5jcl49; 0AA f3@38Oʚ;_R8ʚ;4ddddpO 0<ppzp ppp]  <4dddd 0P<4KdKd 0P<4!d!d 0PN___PPT10DTimes New RomanPPtO 0tDArialNew RomanPPtO 0t ppn___PPT9PH`b2g`kznX{&|(}J2J?  %O  =V QDiagnosis and Management of Acute Rheumatic Fever and Rheumatic Heart Disease nQ8P(' f'(f' f'(f R W This presentation is intended to support the Curriculum for training health workers and others involved in the diagnosis and management of acute rheumatic fever and rheumatic heart disease. It has been made possible thanks to the support of the Vodafone Group Foundation and the International Solidarity, State of Geneva, and the ongoing support of Menzies School of Health Research, Caritas Australia, Cure Kids and Fiji Water. J    P  X  Y Introduction f  bRheumatic Heart Disease is the most common cause of heart disease in children and young adults Approximately 15.6 million people affected worldwide Almost 500,000 new cases each year Approx 350,000 deaths each year Most disease occurs in developing countries. Rheumatic Heart Disease is a disease of poverty Rheumatic Heart Disease can be prevented. D`nZxG8  f$ Z  Z Definitions f  Group A beta-haemolytic streptococci (GAS) Humans are exposed to GAS in the environment Throat and skin are common sites of GAS infection GAS infections usually resolve without treatment Untreated GAS infections can lead to acute rheumatic fever in some people.t+nC CCCc"0$  J  [ Definitions f  QAcute Rheumatic Fever (ARF) A delayed auto-immune response following untreated GAS infection Develops after the GAS infection has resolved Commonly affects the joints, heart, central nervous system and skin Most common between the ages of 5 and 15 years Can recur following further untreated GAS infections Rheumatic Heart Disease (RHD) Residual damage to heart valves following recurrent ARF Valves become scarred, stiff, thickened Blood leaks (blood flows backwards through valves which do not close properly) Blood is blocked (blood can not flow through valves which do not open properly)(nn#######l#3## ##0## #$ O  \ Risk Factors %f   Risk factors ARF include Poverty Poor housing, overcrowded housing Lack of adequate health care Untreated GAS infections Risk factor for RHD Recurrent ARF Prevention The first episode of ARF can be prevented by treating GAS infections with penicillin (primary prophylaxis) If the first ARF episode is not prevented, recurrent ARF can be prevented with long-term penicillin (secondary prophylaxis)&Z`nZ!Zn Zn#`#### #  #  # T #  #d##<`  %   ]Disease Progression%f  CControl of Disease%f   ARF and RHD can be prevented by sustainable control strategies including Trained health staff who diagnose and management disease effectively Secondary prophylaxis to prevent further ARF and the development or worsening of RHD. Community education and awareness Screening for unknown RHD in the community. Control strategies should focus on Prompt identification and treatment of GAS infections Identifying people who have had ARF once and preventing further ARF and the development of RHD.IZnZ$ZnH####$##TI E W ! -   ^  _Revised Jones Criteria%f  ARF can be confirmed if certain signs and symptoms are present. The Revised Jones Criteria (below) can help guide the diagnosis.xC$  ; ' `Revised Jones Criteria%f  The World Health Organisation set the international standard for diagnosis of ARF. First episode or recurrent episode of ARF (no RHD): 2 MAJOR manifestations or 1 MAJOR and 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ARF (with existing RHD): 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ** Individual country guidelines also exist **^xnZZ0 fn]nZ5ZRCC4CAGfEGfcac A  G f E  G fcCAGfEGfcace c%c c C $g$f(A((G(f(E((G(f,c,,a,0C04c44e4 4c4%4c4 8A88C808A8<     bSigns and Symptoms%f  2MAJOR Manifestations Arthritis Painful, swollen joints (usually knees, ankles, wrists, elbows) Very common with ARF, often the first symptom Usually  migratory - disappears from one joint as it starts in another (poly-arthritis), however may just be present in one joint (mono-arthritis). Carditis May present as a heart  murmur Chest pain and/or difficulty breathing may be present in more severe cases 2!xn 0 dnmx Cc(cuccc*ccc Ck c  "   cSigns and Symptoms%f  Sydenham s chorea Twitchy, jerking movements and muscle weakness (most obvious in the face, hands and feet) May occur on both sides or only one side of body More common in teenagers and females (rare after age 20) May be associated with irritability and or depression May begin up to 3-4 months after the streptococcal throat infection, and often occurs without other symptoms Usually resolves within 6 weeks (may last 6 months or more) May recur in females during pregnancyxnC/c+cVcccc&cxk  0  9 6 m  < & dSigns and Symptoms%f  Subcutaneous nodules Painless lumps on the outside surfaces of elbows, wrists, knees, ankles in groups of 3-4 (up to 12) The skin is not red or inflamed Last 1-2 weeks (rarely more than 1 month) Nodules are more common when Carditis is also present. Erythema marginatum Painless, flat pink patches on the skin that spread outward in a circular pattern Usually occurs early, may last months, rarely lasts years Usually on the back or front of body, almost never on the face Hard to see in dark-skinned people.xnPPnCYc c/cc7cc C cx    )    9  >  $ ESigns and Symptoms%f  ZMINOR Manifestations Fever Occurs in the majority of cases, usually with the onset of symptoms Usually ranging from 38.4  40.0 C (101-104 F) Arthralgia Usually involves large joints May be mild or severe Group A streptococcal infection Group A beta-haemolytic streptococci may not be seen on a throat swab since the infection may be resolved at the time of onset of ARF symptoms. ASOT  serum reaches a peak level around 3-6 weeks after infection and starts to fall at 6-8 weeks Anti DNase B  reaches a peak level up to 6-8 weeks after infection and starts to fall at around 3 months after the infection. ** Normal antibody titre ranges vary with age and geography **HxvZ Z8Z!0" dZr0Z(ZFZGCucc C4 c  c  g  c s c   a <A  E         Y    W    < aDifficulties with ARF Diagnosis %f  BA combination of signs and symptoms is required to confirm ARF People with ARF do not always present to the health system with symptoms because Symptoms may not be considered serious Transport to the health facility may be difficult Health staff may not recognise the signs and symptoms of ARF ARF may be confused with other illnesses, for example Sore joints may be confused with a sports injury or  growing pains YntxDCYcc< C  C 7 C DC  eTreatment for ARF%f  :Treat the acute illness Benzathine penicillin G injection or Oral Penicillin for 10 days Relieve symptoms Bed rest Relief of arthritis, pain and fever (Paracetamol or Aspirin) Treat chorea (use Carbamazepine or Valproic acid if severe) Anti-heart failure medication (e.g. Diuretics, ACEi, Digoxin if required) VBnncC"ccc c  c C-cc c/cccc ; fARF Management Plan%f  )First dose of Benzathine penicillin G (start secondary prophylaxis) Baseline echocardiogram (if available) ARF alert on medical notes & computer systems (if applicable) Education for person and family Refer to local doctor / health facility Dental examination Long-term secondary prophylaxis plan )x&cccc.ccclC  d    '  9 gManagement of Probable ARF<%f%f%f  LTreat the symptoms } Dose of Benzathine penicillin G } as for ARF Echocardiogram (if available) } Medical officer review after one month, and Repeat echocardiogram (if available) If NOT ARF& cease Benzathine but monitor for ARF symptoms If ARF& continue Benzathine and manage as for ARF:j" xQxkn?C CCCcC C (CCCCCcccec ' hSummary%f  >The Jones Criteria is used to guide the diagnosis of ARF with a combination of MAJOR Manifestations, MINOR Manifestations and evidence of recent GAS Infection A long-term Management Plan should be established to prevent recurrence of ARF and development or worsening of RHD Probable ARF cases should also be monitored ?xOG'g R!-$e   i  jSecondary Prophylaxis%f  Secondary prophylaxis is the terms used to describe regular delivery of antibiotics to prevent recurrence of GAS infection and subsequent development of ARF. Secondary prophylaxis is recommended for people who have had ARF, or who have RHD to Prevent further Group A Streptococcal infections Prevent recurrence ARF Prevent the development or worsening of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD. PxnCc$   kStandard Treatment%f  Benzathine penicillin G 1,200,000 units for ALL people e"30kg 600,000 units for children <30kg Every 3 or 4 weeks (by intramuscular injection) Penicillin V Given if needles cannot be given due to excessive bleeding 250mg twice daily (by mouth) Erythromycin Given if Penicillin allergy has been confirmed by a Medical Officer 250mg twice daily (by mouth)Zwnx ZXnx Zkq<nC CKCK'Cc c  CMC cc C  C [$c$ $c$$^   lConsiderations%f  When should secondary prophylaxis be considered? ARF confirmed by the Revised Jones Criteria RHD confirmed on echocardiogram ARF or RHD not confirmed by the Revised Jones Criteria, but considered highly  probable Precautions Do not give Benzathine Penicillin G or Penicillin V if there is a documented Penicillin allergy Drug reactions are rare Continue secondary prophylaxis during pregnancy Continue secondary prophylaxis during anticoagulation (e.g. with Warfarin)1Pnq<x Pxnx}x1 <}x0  +  V  . x  ~ m$Guidelines for Secondary Prophylaxis%%%f % nCeasing Secondary Prophylaxis%f  Secondary Prophylaxis should only be ceased following: No ARF signs/symptoms for at least 5 years, and Medical Specialist review (Paediatrician / Physician / Cardiologist) and Echocardiogram to establish presence & severity of RHD (if available) D8 " 2x n7cca&CCCCa C * C  C  C  C a)CCC$  G o(Benzathine Penicillin injection delivery))%f ) Assessment and Preparation Confirm person s identity Review known drug allergies Discuss and record any recent ARF or RHD symptoms (refer to medical officer if required) Obtain consent for injection nchC'CCCT4    X   p(Benzathine Penicillin injection delivery))%f ) q Documentation%f  rCalculating Injection Delivery%f  sNotes on Injection Delivery%f  t$Factors affecting Injection Delivery%%%f % u(Strategies to improve Injection Delivery))%f ) Appoint a dedicated staff member at each clinic to oversee secondary prophylaxis coordination Identify people who need secondary prophylaxis Identify local health facility for each person Develop systems for follow-up Provide ongoing education for people who require injections and their families Communicate with local RHD programme and other health service providers Reduce injection pain Discuss alternative therapy issuesx  vwxSummary%f  uAntibiotics need to be present in the body at all times to help prevent GAS infections and prevent recurrent ARF Benzathine penicillin injections should be given unless there are contraindications to injections or documented penicillin allergy Medical Specialist review is required before ceasing secondary prophylaxis Strategies to improve secondary prophylaxis delivery: Good relationships between community and health staff Education for the community and health staff Systems for follow-up Communication between health services Reduce injection pain Document Benzathine Penicillin injections and monitor injection deliveryvxnIZpJ7@q  y  z{ Definitions %f  <Valve Regurgitation suggests that heart valves Are thickened and sticky against the walls of the heart Do not meet in the middle Leak (the blood flows backwards over the valve) Valve Stenosis suggests that heart valves Become stuck to each other Do not allow blood to flow through easily (restricted forward flow) /q<xx+` W+ *f = |Signs and Symptoms of RHD%f  rSymptoms of RHD may not develop for many years A murmur but no symptoms usually suggests mild-moderate disease Symptoms usually suggest moderate-severe disease Symptoms depend upon the type and severity of disease, and may include Breathlessness with exertion or when lying down flat Waking at night feeling breathless Feeling tired General weakness Peripheral oedema/q<xrxGq<xx/  ()G<?    $ }Heart valve involvement%f  .Mitral valve is affected in over 90% of cases of RHD Mitral regurgitation most commonly found in children & adolescents Mitral stenosis represents longer term chronic disease, commonly in adults Most common complication of mitral stenosis is atrial fibrillation Aortic valve next most commonly affected Generally associated with disease of the mitral valve. Tends to develop as a long term complication of aortic regurgitation Tricuspid and pulmonary valves are much less commonly affected Usually affected in very severe RHD when all valves are affected5ZZ Z*Z~x?ZAZ.C7 C    #  }      'A / ~Clinical Examination%f  Investigations%f  .Electrocardiogram (ECG) To determine sinus rhythm Chest X-ray (CXR) To determine size and placement of heart To identify cardiac failure (pulmonary congestion) Echocardiography To identify heart valve damage To estimate severity of disease Useful to compare results with future echocardiogram resultsZZZ\Z Z Z|Z E|   / Key element in RHD Management%f   Secondary prophylaxis Functions of secondary prophylaxis with established RHD Prevent Group A Streptococcal infections Prevent the repeated development of ARF Prevent the development of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD.pZ8ZZG$E8Cc$N   Elements in RHD Management%f   KRHD and Pregnancy%f   MManagement of RHD in Pregnancy%f   QInfective Endocarditis%f   S-Procedures that increase risk of Endocarditis..%f-   TSurgery for RHD%f   "Guidelines for managing Mild RHDN#%f%f%f%f #  &Guidelines for managing Moderate RHD<'%f%f%f '  $Guidelines for managing Severe RHD<%%f%f%f %  Summary%f  RHD presents as damage to the heart valves The mitral valve is most commonly affected, followed by Aortic, Pulmonary and Tricuspid RHD can be mild, moderate or severe RHD may be asymptomatic Management of RHD includes Treatment of cardiac and other symptoms Long-term secondary prophylaxis (to prevent recurrent ARF) Regular medical and cardiology review Management of existing pregnancy Dental assessment, family planning referral4xn    Elements of a Disease Register%f  }A disease register is a list of people who have a common illness or disease. For example: Tuberculosis register HIV/AIDS register Vaccine-preventable diseases register (measles, rubella) Acute Rheumatic Fever & Rheumatic Heart Disease A disease register should be secure so that the information is not lost or damaged A disease register can be a computer database or a paper list[xnx[N0R    >   ~ :Paper Register  Book or List%f   8Computer Register  Database%f   Information on the Register%f  Information to identify each person (clinic or hospital number) Personal information (name, date of birth, gender, contact details) Current disease status (ARF only, or mild, moderate, severe RHD) Diagnoses, date of diagnoses How the diagnosis was made (hospital admission, screening programme) Secondary prophylaxis details (medication, amount received each year) Surgery details Dates for next medical review (or for heart valve surgery) Date and cause of death.x$c/ c *c8+c  ($c$.((,c,00  Notification of ARF and RHD%f  dAll people who have confirmed and suspected ARF and RHD should be notified to the RHD register so that health authorities can undertake the following: Identify high risk individuals who require priority care Coordinate secondary prophylaxis and follow-up programmes Help identify others who may be at risk Provide information on the local rates of disease Fn<   '  3 Sources of Information%f  eThe following sources may contain information on individuals for the RHD Register Benzathine Penicillin injection books Echocardiogram reports Heart valve surgery lists Notes from Medical Specialists, Heart Specialists, dentists and researchers Hospital admission and discharge records (e.g. ICD-9 or ICD-10 coding) School and community screening referrals:fxc)= ) Reports from the Register%f  VLists of individuals needing urgent care Lists of people receiving inadequate levels of secondary prophylaxis Delivery of Benzathine penicillin injections (for each full year on treatment) Specialist clinic lists Echocardiogram and Surgery waiting lists People who are deceased and cause of death Rates of disease for the region or countryjWx  ccc W Summary%f  A Disease Register can be on paper or computer The information should be confidential and secure The information on the register should Help coordinate health care for individuals Help describe the level of disease in the community All confirmed and suspected cases of ARF and RHD should be notified to the register Sources of information for the register may include Benzathine penicillin injection books Echocardiogram reports and surgery lists Hospital admission books and computer systems School screening referralstx`nxn_    #WHO recommendations for RHD Control$$%f $ A strong commitment from local Government A committed and skilled RHD Advisory Group An RHD Register of all people with confirmed and suspected ARF and RHD A well-trained programme coordinator Notification of ARF and RHD to the relevant health authority Well-coordinated secondary prevention activities A priority system to help deliver care to individuals at highest risk Reliable resources including medications and laboratory support Programmes established centrally and expanded regionally*+x0x(  Core Programme Objectives%f   Identify and register individuals with ARF and RHD Standardise and improve delivery of secondary prophylaxis Standardise diagnosis and management of ARF and RHD Provide training and support for health workers Provide support to the community Report on the programme and rates of disease$!q<x!   'Objective 1 - Identify & Register cases,( %f'f ( Collect information on known cases of ARF & RHD Benzathine Penicillin injection books and clinic records Echocardiogram reports and cardiac surgery lists Hospital admission & death reports Identify new cases Health centres or hospital when individuals present with ARF or RHD School health (screening) programmes Antenatal Clinics Maintain a paper or computer register of all people with confirmed or suspected ARF & RHD 0ZnPZ|nZZ0nAZ</ {    Z      ,Objective 2 - Optimise Secondary Prophylaxis,- %f!'f - LEstablish secondary prophylaxis delivery Identify people who need secondary prophylaxis Identify health facilities where individuals receive secondary prophylaxis Improve secondary prophylaxis  identify specific barriers to treatment Identify people who do not receive adequate Benzathine penicillin injections (>80% injections) Establish recall and reminder systems Support communication between health facilities Refer new cases to peripheral health facilities for ongoing management Identify people who move between health centres for treatment){nHnn)zG   ' jObjective 3  Training and Support for Health Workers,6 %f*'f5  Standardise guidelines for diagnosis and management of ARF and RHD Revised Jones Criteria for diagnosis of ARF Standardise dosing and delivery of secondary prophylaxis Train health workers Curriculum development Training programmes for students and trained staff Updates for staff in rural and remote areas Communicate Referral of new cases to local community health facilities Update staff about on local ARF/ RHD issues Report on RHD in the communityCZfxZwxZ ZxCew      TB g  x t   >Objective 4  Community Support %f  9Educate and Inform Targeted education for people with ARF and RHD Community education materials (posters & brochures) Manage individuals with ARF & RHD Promote ongoing medical care / echocardiogram / pregnancy counseling / dental care Prioritise treatment for severe cases Cardiac assessment Surgery and supportcn x"Tx&'Mcc"  S    &' : G>Objective 5  Screening for RHD %f  Screening may be undertaken when acute cases are identified and managed, and when time and resources become available. Considerations for screening Who to screened (e.g. school children are easier / RHD may be more common in adults) Methods of diagnosis available (e.g. auscultation & clinical assessment, echocardiogram) Availability of trained staff Processes for reporting RHD cases to the RHD programme Health resources available for long-term management of more RHD cases. xLnvEc  :c<x    A RHD Programme Difficulties%f  Lack of local resources (including dedicated staff) Limited funds and other resources Heavy workloads for primary care health staff Priority of other health issues (e.g. TB, Malaria, HIV/AIDS, respiratory disease) The RHD programme is complex Difficulties around communication with remote health facilities Limited travel to provide training & education Demanding data management Programme expanded too quicklyxnco2 c 3  !  -  Q     + Summary%f  EAn RHD Programme should have Local (Government) commitment A manageable RHD Register Well-trained, dedicated staff at all levels Systems to identify known cases and refer of new cases A priority system for severe cases Secondary Prophylaxis monitoring and improvement Ongoing support for health staff and the community. Z%0x(%    fH<  . 7 $ h /4            !!""##$$%%&&''(())**++,,--..//00112233445566778899::;;<<==>>??@@AABDCFDHENFPHRIUJVK7  0N0 6.  (    s *4 F]9   ,66RwxX  C 0AMenziesLogo^ G:+|  C FA.Caritas Australia logo"`  Fh  C 2Acurekidslogo"`9  ]   C ^AFFIJIWaterFoundation_cmyk_72dpi_Med"`9 P KH  0޽h ? ___f3̙;/f9___PPT10i.Q+D=' E= @B +r/ Ws / V1$(A  D/ 0|DArialnd RomanPPHwؖO 0ؖDVerdana RomanPPHwؖO 0ؖ" DWingdingsRomanPPHwؖO 0ؖ0DTimes New RomanPPHwؖO 0ؖ@DGaramond RomanPPHwؖO 0ؖ@ .  @n?" dd@  @@``  D       %,; (`    uw x         )     &      !"#$%&'()*+,-./012569:;<?@CDEFGHIJR$UE5jXkBvhFR$:DORfaFR$mt"r-8P R$I}_e,D-} b$TAdY˴8^ IR$~a# aN+X3dVR$Bo+esۓ R$.1@lC(]nb$ `5jcl49; 0AA f3@38Oʚ;_R8ʚ;4ddddpO 0<ppzp ppp]  <4dddd 0P<4KdKd 0P<4!d!d 0PN___PPT10DTimes New RomanPPtO 0tDArialNew RomanPPtO 0t ppn___PPT9PH`b2g`kznX{&|(}J2J?  %O  =V QDiagnosis and Management of Acute Rheumatic Fever and Rheumatic Heart Disease nQ8P(' f'(f' f'(f R W This presentation is intended to support the Curriculum for training health workers and others involved in the diagnosis and management of acute rheumatic fever and rheumatic heart disease. It has been made possible thanks to the support of the Vodafone Group Foundation and the International Solidarity, State of Geneva, and the ongoing support of Menzies School of Health Research, Caritas Australia, Fiji Water and Cure Kids. X    7   X  Y Introduction f  bRheumatic Heart Disease is the most common cause of heart disease in children and young adults Approximately 15.6 million people affected worldwide Almost 500,000 new cases each year Approx 350,000 deaths each year Most disease occurs in developing countries. Rheumatic Heart Disease is a disease of poverty Rheumatic Heart Disease can be prevented. D`nZxG8  f$ Z  Z Definitions f  Group A beta-haemolytic streptococci (GAS) Humans are exposed to GAS in the environment Throat and skin are common sites of GAS infection GAS infections usually resolve without treatment Untreated GAS infections can lead to acute rheumatic fever in some people.t+nC CCCc"0$  J  [ Definitions f  QAcute Rheumatic Fever (ARF) A delayed auto-immune response following untreated GAS infection Develops after the GAS infection has resolved Commonly affects the joints, heart, central nervous system and skin Most common between the ages of 5 and 15 years Can recur following further untreated GAS infections Rheumatic Heart Disease (RHD) Residual damage to heart valves following recurrent ARF Valves become scarred, stiff, thickened Blood leaks (blood flows backwards through valves which do not close properly) Blood is blocked (blood can not flow through valves which do not open properly)(nn#######l#3## ##0## #$ O  \ Risk Factors %f   Risk factors ARF include Poverty Poor housing, overcrowded housing Lack of adequate health care Untreated GAS infections Risk factor for RHD Recurrent ARF Prevention The first episode of ARF can be prevented by treating GAS infections with penicillin (primary prophylaxis) If the first ARF episode is not prevented, recurrent ARF can be prevented with long-term penicillin (secondary prophylaxis)&Z`nZ!Zn Zn#`#### #  #  # T #  #d##<`  %   ]Disease Progression%f  CControl of Disease%f   ARF and RHD can be prevented by sustainable control strategies including Trained health staff who diagnose and management disease effectively Secondary prophylaxis to prevent further ARF and the development or worsening of RHD. Community education and awareness Screening for unknown RHD in the community. Control strategies should focus on Prompt identification and treatment of GAS infections Identifying people who have had ARF once and preventing further ARF and the development of RHD.IZnZ$ZnH####$##TI E W ! -   ^  _Revised Jones Criteria%f  ARF can be confirmed if certain signs and symptoms are present. The Revised Jones Criteria (below) can help guide the diagnosis.xC$  ; ' `Revised Jones Criteria%f  The World Health Organisation set the international standard for diagnosis of ARF. First episode or recurrent episode of ARF (no RHD): 2 MAJOR manifestations or 1 MAJOR and 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ARF (with existing RHD): 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ** Individual country guidelines also exist **^xnZZ0 fn]nZ5ZRCC4CAGfEGfcac A  G f E  G fcCAGfEGfcace c%c c C $g$f(A((G(f(E((G(f,c,,a,0C04c44e4 4c4%4c4 8A88C808A8<     bSigns and Symptoms%f  2MAJOR Manifestations Arthritis Painful, swollen joints (usually knees, ankles, wrists, elbows) Very common with ARF, often the first symptom Usually  migratory - disappears from one joint as it starts in another (poly-arthritis), however may just be present in one joint (mono-arthritis). Carditis May present as a heart  murmur Chest pain and/or difficulty breathing may be present in more severe cases 2!xn 0 dnmx Cc(cuccc*ccc Ck c  "   cSigns and Symptoms%f  Sydenham s chorea Twitchy, jerking movements and muscle weakness (most obvious in the face, hands and feet) May occur on both sides or only one side of body More common in teenagers and females (rare after age 20) May be associated with irritability and or depression May begin up to 3-4 months after the streptococcal throat infection, and often occurs without other symptoms Usually resolves within 6 weeks (may last 6 months or more) May recur in females during pregnancyxnC/c+cVcccc&cxk  0  9 6 m  < & dSigns and Symptoms%f  Subcutaneous nodules Painless lumps on the outside surfaces of elbows, wrists, knees, ankles in groups of 3-4 (up to 12) The skin is not red or inflamed Last 1-2 weeks (rarely more than 1 month) Nodules are more common when Carditis is also present. Erythema marginatum Painless, flat pink patches on the skin that spread outward in a circular pattern Usually occurs early, may last months, rarely lasts years Usually on the back or front of body, almost never on the face Hard to see in dark-skinned people.xnPPnCYc c/cc7cc C cx    )    9  >  $ ESigns and Symptoms%f  ZMINOR Manifestations Fever Occurs in the majority of cases, usually with the onset of symptoms Usually ranging from 38.4  40.0 C (101-104 F) Arthralgia Usually involves large joints May be mild or severe Group A streptococcal infection Group A beta-haemolytic streptococci may not be seen on a throat swab since the infection may be resolved at the time of onset of ARF symptoms. ASOT  serum reaches a peak level around 3-6 weeks after infection and starts to fall at 6-8 weeks Anti DNase B  reaches a peak level up to 6-8 weeks after infection and starts to fall at around 3 months after the infection. ** Normal antibody titre ranges vary with age and geography **HxvZ Z8Z!0" dZr0Z(ZFZGCucc C4 c  c  g  c s c   a <A  E         Y    W    < aDifficulties with ARF Diagnosis %f  BA combination of signs and symptoms is required to confirm ARF People with ARF do not always present to the health system with symptoms because Symptoms may not be considered serious Transport to the health facility may be difficult Health staff may not recognise the signs and symptoms of ARF ARF may be confused with other illnesses, for example Sore joints may be confused with a sports injury or  growing pains YntxDCYcc< C  C 7 C DC  eTreatment for ARF%f  :Treat the acute illness Benzathine penicillin G injection or Oral Penicillin for 10 days Relieve symptoms Bed rest Relief of arthritis, pain and fever (Paracetamol or Aspirin) Treat chorea (use Carbamazepine or Valproic acid if severe) Anti-heart failure medication (e.g. Diuretics, ACEi, Digoxin if required) VBnncC"ccc c  c C-cc c/cccc ; fARF Management Plan%f  )First dose of Benzathine penicillin G (start secondary prophylaxis) Baseline echocardiogram (if available) ARF alert on medical notes & computer systems (if applicable) Education for person and family Refer to local doctor / health facility Dental examination Long-term secondary prophylaxis plan )x&cccc.ccclC  d    '  9 gManagement of Probable ARF<%f%f%f  LTreat the symptoms } Dose of Benzathine penicillin G } as for ARF Echocardiogram (if available) } Medical officer review after one month, and Repeat echocardiogram (if available) If NOT ARF& cease Benzathine but monitor for ARF symptoms If ARF& continue Benzathine and manage as for ARF:j" xQxkn?C CCCcC C (CCCCCcccec ' hSummary%f  >The Jones Criteria is used to guide the diagnosis of ARF with a combination of MAJOR Manifestations, MINOR Manifestations and evidence of recent GAS Infection A long-term Management Plan should be established to prevent recurrence of ARF and development or worsening of RHD Probable ARF cases should also be monitored ?xOG'g R!-$e   i  jSecondary Prophylaxis%f  Secondary prophylaxis is the terms used to describe regular delivery of antibiotics to prevent recurrence of GAS infection and subsequent development of ARF. Secondary prophylaxis is recommended for people who have had ARF, or who have RHD to Prevent further Group A Streptococcal infections Prevent recurrence ARF Prevent the development or worsening of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD. PxnCc$   kStandard Treatment%f  Benzathine penicillin G 1,200,000 units for ALL people e"30kg 600,000 units for children <30kg Every 3 or 4 weeks (by intramuscular injection) Penicillin V Given if needles cannot be given due to excessive bleeding 250mg twice daily (by mouth) Erythromycin Given if Penicillin allergy has been confirmed by a Medical Officer 250mg twice daily (by mouth)Zwnx ZXnx Zkq<nC CKCK'Cc c  CMC cc C  C [$c$ $c$$^   lConsiderations%f  When should secondary prophylaxis be considered? ARF confirmed by the Revised Jones Criteria RHD confirmed on echocardiogram ARF or RHD not confirmed by the Revised Jones Criteria, but considered highly  probable Precautions Do not give Benzathine Penicillin G or Penicillin V if there is a documented Penicillin allergy Drug reactions are rare Continue secondary prophylaxis during pregnancy Continue secondary prophylaxis during anticoagulation (e.g. with Warfarin)1Pnq<x Pxnx}x1 <}x0  +  V  . x  ~ m$Guidelines for Secondary Prophylaxis%%%f % nCeasing Secondary Prophylaxis%f  Secondary Prophylaxis should only be ceased following: No ARF signs/symptoms for at least 5 years, and Medical Specialist review (Paediatrician / Physician / Cardiologist) and Echocardiogram to establish presence & severity of RHD (if available) D8 " 2x n7cca&CCCCa C * C  C  C  C a)CCC$  G o(Benzathine Penicillin injection delivery))%f ) Assessment and Preparation Confirm person s identity Review known drug allergies Discuss and record any recent ARF or RHD symptoms (refer to medical officer if required) Obtain consent for injection nchC'CCCT4    X   p(Benzathine Penicillin injection delivery))%f ) q Documentation%f  rCalculating Injection Delivery%f  sNotes on Injection Delivery%f  t$Factors affecting Injection Delivery%%%f % u(Strategies to improve Injection Delivery))%f ) Appoint a dedicated staff member at each clinic to oversee secondary prophylaxis coordination Identify people who need secondary prophylaxis Identify local health facility for each person Develop systems for follow-up Provide ongoing education for people who require injections and their families Communicate with local RHD programme and other health service providers Reduce injection pain Discuss alternative therapy issuesx  vwxSummary%f  uAntibiotics need to be present in the body at all times to help prevent GAS infections and prevent recurrent ARF Benzathine penicillin injections should be given unless there are contraindications to injections or documented penicillin allergy Medical Specialist review is required before ceasing secondary prophylaxis Strategies to improve secondary prophylaxis delivery: Good relationships between community and health staff Education for the community and health staff Systems for follow-up Communication between health services Reduce injection pain Document Benzathine Penicillin injections and monitor injection deliveryvxnIZpJ7@q  y  z{ Definitions %f  <Valve Regurgitation suggests that heart valves Are thickened and sticky against the walls of the heart Do not meet in the middle Leak (the blood flows backwards over the valve) Valve Stenosis suggests that heart valves Become stuck to each other Do not allow blood to flow through easily (restricted forward flow) /q<xx+` W+ *f = |Signs and Symptoms of RHD%f  rSymptoms of RHD may not develop for many years A murmur but no symptoms usually suggests mild-moderate disease Symptoms usually suggest moderate-severe disease Symptoms depend upon the type and severity of disease, and may include Breathlessness with exertion or when lying down flat Waking at night feeling breathless Feeling tired General weakness Peripheral oedema/q<xrxGq<xx/  ()G<?    $ }Heart valve involvement%f  .Mitral valve is affected in over 90% of cases of RHD Mitral regurgitation most commonly found in children & adolescents Mitral stenosis represents longer term chronic disease, commonly in adults Most common complication of mitral stenosis is atrial fibrillation Aortic valve next most commonly affected Generally associated with disease of the mitral valve. Tends to develop as a long term complication of aortic regurgitation Tricuspid and pulmonary valves are much less commonly affected Usually affected in very severe RHD when all valves are affected5ZZ Z*Z~x?ZAZ.C7 C    #  }      'A / ~Clinical Examination%f  Investigations%f  .Electrocardiogram (ECG) To determine sinus rhythm Chest X-ray (CXR) To determine size and placement of heart To identify cardiac failure (pulmonary congestion) Echocardiography To identify heart valve damage To estimate severity of disease Useful to compare results with future echocardiogram resultsZZZ\Z Z Z|Z E|   / Key element in RHD Management%f   Secondary prophylaxis Functions of secondary prophylaxis with established RHD Prevent Group A Streptococcal infections Prevent the repeated development of ARF Prevent the development of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD.pZ8ZZG$E8Cc$N   Elements in RHD Management%f   KRHD and Pregnancy%f   MManagement of RHD in Pregnancy%f   QInfective Endocarditis%f   S-Procedures that increase risk of Endocarditis..%f-   TSurgery for RHD%f   "Guidelines for managing Mild RHDN#%f%f%f%f #  &Guidelines for managing Moderate RHD<'%f%f%f '  $Guidelines for managing Severe RHD<%%f%f%f %  Summary%f  RHD presents as damage to the heart valves The mitral valve is most commonly affected, followed by Aortic, Pulmonary and Tricuspid RHD can be mild, moderate or severe RHD may be asymptomatic Management of RHD includes Treatment of cardiac and other symptoms Long-term secondary prophylaxis (to prevent recurrent ARF) Regular medical and cardiology review Management of existing pregnancy Dental assessment, family planning referral4xn    Elements of a Disease Register%f  }A disease register is a list of people who have a common illness or disease. For example: Tuberculosis register HIV/AIDS register Vaccine-preventable diseases register (measles, rubella) Acute Rheumatic Fever & Rheumatic Heart Disease A disease register should be secure so that the information is not lost or damaged A disease register can be a computer database or a paper list[xnx[N0R    >   ~ :Paper Register  Book or List%f   8Computer Register  Database%f   Information on the Register%f  Information to identify each person (clinic or hospital number) Personal information (name, date of birth, gender, contact details) Current disease status (ARF only, or mild, moderate, severe RHD) Diagnoses, date of diagnoses How the diagnosis was made (hospital admission, screening programme) Secondary prophylaxis details (medication, amount received each year) Surgery details Dates for next medical review (or for heart valve surgery) Date and cause of death.x$c/ c *c8+c  ($c$.((,c,00  Notification of ARF and RHD%f  dAll people who have confirmed and suspected ARF and RHD should be notified to the RHD register so that health authorities can undertake the following: Identify high risk individuals who require priority care Coordinate secondary prophylaxis and follow-up programmes Help identify others who may be at risk Provide information on the local rates of disease Fn<   '  3 Sources of Information%f  eThe following sources may contain information on individuals for the RHD Register Benzathine Penicillin injection books Echocardiogram reports Heart valve surgery lists Notes from Medical Specialists, Heart Specialists, dentists and researchers Hospital admission and discharge records (e.g. ICD-9 or ICD-10 coding) School and community screening referrals:fxc)= ) Reports from the Register%f  VLists of individuals needing urgent care Lists of people receiving inadequate levels of secondary prophylaxis Delivery of Benzathine penicillin injections (for each full year on treatment) Specialist clinic lists Echocardiogram and Surgery waiting lists People who are deceased and cause of death Rates of disease for the region or countryjWx  ccc W Summary%f  A Disease Register can be on paper or computer The information should be confidential and secure The information on the register should Help coordinate health care for individuals Help describe the level of disease in the community All confirmed and suspected cases of ARF and RHD should be notified to the register Sources of information for the register may include Benzathine penicillin injection books Echocardiogram reports and surgery lists Hospital admission books and computer systems School screening referralstx`nxn_    #WHO recommendations for RHD Control$$%f $ A strong commitment from local Government A committed and skilled RHD Advisory Group An RHD Register of all people with confirmed and suspected ARF and RHD A well-trained programme coordinator Notification of ARF and RHD to the relevant health authority Well-coordinated secondary prevention activities A priority system to help deliver care to individuals at highest risk Reliable resources including medications and laboratory support Programmes established centrally and expanded regionally*+x0x(  Core Programme Objectives%f   Identify and register individuals with ARF and RHD Standardise and improve delivery of secondary prophylaxis Standardise diagnosis and management of ARF and RHD Provide training and support for health workers Provide support to the community Report on the programme and rates of disease$!q<x!   'Objective 1 - Identify & Register cases,( %f'f ( Collect information on known cases of ARF & RHD Benzathine Penicillin injection books and clinic records Echocardiogram reports and cardiac surgery lists Hospital admission & death reports Identify new cases Health centres or hospital when individuals present with ARF or RHD School health (screening) programmes Antenatal Clinics Maintain a paper or computer register of all people with confirmed or suspected ARF & RHD 0ZnPZ|nZZ0nAZ</{    Z      ,Objective 2 - Optimise Secondary Prophylaxis,- %f!'f - LEstablish secondary prophylaxis delivery Identify people who need secondary prophylaxis Identify health facilities where individuals receive secondary prophylaxis Improve secondary prophylaxis  identify specific barriers to treatment Identify people who do not receive adequate Benzathine penicillin injections (>80% injections) Establish recall and reminder systems Support communication between health facilities Refer new cases to peripheral health facilities for ongoing management Identify people who move between health centres for treatment){nHnn)zG   ' jObjective 3  Training and Support for Health Workers,6 %f*'f5  Standardise guidelines for diagnosis and management of ARF and RHD Revised Jones Criteria for diagnosis of ARF Standardise dosing and delivery of secondary prophylaxis Train health workers Curriculum development Training programmes for students and trained staff Updates for staff in rural and remote areas Communicate Referral of new cases to local community health facilities Update staff about on local ARF/ RHD issues Report on RHD in the communityCZfxZwxZ ZxCew      TB g  x t   >Objective 4  Community Support %f  9Educate and Inform Targeted education for people with ARF and RHD Community education materials (posters & brochures) Manage individuals with ARF & RHD Promote ongoing medical care / echocardiogram / pregnancy counseling / dental care Prioritise treatment for severe cases Cardiac assessment Surgery and supportcn x"Tx&'Mcc"  S    &' : G>Objective 5  Screening for RHD %f  Screening may be undertaken when acute cases are identified and managed, and when time and resources become available. Considerations for screening Who to screened (e.g. school children are easier / RHD may be more common in adults) Methods of diagnosis available (e.g. auscultation & clinical assessment, echocardiogram) Availability of trained staff Processes for reporting RHD cases to the RHD programme Health resources available for long-term management of more RHD cases. xLnvEc  :c<x    A RHD Programme Difficulties%f  Lack of local resources (including dedicated staff) Limited funds and other resources Heavy workloads for primary care health staff Priority of other health issues (e.g. TB, Malaria, HIV/AIDS, respiratory disease) The RHD programme is complex Difficulties around communication with remote health facilities Limited travel to provide training & education Demanding data management Programme expanded too quicklyxnco2 c 3  !  -  Q     + Summary%f  EAn RHD Programme should have Local (Government) commitment A manageable RHD Register Well-trained, dedicated staff at all levels Systems to identify known cases and refer of new cases A priority system for severe cases Secondary Prophylaxis monitoring and improvement Ongoing support for health staff and the community. 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" # $ % & ' ( ) * + , - . / 0 1 2 3 4 5 6 7 8 9 : ; < = > ? @ A B C D E F G H I J K L M N O P Q R S T U V W X Y Z [ \ ] ^ _ ` a b c d e f g h i j k l m n o p q r s t u v w x y z { | } ~ nPPHwؖO 0ؖ0DTimes New RomanPPHwؖO 0ؖ@DGaramond RomanPPHwؖO 0ؖ@ .  @n?" dd@  @@``  D       %,; (`    uw x         )     &      !"#$%&'()*+,-./012569:;<?@CDEFGHIJR$UE5jXkBvhFR$:DORfaFR$mt"r-8P R$I}_e,D-} b$TAdY˴8^ IR$~a# aN+X3dVR$Bo+esۓ R$.1@lC(]nb$ `5jcl49; 0AA f3@38Oʚ;_R8ʚ;4ddddO 0<ppzp ppp]  <4dddd 0P<4KdKd 0P<4!d!d 0PN___PPT10DTimes New RomanPPtO 0tDArialNew RomanPPtO 0t ppn___PPT9PH`b2g`kznX{&|(}J2J?  %O  =V QDiagnosis and Management of Acute Rheumatic Fever and Rheumatic Heart Disease nQ8P(' f'(f' f'(f R W This presentation is intended to support the Curriculum for training health workers and others involved in the diagnosis and management of acute rheumatic fever and rheumatic heart disease. It has been made possible thanks to the support of the Vodafone Group Foundation and the International Solidarity, State of Geneva, and the ongoing support of Menzies School of Health Research, Caritas Australia, Fiji Water Foundation and Cure Kids. J      X  Y Introduction f  bRheumatic Heart Disease is the most common cause of heart disease in children and young adults Approximately 15.6 million people affected worldwide Almost 500,000 new cases each year Approx 350,000 deaths each year Most disease occurs in developing countries. Rheumatic Heart Disease is a disease of poverty Rheumatic Heart Disease can be prevented. D`nZxG8  f$ Z  Z Definitions f  Group A beta-haemolytic streptococci (GAS) Humans are exposed to GAS in the environment Throat and skin are common sites of GAS infection GAS infections usually resolve without treatment Untreated GAS infections can lead to acute rheumatic fever in some people.t+nC CCCc"0$  J  [ Definitions f  QAcute Rheumatic Fever (ARF) A delayed auto-immune response following untreated GAS infection Develops after the GAS infection has resolved Commonly affects the joints, heart, central nervous system and skin Most common between the ages of 5 and 15 years Can recur following further untreated GAS infections Rheumatic Heart Disease (RHD) Residual damage to heart valves following recurrent ARF Valves become scarred, stiff, thickened Blood leaks (blood flows backwards through valves which do not close properly) Blood is blocked (blood can not flow through valves which do not open properly)(nn#######l#3## ##0## #$ O  \ Risk Factors %f   Risk factors ARF include Poverty Poor housing, overcrowded housing Lack of adequate health care Untreated GAS infections Risk factor for RHD Recurrent ARF Prevention The first episode of ARF can be prevented by treating GAS infections with penicillin (primary prophylaxis) If the first ARF episode is not prevented, recurrent ARF can be prevented with long-term penicillin (secondary prophylaxis)&Z`nZ!Zn Zn#`#### #  #  # T #  #d##<`  %   ]Disease Progression%f  CControl of Disease%f   ARF and RHD can be prevented by sustainable control strategies including Trained health staff who diagnose and management disease effectively Secondary prophylaxis to prevent further ARF and the development or worsening of RHD. Community education and awareness Screening for unknown RHD in the community. Control strategies should focus on Prompt identification and treatment of GAS infections Identifying people who have had ARF once and preventing further ARF and the development of RHD.IZnZ$ZnH####$##TI E W ! -   ^  _Revised Jones Criteria%f  ARF can be confirmed if certain signs and symptoms are present. The Revised Jones Criteria (below) can help guide the diagnosis.xC$  ; ' `Revised Jones Criteria%f  The World Health Organisation set the international standard for diagnosis of ARF. First episode or recurrent episode of ARF (no RHD): 2 MAJOR manifestations or 1 MAJOR and 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ARF (with existing RHD): 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ** Individual country guidelines also exist **^xnZZ0 fn]nZ5ZRCC4CAGfEGfcac A  G f E  G fcCAGfEGfcace c%c c C $g$f(A((G(f(E((G(f,c,,a,0C04c44e4 4c4%4c4 8A88C808A8<     bSigns and Symptoms%f  2MAJOR Manifestations Arthritis Painful, swollen joints (usually knees, ankles, wrists, elbows) Very common with ARF, often the first symptom Usually  migratory - disappears from one joint as it starts in another (poly-arthritis), however may just be present in one joint (mono-arthritis). Carditis May present as a heart  murmur Chest pain and/or difficulty breathing may be present in more severe cases 2!xn 0 dnmx Cc(cuccc*ccc Ck c  "   cSigns and Symptoms%f  Sydenham s chorea Twitchy, jerking movements and muscle weakness (most obvious in the face, hands and feet) May occur on both sides or only one side of body More common in teenagers and females (rare after age 20) May be associated with irritability and or depression May begin up to 3-4 months after the streptococcal throat infection, and often occurs without other symptoms Usually resolves within 6 weeks (may last 6 months or more) May recur in females during pregnancyxnC/c+cVcccc&cxk  0  9 6 m  < & dSigns and Symptoms%f  Subcutaneous nodules Painless lumps on the outside surfaces of elbows, wrists, knees, ankles in groups of 3-4 (up to 12) The skin is not red or inflamed Last 1-2 weeks (rarely more than 1 month) Nodules are more common when Carditis is also present. Erythema marginatum Painless, flat pink patches on the skin that spread outward in a circular pattern Usually occurs early, may last months, rarely lasts years Usually on the back or front of body, almost never on the face Hard to see in dark-skinned people.xnPPnCYc c/cc7cc C cx    )    9  >  $ ESigns and Symptoms%f  ZMINOR Manifestations Fever Occurs in the majority of cases, usually with the onset of symptoms Usually ranging from 38.4  40.0 C (101-104 F) Arthralgia Usually involves large joints May be mild or severe Group A streptococcal infection Group A beta-haemolytic streptococci may not be seen on a throat swab since the infection may be resolved at the time of onset of ARF symptoms. ASOT  serum reaches a peak level around 3-6 weeks after infection and starts to fall at 6-8 weeks Anti DNase B  reaches a peak level up to 6-8 weeks after infection and starts to fall at around 3 months after the infection. ** Normal antibody titre ranges vary with age and geography **HxvZ Z8Z!0" dZr0Z(ZFZGCucc C4 c  c  g  c s c   a <A  E         Y    W    < aDifficulties with ARF Diagnosis %f  BA combination of signs and symptoms is required to confirm ARF People with ARF do not always present to the health system with symptoms because Symptoms may not be considered serious Transport to the health facility may be difficult Health staff may not recognise the signs and symptoms of ARF ARF may be confused with other illnesses, for example Sore joints may be confused with a sports injury or  growing pains YntxDCYcc< C  C 7 C DC  eTreatment for ARF%f  :Treat the acute illness Benzathine penicillin G injection or Oral Penicillin for 10 days Relieve symptoms Bed rest Relief of arthritis, pain and fever (Paracetamol or Aspirin) Treat chorea (use Carbamazepine or Valproic acid if severe) Anti-heart failure medication (e.g. Diuretics, ACEi, Digoxin if required) VBnncC"ccc c  c C-cc c/cccc ; fARF Management Plan%f  )First dose of Benzathine penicillin G (start secondary prophylaxis) Baseline echocardiogram (if available) ARF alert on medical notes & computer systems (if applicable) Education for person and family Refer to local doctor / health facility Dental examination Long-term secondary prophylaxis plan )x&cccc.ccclC  d    '  9 gManagement of Probable ARF<%f%f%f  LTreat the symptoms } Dose of Benzathine penicillin G } as for ARF Echocardiogram (if available) } Medical officer review after one month, and Repeat echocardiogram (if available) If NOT ARF& cease Benzathine but monitor for ARF symptoms If ARF& continue Benzathine and manage as for ARF:j" xQxkn?C CCCcC C (CCCCCcccec ' hSummary%f  >The Jones Criteria is used to guide the diagnosis of ARF with a combination of MAJOR Manifestations, MINOR Manifestations and evidence of recent GAS Infection A long-term Management Plan should be established to prevent recurrence of ARF and development or worsening of RHD Probable ARF cases should also be monitored ?xOG'g R!-$e   i  jSecondary Prophylaxis%f  Secondary prophylaxis is the terms used to describe regular delivery of antibiotics to prevent recurrence of GAS infection and subsequent development of ARF. Secondary prophylaxis is recommended for people who have had ARF, or who have RHD to Prevent further Group A Streptococcal infections Prevent recurrence ARF Prevent the development or worsening of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD. PxnCc$   kStandard Treatment%f  Benzathine penicillin G 1,200,000 units for ALL people e"30kg 600,000 units for children <30kg Every 3 or 4 weeks (by intramuscular injection) Penicillin V Given if needles cannot be given due to excessive bleeding 250mg twice daily (by mouth) Erythromycin Given if Penicillin allergy has been confirmed by a Medical Officer 250mg twice daily (by mouth)Zwnx ZXnx Zkq<nC CKCK'Cc c  CMC cc C  C [$c$ $c$$^   lConsiderations%f  When should secondary prophylaxis be considered? ARF confirmed by the Revised Jones Criteria RHD confirmed on echocardiogram ARF or RHD not confirmed by the Revised Jones Criteria, but considered highly  probable Precautions Do not give Benzathine Penicillin G or Penicillin V if there is a documented Penicillin allergy Drug reactions are rare Continue secondary prophylaxis during pregnancy Continue secondary prophylaxis during anticoagulation (e.g. with Warfarin)1Pnq<x Pxnx}x1 <}x0  +  V  . x  ~ m$Guidelines for Secondary Prophylaxis%%%f % nCeasing Secondary Prophylaxis%f  Secondary Prophylaxis should only be ceased following: No ARF signs/symptoms for at least 5 years, and Medical Specialist review (Paediatrician / Physician / Cardiologist) and Echocardiogram to establish presence & severity of RHD (if available) D8 " 2x n7cca&CCCCa C * C  C  C  C a)CCC$  G o(Benzathine Penicillin injection delivery))%f ) Assessment and Preparation Confirm person s identity Review known drug allergies Discuss and record any recent ARF or RHD symptoms (refer to medical officer if required) Obtain consent for injection nchC'CCCT4    X   p(Benzathine Penicillin injection delivery))%f ) q Documentation%f  rCalculating Injection Delivery%f  sNotes on Injection Delivery%f  t$Factors affecting Injection Delivery%%%f % u(Strategies to improve Injection Delivery))%f ) Appoint a dedicated staff member at each clinic to oversee secondary prophylaxis coordination Identify people who need secondary prophylaxis Identify local health facility for each person Develop systems for follow-up Provide ongoing education for people who require injections and their families Communicate with local RHD programme and other health service providers Reduce injection pain Discuss alternative therapy issuesx  vwxSummary%f  uAntibiotics need to be present in the body at all times to help prevent GAS infections and prevent recurrent ARF Benzathine penicillin injections should be given unless there are contraindications to injections or documented penicillin allergy Medical Specialist review is required before ceasing secondary prophylaxis Strategies to improve secondary prophylaxis delivery: Good relationships between community and health staff Education for the community and health staff Systems for follow-up Communication between health services Reduce injection pain Document Benzathine Penicillin injections and monitor injection deliveryvxnIZpJ7@q  y  z{ Definitions %f  <Valve Regurgitation suggests that heart valves Are thickened and sticky against the walls of the heart Do not meet in the middle Leak (the blood flows backwards over the valve) Valve Stenosis suggests that heart valves Become stuck to each other Do not allow blood to flow through easily (restricted forward flow) /q<xx+` W+ *f = |Signs and Symptoms of RHD%f  rSymptoms of RHD may not develop for many years A murmur but no symptoms usually suggests mild-moderate disease Symptoms usually suggest moderate-severe disease Symptoms depend upon the type and severity of disease, and may include Breathlessness with exertion or when lying down flat Waking at night feeling breathless Feeling tired General weakness Peripheral oedema/q<xrxGq<xx/  ()G<?    $ }Heart valve involvement%f  .Mitral valve is affected in over 90% of cases of RHD Mitral regurgitation most commonly found in children & adolescents Mitral stenosis represents longer term chronic disease, commonly in adults Most common complication of mitral stenosis is atrial fibrillation Aortic valve next most commonly affected Generally associated with disease of the mitral valve. Tends to develop as a long term complication of aortic regurgitation Tricuspid and pulmonary valves are much less commonly affected Usually affected in very severe RHD when all valves are affected5ZZ Z*Z~x?ZAZ.C7 C    #  }      'A / ~Clinical Examination%f  Investigations%f  .Electrocardiogram (ECG) To determine sinus rhythm Chest X-ray (CXR) To determine size and placement of heart To identify cardiac failure (pulmonary congestion) Echocardiography To identify heart valve damage To estimate severity of disease Useful to compare results with future echocardiogram resultsZZZ\Z Z Z|Z E|   / Key element in RHD Management%f   Secondary prophylaxis Functions of secondary prophylaxis with established RHD Prevent Group A Streptococcal infections Prevent the repeated development of ARF Prevent the development of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD.pZ8ZZG$E8Cc$N   Elements in RHD Management%f   KRHD and Pregnancy%f   MManagement of RHD in Pregnancy%f   QInfective Endocarditis%f   S-Procedures that increase risk of Endocarditis..%f-   TSurgery for RHD%f   "Guidelines for managing Mild RHDN#%f%f%f%f #  &Guidelines for managing Moderate RHD<'%f%f%f '  $Guidelines for managing Severe RHD<%%f%f%f %  Summary%f  RHD presents as damage to the heart valves The mitral valve is most commonly affected, followed by Aortic, Pulmonary and Tricuspid RHD can be mild, moderate or severe RHD may be asymptomatic Management of RHD includes Treatment of cardiac and other symptoms Long-term secondary prophylaxis (to prevent recurrent ARF) Regular medical and cardiology review Management of existing pregnancy Dental assessment, family planning referral4xn    Elements of a Disease Register%f  }A disease register is a list of people who have a common illness or disease. For example: Tuberculosis register HIV/AIDS register Vaccine-preventable diseases register (measles, rubella) Acute Rheumatic Fever & Rheumatic Heart Disease A disease register should be secure so that the information is not lost or damaged A disease register can be a computer database or a paper list[xnx[N0R    >   ~ :Paper Register  Book or List%f   8Computer Register  Database%f   Information on the Register%f  Information to identify each person (clinic or hospital number) Personal information (name, date of birth, gender, contact details) Current disease status (ARF only, or mild, moderate, severe RHD) Diagnoses, date of diagnoses How the diagnosis was made (hospital admission, screening programme) Secondary prophylaxis details (medication, amount received each year) Surgery details Dates for next medical review (or for heart valve surgery) Date and cause of death.x$c/ c *c8+c  ($c$.((,c,00  Notification of ARF and RHD%f  dAll people who have confirmed and suspected ARF and RHD should be notified to the RHD register so that health authorities can undertake the following: Identify high risk individuals who require priority care Coordinate secondary prophylaxis and follow-up programmes Help identify others who may be at risk Provide information on the local rates of disease Fn<   '  3 Sources of Information%f  eThe following sources may contain information on individuals for the RHD Register Benzathine Penicillin injection books Echocardiogram reports Heart valve surgery lists Notes from Medical Specialists, Heart Specialists, dentists and researchers Hospital admission and discharge records (e.g. ICD-9 or ICD-10 coding) School and community screening referrals:fxc)= ) Reports from the Register%f  VLists of individuals needing urgent care Lists of people receiving inadequate levels of secondary prophylaxis Delivery of Benzathine penicillin injections (for each full year on treatment) Specialist clinic lists Echocardiogram and Surgery waiting lists People who are deceased and cause of death Rates of disease for the region or countryjWx  ccc W Summary%f  A Disease Register can be on paper or computer The information should be confidential and secure The information on the register should Help coordinate health care for individuals Help describe the level of disease in the community All confirmed and suspected cases of ARF and RHD should be notified to the register Sources of information for the register may include Benzathine penicillin injection books Echocardiogram reports and surgery lists Hospital admission books and computer systems School screening referralstx`nxn_    #WHO recommendations for RHD Control$$%f $ A strong commitment from local Government A committed and skilled RHD Advisory Group An RHD Register of all people with confirmed and suspected ARF and RHD A well-trained programme coordinator Notification of ARF and RHD to the relevant health authority Well-coordinated secondary prevention activities A priority system to help deliver care to individuals at highest risk Reliable resources including medications and laboratory support Programmes established centrally and expanded regionally*+x0x(  Core Programme Objectives%f   Identify and register individuals with ARF and RHD Standardise and improve delivery of secondary prophylaxis Standardise diagnosis and management of ARF and RHD Provide training and support for health workers Provide support to the community Report on the programme and rates of disease$!q<x!   'Objective 1 - Identify & Register cases,( %f'f ( Collect information on known cases of ARF & RHD Benzathine Penicillin injection books and clinic records Echocardiogram reports and cardiac surgery lists Hospital admission & death reports Identify new cases Health centres or hospital when individuals present with ARF or RHD School health (screening) programmes Antenatal Clinics Maintain a paper or computer register of all people with confirmed or suspected ARF & RHD 0ZnPZ|nZZ0nAZ</{    Z      ,Objective 2 - Optimise Secondary Prophylaxis,- %f!'f - LEstablish secondary prophylaxis delivery Identify people who need secondary prophylaxis Identify health facilities where individuals receive secondary prophylaxis Improve secondary prophylaxis  identify specific barriers to treatment Identify people who do not receive adequate Benzathine penicillin injections (>80% injections) Establish recall and reminder systems Support communication between health facilities Refer new cases to peripheral health facilities for ongoing management Identify people who move between health centres for treatment){nHnn)zG   ' jObjective 3  Training and Support for Health Workers,6 %f*'f5  Standardise guidelines for diagnosis and management of ARF and RHD Revised Jones Criteria for diagnosis of ARF Standardise dosing and delivery of secondary prophylaxis Train health workers Curriculum development Training programmes for students and trained staff Updates for staff in rural and remote areas Communicate Referral of new cases to local community health facilities Update staff about on local ARF/ RHD issues Report on RHD in the communityCZfxZwxZ ZxCew      TB g  x t   >Objective 4  Community Support %f  9Educate and Inform Targeted education for people with ARF and RHD Community education materials (posters & brochures) Manage individuals with ARF & RHD Promote ongoing medical care / echocardiogram / pregnancy counseling / dental care Prioritise treatment for severe cases Cardiac assessment Surgery and supportcn x"Tx&'Mcc"  S    &' : G>Objective 5  Screening for RHD %f  Screening may be undertaken when acute cases are identified and managed, and when time and resources become available. Considerations for screening Who to screened (e.g. school children are easier / RHD may be more common in adults) Methods of diagnosis available (e.g. auscultation & clinical assessment, echocardiogram) Availability of trained staff Processes for reporting RHD cases to the RHD programme Health resources available for long-term management of more RHD cases. xLnvEc  :c<x    A RHD Programme Difficulties%f  Lack of local resources (including dedicated staff) Limited funds and other resources Heavy workloads for primary care health staff Priority of other health issues (e.g. TB, Malaria, HIV/AIDS, respiratory disease) The RHD programme is complex Difficulties around communication with remote health facilities Limited travel to provide training & education Demanding data management Programme expanded too quicklyxnco2 c 3  !  -  Q     + Summary%f  EAn RHD Programme should have Local (Government) commitment A manageable RHD Register Well-trained, dedicated staff at all levels Systems to identify known cases and refer of new cases A priority system for severe cases Secondary Prophylaxis monitoring and improvement Ongoing support for health staff and the community. Z%0x(%    fH<  . 7 $ h /4            !!""##$$%%&&''(())**++,,--..//00112233445566778899::;;<<==>>??@@AABDCFDHENFPHRIUJVK7  0N0 6.  (    s *4 F]9   ,66RwxX  C 0AMenziesLogo^ G:+|  C FA.Caritas Australia logo"`  Fh  C 2Acurekidslogo"`9  ]   C ^AFFIJIWaterFoundation_cmyk_72dpi_Med"`9 P KH  0޽h ? ___f3̙;/f9___PPT10i.Q+D=' o= @B +r  Ws  Q V1!(A  D/ 0|DArialnd RomanPPHwؖO 0ؖDVerdana RomanPPHwؖO 0ؖ" DWingdingsRomanPPHwؖO 0ؖ0DTimes New RomanPPHwؖO 0ؖ@DGaramond RomanPPHwؖO 0ؖ@ .  @n?" dd@  @@``  D       %,; (`    uw x         )     &      !"#$%&'()*+,-./012569:;<?@CDEFGHIJR$UE5jXkBvhFR$:DORfaFR$mt"r-8P R$I}_e,D-} b$TAdY˴8^ IR$~a# aN+X3dVR$Bo+esۓ R$.1@lC(]nb$ `5jcl49; 0AA f3@38Oʚ;_R8ʚ;4ddddO 0<ppzp ppp]  <4dddd 0P<4KdKd 0P<4!d!d 0PN___PPT10DTimes New RomanPPtO 0tDArialNew RomanPPtO 0t ppn___PPT9PH`b2g`kznX{&|(}J2J?  %O  =V QDiagnosis and Management of Acute Rheumatic Fever and Rheumatic Heart Disease nQ8P(' f'(f' f'(f R W This presentation is intended to support the Curriculum for training health workers and others involved in the diagnosis and management of acute rheumatic fever and rheumatic heart disease. It has been made possible thanks to the support of the Vodafone Group Foundation and the International Solidarity, State of Geneva, and the ongoing support of Menzies School of Health Research, Caritas Australia, Fiji Water Foundation and Cure Kids. J      X  Y Introduction f  bRheumatic Heart Disease is the most common cause of heart disease in children and young adults Approximately 15.6 million people affected worldwide Almost 500,000 new cases each year Approx 350,000 deaths each year Most disease occurs in developing countries. Rheumatic Heart Disease is a disease of poverty Rheumatic Heart Disease can be prevented. D`nZxG8  f$ Z  Z Definitions f  Group A beta-haemolytic streptococci (GAS) Humans are exposed to GAS in the environment Throat and skin are common sites of GAS infection GAS infections usually resolve without treatment Untreated GAS infections can lead to acute rheumatic fever in some people.t+nC CCCc"0$  J  [ Definitions f  QAcute Rheumatic Fever (ARF) A delayed auto-immune response following untreated GAS infection Develops after the GAS infection has resolved Commonly affects the joints, heart, central nervous system and skin Most common between the ages of 5 and 15 years Can recur following further untreated GAS infections Rheumatic Heart Disease (RHD) Residual damage to heart valves following recurrent ARF Valves become scarred, stiff, thickened Blood leaks (blood flows backwards through valves which do not close properly) Blood is blocked (blood can not flow through valves which do not open properly)(nn#######l#3## ##0## #$ O  \ Risk Factors %f   Risk factors ARF include Poverty Poor housing, overcrowded housing Lack of adequate health care Untreated GAS infections Risk factor for RHD Recurrent ARF Prevention The first episode of ARF can be prevented by treating GAS infections with penicillin (primary prophylaxis) If the first ARF episode is not prevented, recurrent ARF can be prevented with long-term penicillin (secondary prophylaxis)&Z`nZ!Zn Zn#`#### #  #  # T #  #d##<`  %   ]Disease Progression%f  CControl of Disease%f   ARF and RHD can be prevented by sustainable control strategies including Trained health staff who diagnose and management disease effectively Secondary prophylaxis to prevent further ARF and the development or worsening of RHD. Community education and awareness Screening for unknown RHD in the community. Control strategies should focus on Prompt identification and treatment of GAS infections Identifying people who have had ARF once and preventing further ARF and the development of RHD.IZnZ$ZnH####$##TI E W ! -   ^  _Revised Jones Criteria%f  ARF can be confirmed if certain signs and symptoms are present. The Revised Jones Criteria (below) can help guide the diagnosis.xC$  ; ' `Revised Jones Criteria%f  The World Health Organisation set the international standard for diagnosis of ARF. First  episode or recurrent episode of ARF (no RHD): 2 MAJOR manifestations or 1 MAJOR and 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ARF (with existing RHD): 2 MINOR manifestations and Evidence of preceding Group A streptococcal infection & (within 3 weeks before ARF symptoms) ** Individual country guidelines also exist **^xnZZ0 fn]nZ5ZRCC4CAGfEGfcac A  G f E  G fcCAGfEGfcace c%c c C $g$f(A((G(f(E((G(f,c,,a,0C04c44e4 4c4%4c4 8A88C808A8<     bSigns and Symptoms%f  2MAJOR Manifestations Arthritis Painful, swollen joints (usually knees, ankles, wrists, elbows) Very common with ARF, often the first symptom Usually  migratory - disappears from one joint as it starts in another (poly-arthritis), however may just be present in one joint (mono-arthritis). Carditis May present as a heart  murmur Chest pain and/or difficulty breathing may be present in more severe cases 2!xn 0 dnmx Cc(cuccc*ccc Ck c  "   cSigns and Symptoms%f  Sydenham s chorea Twitchy, jerking movements and muscle weakness (most obvious in the face, hands and feet) May occur on both sides or only one side of body More common in teenagers and females (rare after age 20) May be associated with irritability and or depression May begin up to 3-4 months after the streptococcal throat infection, and often occurs without other symptoms Usually resolves within 6 weeks (may last 6 months or more) May recur in females during pregnancyxnC/c+cVcccc&cxk  0  9 6 m  < & dSigns and Symptoms%f  Subcutaneous nodules Painless lumps on the outside surfaces of elbows, wrists, knees, ankles in groups of 3-4 (up to 12) The skin is not red or inflamed Last 1-2 weeks (rarely more than 1 month) Nodules are more common when Carditis is also present. Erythema marginatum Painless, flat pink patches on the skin that spread outward in a circular pattern Usually occurs early, may last months, rarely lasts years Usually on the back or front of body, almost never on the face Hard to see in dark-skinned people.xnPPnCYc c/cc7cc C cx    )    9  >  $ ESigns and Symptoms%f  ZMINOR Manifestations Fever Occurs in the majority of cases, usually with the onset of symptoms Usually ranging from 38.4  40.0 C (101-104 F) Arthralgia Usually involves large joints May be mild or severe Group A streptococcal infection Group A beta-haemolytic streptococci may not be seen on a throat swab since the infection may be resolved at the time of onset of ARF symptoms. ASOT  serum reaches a peak level around 3-6 weeks after infection and starts to fall at 6-8 weeks Anti DNase B  reaches a peak level up to 6-8 weeks after infection and starts to fall at around 3 months after the infection. ** Normal antibody titre ranges vary with age and geography **HxvZ Z8Z!0" dZr0Z(ZFZGCucc C4 c  c  g  c s c   a <A  E         Y    W    < aDifficulties with ARF Diagnosis %f  BA combination of signs and symptoms is required to confirm ARF People with ARF do not always present to the health system with symptoms because Symptoms may not be considered serious Transport to the health facility may be difficult Health staff may not recognise the signs and symptoms of ARF ARF may be confused with other illnesses, for example Sore joints may be confused with a sports injury or  growing pains YntxDCYcc< C  C 7 C DC  eTreatment for ARF%f  :Treat the acute illness Benzathine penicillin G injection or Oral Penicillin for 10 days Relieve symptoms Bed rest Relief of arthritis, pain and fever (Paracetamol or Aspirin) Treat chorea (use Carbamazepine or Valproic acid if severe) Anti-heart failure medication (e.g. Diuretics, ACEi, Digoxin if required) VBnncC"ccc c  c C-cc c/cccc ; fARF Management Plan%f  )First dose of Benzathine penicillin G (start secondary prophylaxis) Baseline echocardiogram (if available) ARF alert on medical notes & computer systems (if applicable) Education for person and family Refer to local doctor / health facility Dental examination Long-term secondary prophylaxis plan )x&cccc.ccclC  d    '  9 gManagement of Probable ARF<%f%f%f  LTreat the symptoms } Dose of Benzathine penicillin G } as for ARF Echocardiogram (if available) } Medical officer review after one month, and Repeat echocardiogram (if available) If NOT ARF& cease Benzathine but monitor for ARF symptoms If ARF& continue Benzathine and manage as for ARF:j" xQxkn?C CCCcC C (CCCCCcccec ' hSummary%f  >The Jones Criteria is used to guide the diagnosis of ARF with a combination of MAJOR Manifestations, MINOR Manifestations and evidence of recent GAS Infection A long-term Management Plan should be established to prevent recurrence of ARF and development or worsening of RHD Probable ARF cases should also be monitored ?xOG'g R!-$e   i  jSecondary Prophylaxis%f  Secondary prophylaxis is the terms used to describe regular delivery of antibiotics to prevent recurrence of GAS infection and subsequent development of ARF. Secondary prophylaxis is recommended for people who have had ARF, or who have RHD to Prevent further Group A Streptococcal infections Prevent recurrence ARF Prevent the development or worsening of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD. PxnCc$   kStandard Treatment%f  Benzathine penicillin G 1,200,000 units for ALL people e"30kg 600,000 units for children <30kg Every 3 or 4 weeks (by intramuscular injection) Penicillin V Given if needles cannot be given due to excessive bleeding 250mg twice daily (by mouth) Erythromycin Given if Penicillin allergy has been confirmed by a Medical Officer 250mg twice daily (by mouth)Zwnx ZXnx Zkq<nC CKCK'Cc c  CMC cc C  C [$c$ $c$$^   lConsiderations%f  When should secondary prophylaxis be considered? ARF confirmed by the Revised Jones Criteria RHD confirmed on echocardiogram ARF or RHD not confirmed by the Revised Jones Criteria, but considered highly  probable Precautions Do not give Benzathine Penicillin G or Penicillin V if there is a documented Penicillin allergy Drug reactions are rare Continue secondary prophylaxis during pregnancy Continue secondary prophylaxis during anticoagulation (e.g. with Warfarin)1Pnq<x Pxnx}x1 <}x0  +  V  . x  ~ m$Guidelines for Secondary Prophylaxis%%%f % nCeasing Secondary Prophylaxis%f  Secondary Prophylaxis should only be ceased following: No ARF signs/symptoms for at least 5 years, and Medical Specialist review (Paediatrician / Physician / Cardiologist) and Echocardiogram to establish presence & severity of RHD (if available) D8 " 2x n7cca&CCCCa C * C  C  C  C a)CCC$  G o(Benzathine Penicillin injection delivery))%f ) Assessment and Preparation Confirm person s identity Review known drug allergies Discuss and record any recent ARF or RHD symptoms (refer to medical officer if required) Obtain consent for injection nchC'CCCT4    X   p(Benzathine Penicillin injection delivery))%f ) q Documentation%f  rCalculating Injection Delivery%f  sNotes on Injection Delivery%f  t$Factors affecting Injection Delivery%%%f % u(Strategies to improve Injection Delivery))%f ) Appoint a dedicated staff member at each clinic to oversee secondary prophylaxis coordination Identify people who need secondary prophylaxis Identify local health facility for each person Develop systems for follow-up Provide ongoing education for people who require injections and their families Communicate with local RHD programme and other health service providers Reduce injection pain Discuss alternative therapy issuesx  vwxSummary%f  uAntibiotics need to be present in the body at all times to help prevent GAS infections and prevent recurrent ARF Benzathine penicillin injections should be given unless there are contraindications to injections or documented penicillin allergy Medical Specialist review is required before ceasing secondary prophylaxis Strategies to improve secondary prophylaxis delivery: Good relationships between community and health staff Education for the community and health staff Systems for follow-up Communication between health services Reduce injection pain Document Benzathine Penicillin injections and monitor injection deliveryvxnIZpJ7@q  y  z{ Definitions %f  <Valve Regurgitation suggests that heart valves Are thickened and sticky against the walls of the heart Do not meet in the middle Leak (the blood flows backwards over the valve) Valve Stenosis suggests that heart valves Become stuck to each other Do not allow blood to flow through easily (restricted forward flow) /q<xx+` W+ *f = |Signs and Symptoms of RHD%f  rSymptoms of RHD may not develop for many years A murmur but no symptoms usually suggests mild-moderate disease Symptoms usually suggest moderate-severe disease Symptoms depend upon the type and severity of disease, and may include Breathlessness with exertion or when lying down flat Waking at night feeling breathless Feeling tired General weakness Peripheral oedema/q<xrxGq<xx/  ()G<?    $ }Heart valve involvement%f  .Mitral valve is affected in over 90% of cases of RHD Mitral regurgitation most commonly found in children & adolescents Mitral stenosis represents longer term chronic disease, commonly in adults Most common complication of mitral stenosis is atrial fibrillation Aortic valve next most commonly affected Generally associated with disease of the mitral valve. Tends to develop as a long term complication of aortic regurgitation Tricuspid and pulmonary valves are much less commonly affected Usually affected in very severe RHD when all valves are affected5ZZ Z*Z~x?ZAZ.C7 C    #  }      'A / ~Clinical Examination%f  Investigations%f  .Electrocardiogram (ECG) To determine sinus rhythm Chest X-ray (CXR) To determine size and placement of heart To identify cardiac failure (pulmonary congestion) Echocardiography To identify heart valve damage To estimate severity of disease Useful to compare results with future echocardiogram resultsZZZ\Z Z Z|Z E|   / Key element in RHD Management%f   Secondary prophylaxis Functions of secondary prophylaxis with established RHD Prevent Group A Streptococcal infections Prevent the repeated development of ARF Prevent the development of RHD Reduce the severity of RHD Help reduce the risk of death from severe RHD.pZ8ZZG$E8Cc$N   Elements in RHD Management%f   KRHD and Pregnancy%f   MManagement of RHD in Pregnancy%f   QInfective Endocarditis%f   S-Procedures that increase risk of Endocarditis..%f-   TSurgery for RHD%f   "Guidelines for managing Mild RHDN#%f%f%f%f #  &Guidelines for managing Moderate RHD<'%f%f%f '  $Guidelines for managing Severe RHD<%%f%f%f %  Summary%f  RHD presents as damage to the heart valves The mitral valve is most commonly affected, followed by Aortic, Pulmonary and Tricuspid RHD can be mild, moderate or severe RHD may be asymptomatic Management of RHD includes Treatment of cardiac and other symptoms Long-term secondary prophylaxis (to prevent recurrent ARF) Regular medical and cardiology review Management of existing pregnancy Dental assessment, family planning referral4xn    Elements of a Disease Register%f  }A disease register is a list of people who have a common illness or disease. For example: Tuberculosis register HIV/AIDS register Vaccine-preventable diseases register (measles, rubella) Acute Rheumatic Fever & Rheumatic Heart Disease A disease register should be secure so that the information is not lost or damaged A disease register can be a computer database or a paper list[xnx[N0R    >   ~ :Paper Register  Book or List%f   8Computer Register  Database%f   Information on the Register%f  Information to identify each person (clinic or hospital number) Personal information (name, date of birth, gender, contact details) Current disease status (ARF only, or mild, moderate, severe RHD) Diagnoses, date of diagnoses How the diagnosis was made (hospital admission, screening programme) Secondary prophylaxis details (medication, amount received each year) Surgery details Dates for next medical review (or for heart valve surgery) Date and cause of death.x$c/ c *c8+c  ($c$.((,c,00  Notification of ARF and RHD%f  dAll people who have confirmed and suspected ARF and RHD should be notified to the RHD register so that health authorities can undertake the following: Identify high risk individuals who require priority care Coordinate secondary prophylaxis and follow-up programmes Help identify others who may be at risk Provide information on the local rates of disease Fn<   '  3 Sources of Information%f  eThe following sources may contain information on individuals for the RHD Register Benzathine Penicillin injection books Echocardiogram reports Heart valve surgery lists Notes from Medical Specialists, Heart Specialists, dentists and researchers Hospital admission and discharge records (e.g. ICD-9 or ICD-10 coding) School and community screening referrals:fxc)= ) Reports from the Register%f  VLists of individuals needing urgent care Lists of people receiving inadequate levels of secondary prophylaxis Delivery of Benzathine penicillin injections (for each full year on treatment) Specialist clinic lists Echocardiogram and Surgery waiting lists People who are deceased and cause of death Rates of disease for the region or countryjWx  ccc W Summary%f  A Disease Register can be on paper or computer The information should be confidential and secure The information on the register should Help coordinate health care for individuals Help describe the level of disease in the community All confirmed and suspected cases of ARF and RHD should be notified to the register Sources of information for the register may include Benzathine penicillin injection books Echocardiogram reports and surgery lists Hospital admission books and computer systems School screening referralstx`nxn_    #WHO recommendations for RHD Control$$%f $ A strong commitment from local Government A committed and skilled RHD Advisory Group An RHD Register of all people with confirmed and suspected ARF and RHD A well-trained programme coordinator Notification of ARF and RHD to the relevant health authority Well-coordinated secondary prevention activities A priority system to help deliver care to individuals at highest risk Reliable resources including medications and laboratory support Programmes established centrally and expanded regionally*+x0x(  Core Programme Objectives%f   Identify and register individuals with ARF and RHD Standardise and improve delivery of secondary prophylaxis Standardise diagnosis and management of ARF and RHD Provide training and support for health workers Provide support to the community Report on the programme and rates of disease$!q<x!   'Objective 1 - Identify & Register cases,( %f'f ( Collect information on known cases of ARF & RHD Benzathine Penicillin injection books and clinic records Echocardiogram reports and cardiac surgery lists Hospital admission & death reports Identify new cases Health centres or hospital when individuals present with ARF or RHD School health (screening) programmes Antenatal Clinics Maintain a paper or computer register of all people with confirmed or suspected ARF & RHD 0ZnPZ|nZZ0nAZ</{    Z      ,Objective 2 - Optimise Secondary Prophylaxis,- %f!'f - LEstablish secondary prophylaxis delivery Identify people who need secondary prophylaxis Identify health facilities where individuals receive secondary prophylaxis Improve secondary prophylaxis  identify specific barriers to treatment Identify people who do not receive adequate Benzathine penicillin injections (>80% injections) Establish recall and reminder systems Support communication between health facilities Refer new cases to peripheral health facilities for ongoing management Identify people who move between health centres for treatment){nHnn)zG   ' jObjective 3  Training and Support for Health Workers,6 %f*'f5  Standardise guidelines for diagnosis and management of ARF and RHD Revised Jones Criteria for diagnosis of ARF Standardise dosing and delivery of secondary prophylaxis Train health workers Curriculum development Training programmes for students and trained staff Updates for staff in rural and remote areas Communicate Referral of new cases to local community health facilities Update staff about on local ARF/ RHD issues Report on RHD in the communityCZfxZwxZ ZxCew      TB g  x t   >Objective 4  Community Support %f  9Educate and Inform Targeted education for people with ARF and RHD Community education materials (posters & brochures) Manage individuals with ARF & RHD Promote ongoing medical care / echocardiogram / pregnancy counseling / dental care Prioritise treatment for severe cases Cardiac assessment Surgery and supportcn x"Tx&'Mcc"  S    &' : G>Objective 5  Screening for RHD %f  Screening may be undertaken when acute cases are identified and managed, and when time and resources become available. Considerations for screening Who to screened (e.g. school children are easier / RHD may be more common in adults) Methods of diagnosis available (e.g. auscultation & clinical assessment, echocardiogram) Availability of trained staff Processes for reporting RHD cases to the RHD programme Health resources available for long-term management of more RHD cases. xLnvEc  :c<x    A RHD Programme Difficulties%f  Lack of local resources (including dedicated staff) Limited funds and other resources Heavy workloads for primary care health staff Priority of other health issues (e.g. TB, Malaria, HIV/AIDS, respiratory disease) The RHD programme is complex Difficulties around communication with remote health facilities Limited travel to provide training & education Demanding data management Programme expanded too quicklyxnco2 c 3  !  -  Q     + Summary%f  EAn RHD Programme should have Local (Government) commitment A manageable RHD Register Well-trained, dedicated staff at all levels Systems to identify known cases and refer of new cases A priority system for severe cases Secondary Prophylaxis monitoring and improvement Ongoing support for health staff and the community. 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